Inhibitors in Patients with Congenital Bleeding Disorders Other Than Hemophilia [PDF]
, 2017 The most worrying complication of replacement therapy for severe hemophilia A and B is currently the occurrence of inhibitory alloantibodies against infused factor VIII and factor IX, respectively.
Franchini, Massimo +6 more
core +1 more source
Inhibitors to factor
Haemophilia, 2014 We performed a prospective study of FVII inhibitor occurrence in a large number of patients with FVII deficiency who had received replacement therapy for spontaneous or traumatic bleeding episodes, major or minor surgical interventions or prophylaxis.Inhibitor development was detected in 2.6% (3/115) of patients, but the incidence of de novo inhibitors
Batorova A +11 more
openaire +3 more sources
Congenital factor VII deficiency presenting first time as isolated recurrent hematuria at late age
Saudi Journal of Kidney Diseases and Transplantation, 2019 Hematological conditions rarely present as isolated hematuria. Factor VII deficiency is a rare congenital coagulopathy inherited as autosomal recessive pattern. It usually presents a severe life-threatening bleeding at an early age.
Suman Sethi +5 more
doaj +1 more source
Stem Cell Research, 2020 Factor VII (FVII) deficiency is the most common among the rare bleeding disorders, which is caused by mutations in coagulation factor VII. Clinical features caused by FVII deficiency vary from mild or asymptomatic to fatal cerebral hemorrhage.
Do-Hun Kim +3 more
doaj +1 more source
Replacement therapy for bleeding episodes in factor VII deficiency: A prospective evaluation [PDF]
, 2013 Patients with inherited factor VII (FVII) deficiency display different clinical phenotypes requiring ad hoc management. This study evaluated treatments for spontaneous and traumatic bleeding using data from the Seven Treatment Evaluation Registry (STER).
Auerswald,G +14 more
core +1 more source
Successful Treatment of Intracranial Hemorrhage with Recombinant Activated Factor VII in a Patient with Newly Diagnosed Acute Myeloid Leukemia: A Case Report and Review of the Literature [PDF]
, 2015 Intracranial hemorrhage (ICH) is a common complication in acute myeloid leukemia (AML) patients with an incidence rate of 6.3% [1]. Bleeding disorders related to disseminated intravascular coagulation (DIC) are common complications in AML cases [2 ...
Daniel Johnson +10 more
core +3 more sources
Vitamin K as a diet supplement with impact in human health: current evidence in age-related idseases [PDF]
, 2020 Vitamin K health benefits have been recently widely shown to extend beyond blood homeostasis and implicated in chronic low-grade inflammatory diseases such as cardiovascular disease, osteoarthritis, dementia, cognitive impairment, mobility disability ...
Araujo, Nuna C. P. +3 more
core +1 more source
The Turkish Journal of Pediatrics, 2018 Intracranial hemorrhage is considered the most common cause of death in newborns with congenital factor VII (FVII) deficiency. Recombinant activated FVII (rFVIIa) provides specific replacement therapy, however there is limited experience with its ...
Zeynep İnce +5 more
doaj +1 more source
Dental extraction in congenital factor Vll deficiency with inhibitor – a case report
The Journal of Haemophilia Practice, 2021 Hereditary factor VII (FVII) deficiency is a rare bleeding disorder with autosomal recessive inheritance, and FVII deficiency with an inhibitor is extremely rare.
Nayar Geeta +3 more
doaj +1 more source
The Arecibo Galaxy Environment Survey VII : A Dense Filament With Extremely Long HI Streams [PDF]
, 2014 We present completed observations of the NGC 7448 galaxy group and background volume as part of the blind neutral hydrogen Arecibo Galaxy Environment Survey (AGES).
Davies, J. I. +5 more
core +1 more source