Results 181 to 190 of about 12,218 (212)
Some of the next articles are maybe not open access.
Fibrillin immunofluorescence in pseudoxanthoma elasticum
Journal of the American Academy of Dermatology, 1995Pseudoxanthoma elasticum (PXE) is a rare heritable connective tissue disorder manifested by skin, ocular, and cardiovascular anomalies. The basic defect is unknown; however, the microscopic findings are indicative of defects in elastic fibers. Among the components of the elastic fibers are elastin and elastin-associated microfibrils.We assessed the ...
M, Godfrey +6 more
openaire +2 more sources
2010
Microfibrils are supramolecular structures ubiquitously found in the extracellular matrix of elastic and nonelastic tissues. The three members of the cysteine-rich fibrillin family constitute the core of microfibrils. Mutations in fibrillin-1 and -2 lead to a number of heritable connective tissue disorders termed fibrillinopathies.
Dirk Hubmacher, Dieter P. Reinhardt
openaire +1 more source
Microfibrils are supramolecular structures ubiquitously found in the extracellular matrix of elastic and nonelastic tissues. The three members of the cysteine-rich fibrillin family constitute the core of microfibrils. Mutations in fibrillin-1 and -2 lead to a number of heritable connective tissue disorders termed fibrillinopathies.
Dirk Hubmacher, Dieter P. Reinhardt
openaire +1 more source
Journal of Dental Research, 2002
The elastic system fibers consist of three types—oxytalan, elaunin, and elastic fibers—differing in their relative microfibril and elastin contents. All three types are found in human gingiva, but human periodontal ligaments contain only elastin-free fibers.
E, Tsuruga, K, Irie, T, Yajima
openaire +2 more sources
The elastic system fibers consist of three types—oxytalan, elaunin, and elastic fibers—differing in their relative microfibril and elastin contents. All three types are found in human gingiva, but human periodontal ligaments contain only elastin-free fibers.
E, Tsuruga, K, Irie, T, Yajima
openaire +2 more sources
Organization and Biomechanical Properties of Fibrillin Microfibrils
2004The evolution and function of multicellular organisms has required tissue flexibility and the necessity to withstand stretch. These properties underpin movement and allow responses to changing environments. The elastic fibre is a bio-composite material composed of two insoluble extracellular matrix assemblies; fibrillin-rich microfibrils and elastin ...
Kielty, C M +5 more
openaire +3 more sources
Marfan's Syndrome and Other Disorders of Fibrillin
New England Journal of Medicine, 1994Marfan's syndrome is classically defined as an autosomal dominant disorder of connective tissue with variable manifestations involving primarily the cardiovascular, ocular, and musculoskeletal syst...
U, Francke, H, Furthmayr
openaire +2 more sources
The structure and function of fibrillin.
Ciba Foundation symposium, 1996Fibrillin is a very large molecule whose primary structure is now known from the cloning and sequencing of 10 kb of cDNA. Immunohistochemical results suggest that one of the functions of fibrillin molecules is to contribute to the structure of the microfibril.
D P, Reinhardt +2 more
openaire +1 more source
The Role of Fibrillin 1 and Fibrillin 2 in Severe Scoliosis
1999Child A +5 more
openaire +1 more source
Fibrillin-1 regulates white adipose tissue development, homeostasis, and function
Matrix Biology, 2022Muthu L Muthu +2 more
exaly