Results 11 to 20 of about 29,955 (251)
PB1834: ACQUIRED FACTOR VII DEFICIENCY ASSOCIATED WITH ACUTE MYELOID LEUKEMIA [PDF]
HemaSphere, 2023 Haifa Hafsa +6 more
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Seminars in Thrombosis and Hemostasis, 2009 The complex formed between the procoagulant serine protease activated factor VII (FVII) and the membrane protein tissue factor, exposed on the vascular lumen upon injury, triggers the initiation of blood clotting. This review describes the clinical picture of FVII deficiency and provides information on diagnosis and management of the disease.
G. Mariani, BERNARDI, Francesco
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Congenital Factor VII Deficiency Presenting with Isolated Recurrent Hematuria: A Case Report
Acta Medica Iranica, 2021 Introduction: Factor VII deficiency is a rare congenital coagulopathy disorder. In most cases this disorder is diagnosed in childhood. Common symptoms of congenital factor VII deficiency are different and consist of mucosal cutaneous hemorrhage ...
Shahla Ansary Damavandi +3 more
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Thrombosis Journal, 2023 Background Factor VII deficiency is a rare bleeding disorder caused by a deficiency of clotting factor VII. However, there have been some case reports of venous thrombosis in patients with factor VII deficiency, especially underlying the prothrombotic ...
Lei Li +4 more
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Blood Coagulation & Fibrinolysis, 2002 As yet, there have been neither systematic reviews nor reports of randomized, controlled trials involving factor VII (FVII) deficiency. Hence, a picture of this disorder can only be drawn by reviewing and summarizing the data that is available. This article provides an overview of the understanding of this rare, inherited disorder of coagulation.
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Haematologica, 2013 Because of the very short half-life of factor VII, prophylaxis in factor VII deficiency is considered a difficult endeavor. The clinical efficacy and safety of prophylactic regimens, and indications for their use, were evaluated in factor VII-deficient ...
Mariasanta Napolitano +13 more
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A case of intracranial hemorrhage in a neonate with congenital factor VII deficiency [PDF]
Korean Journal of Pediatrics, 2010 Congenital factor VII deficiency is a rare autosomal-recessive bleeding disorder. Bleeding manifestations and clinical findings vary widely, ranging from asymptomatic subjects to patients with hemorrhages that may cause significant handicaps.
Won Seok Lee, Young Sil Park
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Inhibitors to factor
Haemophilia, 2014 We performed a prospective study of FVII inhibitor occurrence in a large number of patients with FVII deficiency who had received replacement therapy for spontaneous or traumatic bleeding episodes, major or minor surgical interventions or prophylaxis.Inhibitor development was detected in 2.6% (3/115) of patients, but the incidence of de novo inhibitors
Batorova A +11 more
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Congenital factor VII deficiency presenting first time as isolated recurrent hematuria at late age
Saudi Journal of Kidney Diseases and Transplantation, 2019 Hematological conditions rarely present as isolated hematuria. Factor VII deficiency is a rare congenital coagulopathy inherited as autosomal recessive pattern. It usually presents a severe life-threatening bleeding at an early age.
Suman Sethi +5 more
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Stem Cell Research, 2020 Factor VII (FVII) deficiency is the most common among the rare bleeding disorders, which is caused by mutations in coagulation factor VII. Clinical features caused by FVII deficiency vary from mild or asymptomatic to fatal cerebral hemorrhage.
Do-Hun Kim +3 more
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