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Liver transplantation for type IV glycogen storage disease [PDF]
, 1991 TYPE IV glycogen storage disease is a rare autosomal recessive disorder (also called Andersen's disease1 or amylopectinosis) in which the activity of branching enzyme alpha-1, 4-glucan: alpha-1, 4-glucan 6-glucosyltransferase is deficient in the liver as
Andreas Tzakis +17 more
core +1 more source
Hepatology Communications, 2019 Mutations in the liver glycogen phosphorylase (Pygl) gene are associated with the diagnosis of glycogen storage disease type VI (GSD‐VI). To understand the pathogenesis of GSD‐VI, we generated a mouse model with Pygl deficiency (Pygl−/−).
Lane H. Wilson +8 more
doaj +1 more source
Sleep and Wake Affect Glycogen Content and Turnover at Perisynaptic Astrocytic Processes
Frontiers in Cellular Neuroscience, 2018 Astrocytic glycogen represents the only form of glucose storage in the brain, and one of the outcomes of its breakdown is the production of lactate that can be used by neurons as an alternative energetic substrate.
Michele Bellesi +5 more
doaj +1 more source
Journal of Limnology, 2016 The success of Limnoperna fortunei as an invasive species is related to its physiological plasticity that allows them to endure adverse environmental conditions.
Nelmara I.S. Cordeiro +7 more
doaj +1 more source
Insects, 2019 Use of neonicotinoid pesticides is now ubiquitous, and consequently non-targeted arthropods are exposed to their residues at sub-lethal doses. Exposure to these neurotoxins may be a major contributor to poor honey bee colony health.
Steven C. Cook
doaj +1 more source
Molecules, 2012 Pumpkin (Cucurbita moschata) is a popular and nutritious vegetable consumed worldwide. The overall purpose of this study was to evaluate the effects of C.
Chia-Chung Hou +8 more
doaj +1 more source
Frontiers in Microbiology, 2023 Photosynthetic productivity is limited by low energy conversion efficiency in naturally evolved photosynthetic organisms, via multiple mechanisms that are not fully understood.
Michael Cantrell +6 more
doaj +1 more source
Contrast of nuclei in stratified squamous epithelium in optical coherence tomography images at 800 nm [PDF]
Journal of Biophotonics 2019, 2019 Imaging nuclei of keratinocytes in the stratified squamous epithelium has been a subject of intense research since nucleus associated cellular atypia is the key criteria for the screening and diagnosis of epithelial cancers and their precursors. However, keratinocyte nuclei have been reported to be either low scattering or high scattering, so that ...
arxiv +1 more source
Life, 2014 The cyAbrB2 transcriptional regulator is essential for active sugar catabolism in Synechocystis sp. PCC 6803 grown under light conditions. In the light-grown cyabrB2-disrupted mutant, glycogen granules and sugar phosphates corresponding to early steps ...
Masamitsu Hanai +7 more
doaj +1 more source
The Role of Muscle in Insect Energy Homeostasis
Frontiers in Physiology, 2020 Maintaining energy homeostasis is critical for ensuring proper growth and maximizing survival potential of all organisms. Here we review the role of somatic muscle in regulating energy homeostasis in insects.
Heidi Bretscher, Michael B. O’Connor
doaj +1 more source