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Fmf - Open Access .click
Results 1 to 10 of about 6,508 (115)

AA amyloidosis in the four historical monogenic autoinflammatory diseases: Clinical burden and insights from a retrospective referral-centre study. [PDF]

open access: yesJ Intern Med
Abstract Background AA amyloidosis (AAA) remains a life‐threatening yet largely preventable complication of monogenic autoinflammatory diseases (AIDs). Methods We retrospectively described patients with AAA secondary to one of the four historical monogenic AIDs (familial Mediterranean fever [FMF], cryopyrin‐associated periodic syndrome [CAPS ...
El Moussaoui M   +11 more
europepmc   +2 more sources

First Trimester Screening for Preterm Preeclampsia in the United Kingdom: A Cost-Effectiveness Analysis. [PDF]

open access: yesBJOG
ABSTRACT Objective To evaluate the cost‐effectiveness of the Fetal Medicine Foundation (FMF) strategy, compared with the National Institute for Health and Care Excellence (NICE) strategy, for first‐trimester screening for preterm preeclampsia (PE) in the United Kingdom (UK). Design Cost‐effectiveness analysis.
Ani MA   +4 more
europepmc   +2 more sources

Digital Light Processing of Thermoplastic Poly(methyl methacrylate) Photoresin Combined With Solvent Vapor Smoothing

open access: yesAdvanced Engineering Materials, EarlyView.
A thermoplastic PMMA‐based photoresin enables high‐resolution DLP printing followed by solvent‐vapor smoothing. The treatment reduces staircase‐induced surface roughness from 2.33 µm to 129 nm and increases visible‐light transmittance from approximately 30% to 80%, providing a route toward transparent PMMA components for rapid prototyping and non ...
Rozhin Heydarpour   +5 more
wiley   +1 more source

Lone‐Pair‐Induced Lattice Distortion in Lead‐Free Hybrid Perovskites for High‐Performance Nanogenerators

open access: yesAdvanced Functional Materials, EarlyView.
A lead‐free tin‐based hybrid perovskite is designed in which stereochemically active lone‐pair electrons on tin distort the crystal lattice and break its symmetry. Blended into a flexible polymer, the material converts pressure into electricity at milliwatt‐scale power density and continues working far below freezing, powering a commercial wristwatch ...
Majid Haji Bagheri   +12 more
wiley   +1 more source

Rethinking Charge Transport and Recombination in Donor‐Diluted Organic Solar Cells

open access: yesAdvanced Materials, EarlyView.
Organic solar cells with 1–45% PM6 content in Y12 were studied to link structure and charge dynamics to performance. The conductivity follows a 3D percolation model without a sharp threshold. Donor dilution preserves the photogeneration yield, but limits the fill factor due to transport resistance losses.
Chen Wang   +14 more
wiley   +1 more source

Multicomponent Molecular Editing of Polybutadiene: From Design Space to Battery Function

open access: yesAdvanced Science, EarlyView.
Multicomponent molecular editing transforms polybutadiene into an 18‐member polymer library with tunable thermal properties, nanoscale organization, and molecular dynamics. Mapping this multidimensional design space reveals distinct molecular input–property relationships and guides the selection of a candidate electrolyte additive for lithium–sulfur ...
Janna Jeschke   +8 more
wiley   +1 more source

Space Pump: Repairable 3D‐Printed Bioinspired Pneumatic Peristaltic Pump for Fluid and Regolith Transport in Space

open access: yesAdvanced Intelligent Systems, EarlyView.
The space pump transports lunar regolith under vacuum condition. A fully 3D‐printed biomimetic peristaltic pump demonstrates reliable transport of liquids and solids using pneumatic ring actuators and flexible fused filament fabrication. The system operates under atmospheric and vacuum conditions, achieves high flow rates, and enables self‐priming ...
Daniel Bellin   +4 more
wiley   +1 more source

Patient‐Derived Fibroblasts as a Clinically Relevant Model of Kearns–Sayre Syndrome

open access: yesAnnals of Neurology, EarlyView.
Objective Kearns–Sayre syndrome (KSS) is characterized by single large‐scale mitochondrial DNA deletions and by severe early‐onset clinical manifestations with neurological involvement. Reliable disease models, as well as validated biomarkers or effective treatments, are lacking.
Laura Valls‐Roca   +24 more
wiley   +1 more source

NiFe‐NO3 Layered Double Hydroxide as a Novel Anode for Sodium Ion Batteries

open access: yesBatteries &Supercaps, Volume 8, Issue 3, March 2025.
This study demonstrates, for the first time, the effectiveness of using LDH as an anodic material in SIB. The material is stable and show high specific capacity, the reaction mechanism has been thoroughly investigated and comprehensively described and involves a phase change reaction followed by sodium intercalation.
Marco Fortunato   +4 more
wiley   +1 more source

Patient‐reported outcomes and medication errors during oral antitumour therapy in paediatrics: Results from the youngAMBORA care programme

open access: yesBritish Journal of Clinical Pharmacology, EarlyView.
Aim Increasing use of oral antitumour therapeutics (OAT) in paediatrics is associated with numerous advantages, but also with error‐prone aspects. Based on the randomized AMBORA trial including adults treated with various OAT, we developed a tailored pharmacological/pharmaceutical care programme for children and their caregivers during OAT treatment ...
Phyllis Lensker   +4 more
wiley   +1 more source

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