Structure and Function of the Extracellular Matrix in Normal and Pathological Conditions: Looking at the Bicuspid Aortic Valve. [PDF]
Nappi F.
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Expression of Elastin, F-Box and WD-40 Domain-Containing Protein 2, Fibrillin-1, and Alpha-Smooth Muscle Actin in Utilized Blood Vessels for explant culture-A New 3D in Vitro Vascular Model from Bovine Legs. [PDF]
Akiyama M.
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Integrin-mediated mTOR signaling drives TGF-β overactivity and myxomatous mitral valve degeneration in hypomorphic fibrillin-1 mice. [PDF]
Gao F +9 more
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Downregulation of <i>S100a8</i> mitigates fibrosis in skeletal muscles affected by Marfan syndrome. [PDF]
Santos AR +7 more
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Case Report: A <i>FBN1</i> frameshift-and-nonsense mutation and aortic dissection in Marfan syndrome. [PDF]
Su C, Zeng L, Lu H, Wang Z, Wei M.
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Zonulopathies as Genetic Disorders of the Extracellular Matrix. [PDF]
Chipeta C, Aragon-Martin J, Chandra A.
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Chloroplast Fibrillin-Mediated α-Tocopherol Biosynthesis Impaired by a Virus to Enhance Infection and to Improve Drought Tolerance. [PDF]
Liu S +8 more
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Vitreous Fibrillar Structure and Interfibrillar Composition in Adult Mice. [PDF]
Jaramillo-Garcés P +5 more
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Histological and Immunohistochemical Insights into Disc Perforation in the Temporomandibular Joint: A Case Report. [PDF]
Freni J +5 more
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Fibrillins 1 and 2 are the main constituents of the extracellular microfibrils responsible for the biomechanical properties of most tissues and organs. They are cysteine-rich glycoproteins predominantly made of multiple repeats homologous to the calcium-binding epidermal growth factor module, and are translated as precursor proteins cleaved by furine ...
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