Results 1 to 10 of about 245,598 (258)
AbstractGlycogen autophagy, which includes the sequestration and degradation of cell glycogen in the autophagic vacuoles, is a selective process under conditions of demand for the massive hepatic production of glucose, as in the postnatal period. It represents a link between autophagy and glycogen metabolism. The formation of autophagic vacuoles in the
Kotoulas, O. B. +2 more
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Ketotic hypoglycemia in patients with Down syndrome
Background Ketotic hypoglycemia (KH) without an identifiable underlying metabolic or hormonal disease is historically named idiopathic KH. The prevalence is unknown, but idiopathic KH is considered the most frequent cause of hypoglycemia beyond the ...
Danielle Drachmann +4 more
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Clinical practice guidelines for glycogen storage disease V & VII (McArdle disease and Tarui disease) from an international study group [PDF]
Supplementary material is available online at https://www.sciencedirect.com/science/article/pii/S0960896621006878#sec0054 .Highlights: • Management of physical activity intolerance in GSD V and GSD VII is nuanced and impacts activities of daily living (
Løkken, N +17 more
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This study aimed to determine the effects of flavored dairy milk based recovery beverages of different nutrition compositions on markers of gastrointestinal and immune status, and subsequent recovery optimisation markers.
Isabella Russo +6 more
doaj +1 more source
Photosynthetic productivity is limited by low energy conversion efficiency in naturally evolved photosynthetic organisms, via multiple mechanisms that are not fully understood.
Michael Cantrell +6 more
doaj +1 more source
Incorporation of phosphate into glycogen by glycogen synthase [PDF]
The storage polymer glycogen normally contains small amounts of covalently attached phosphate as phosphomonoesters at C2, C3 and C6 atoms of glucose residues. In the absence of the laforin phosphatase, as in the rare childhood epilepsy Lafora disease, the phosphorylation level is elevated and is associated with abnormal glycogen structure that ...
Christopher J. Contreras +7 more
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Glycogen Metabolism in Glycogen-rich Erythrocytes [PDF]
Abstract High concentrations of red blood cell glycogen were visualized by electron microscopy and demonstrated biochemically in amylo-1,6-glucosidase- and phosphorylase-deficient red blood cells. Glycogen concentration decreased as a function of cell age.
S W, Moses +3 more
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Glycogen metabolism and glycogen storage disorders [PDF]
Glucose is the main energy fuel for the human brain. Maintenance of glucose homeostasis is therefore, crucial to meet cellular energy demands in both - normal physiological states and during stress or increased demands. Glucose is stored as glycogen primarily in the liver and skeletal muscle with a small amount stored in the brain.
Shibani, Kanungo +3 more
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The polymorphic fungus Candida albicans remains a leading cause of both invasive and superficial mycoses, including vulvovaginal candidiasis (VVC). Metabolic plasticity, including carbohydrate catabolism, confers fitness advantages at anatomical site ...
Jian Miao +6 more
doaj +1 more source
Action Patterns of Phosphorylase and Glycogen Synthetase on Glycogen [PDF]
The action patterns of liver and muscle glycogen synthetases and of muscle phosphorylase b on glycogen samples of different molecular weight and on β‐amylase limit dextrins were studied. For this purpose a method for measuring the number of newly added glucose residues that are at non‐reducing ends was developed.It was found that glucose transfer to ...
Parodi, Armando José A. +3 more
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