Results 1 to 10 of about 88 (85)

A series of lanthanide glutarates: lanthanide contraction effect on crystal frameworks of lanthanide glutarates

RSC Advances, 2017
Although some 3-D lanthanide glutarates have been reported, they exhibit a very robust structural type, whose structure is not changed by different Ln3+ions, but compound3shows a new structural type.
Jian Zhou, Lianshe Fu, Jian Zhou
exaly   +4 more sources

Conversion of lanthanide glutarate chlorides with interstitial THF into lanthanide glutarates with unprecedented topologies

Inorganica Chimica Acta, 2018
Abstract Using slow diffusion methods at room temperature (RT), we obtained four isomorphous lanthanide glutarate chlorides, accommodating interstitial THF and water molecules, [Ln2(Glut)2Cl2(H2O)8]·2H2O·THF (1–4), with Ln = La (1), Ce (2), Pr (3), Nd (4).
Matthias Zeller
exaly   +4 more sources

Glutaric Acidemia, Pathogenesis and Nutritional Therapy [PDF]

Frontiers in Nutrition, 2021
Glutaric acidemia (GA) are heterogeneous, genetic diseases that present with specific catabolic deficiencies of amino acid or fatty acid metabolism. The disorders can be divided into type I and type II by the occurrence of different types of recessive mutations of autosomal, metabolically important genes.
Qian Li, Chunlan Yang, Lijuan Feng, Yazi Zhao, Yong Su, Hong Liu, Hongkang Men, Yan Huang, Heinrich Körner, Xinming Wang, Xinming Wang   +10 more
openaire   +3 more sources

Essential lipid autacoids rewire mitochondrial energy efficiency in metabolic dysfunction‐associated fatty liver disease

Hepatology, EarlyView., 2022
Increased liver content of DHA‐derived small lipid autacoids (i.e resolvin D1 and maresin 1) associates with enhanced mitochondrial oxidative phosphorylation, fatty acid β‐oxidation and bioenergetic metabolic flux. These features provide hepatic protection from steatotic, pro‐inflammatory and fibrogenic insults.
Cristina López‐Vicario, David Sebastián, Mireia Casulleras, Marta Duran‐Güell, Roger Flores‐Costa, Ferran Aguilar, Juan José Lozano, Ingrid W. Zhang, Esther Titos, Jing X. Kang, Antonio Zorzano, Makoto Arita, Joan Clària   +12 more
wiley   +1 more source

Glutaric acidemia type 1 [PDF]

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, 2006
AbstractGlutaric acidemias comprise different disorders resulting in an increased urinary excretion of glutaric acid. Glutaric acidemia type 1 (GA‐1) is an autosomal recessive disorder of lysine, hydroxylysine, and tryptophan metabolism caused by deficiency of glutaryl‐CoA dehydrogenase.
Nicola Longo, Gary L. Hedlund, Marzia Pasquali   +2 more
openaire   +3 more sources

GLUTARIC ACIDURIA ‘TYPE II’ [PDF]

Pediatric Research, 1975
A new fetal metabolic disorder is described, mainly characterised by severe acidosis and hypoglycaemia, a' sweaty-feet' like odour, and massive glutaric aciduria and acidaemia. In addition, urinary excretion of isobutyric and isovaleric acid was increased, as well as that of some dicarboxylic acids.
Sybe K. Wadman, H. J. Bremer, H. Przyrembel, Udo Wendel   +3 more
openaire   +3 more sources

Significance of bound glutarate in the diagnosis of glutaric aciduria type I

Journal of Inherited Metabolic Disease, 1992
Glutaric aciduria type I (GA-I) (McKusick 231670) is an autosomal recessive disorder caused by glutaryl-CoA dehydro genase (GD) deficiency. The diagnosis of GA-I is determined by organic acid analysis of urine and is confirmed by measuring the enzyme activity in cultured skin fibroblasts or leukocytes.
Jaime Campistol, Antonia Ribes, Encarnació Riudor, Paz Briones, Ernst Christensen, David S. Millington   +5 more
openaire   +4 more sources

Mammalian Metabolism of Glutaric Acid

Journal of Biological Chemistry, 1969
Abstract Rat liver mitochondria metabolize glutarate at a very slow rate as compared with glutaryl coenzyme A. The stimulatory effect of citric acid cycle intermediates, NAD, and coenzyme A on glutarate metabolism was interpreted as a manifestation of their involvement in the activation of glutarate by a thiol transferase with succinyl-CoA as the ...
Carl E. Polan, Abraham Besrat, LaVell M. Henderson   +2 more
openaire   +3 more sources

Deliquescence and crystallization of ammonium sulfate‐glutaric acid and sodium chloride‐glutaric acid particles [PDF]

Geophysical Research Letters, 2004
In the following, we report the deliquescence relative humidities (DRH) and crystallization relative humidities (CRH) of mixed inorganic‐organic particles, specifically ammonium sulfate‐glutaric acid and sodium chloride‐glutaric acid particles. Knowledge of the DRH and CRH of mixed inorganic‐organic particles is crucial for predicting the role of ...
Parsons, Matthew T., Fok, Abel, Pant, Atul, Bertram, Allan K., Mak, Jackson   +4 more
openaire   +3 more sources

Characterization of the Cubamyces Menziesii Terpenome

ChemBioChem, EarlyView.
The genome of Cubamyces menziesii reveals 18 putative sesquiterpene cyclase genes. These genes are cloned and expressed in Escherichia coli, yielding 10 active enzymes. Using farnesyl diphosphate as substrate, the enzymes are analyzed, and the products characterized after bioconversion, uncovering diverse sesquiterpene structures. This study highlights
Létitia Leydet, Julie Couillaud, Agnès Amouric, Elise Courvoisier‐Dezord, Carole Avesque, Thierry Giardina, Mireille Attolini, Pierre Rousselot‐Pailley, Katia Duquesne, Marie‐Noelle Rosso, Gilles Iacazio   +10 more
wiley   +1 more source