Results 211 to 220 of about 6,177 (249)

Apparent absence of glycogen branching enzyme activity in phosphofructokinase deficiency

Journal of Inherited Metabolic Disease, 1991
SummaryA 30‐year‐old woman with clinical features and biochemical findings of muscle phosphofructokinase deficiency was found to have a very low level of α‐1,4‐glucan:α‐1,4‐glucan‐6‐transglucosylase (branching enzyme, EC 2.4.1.18) activity in muscle. In contrast, branching enzyme activity in the leukocytes was in the range of control values.
V, Barash, S, Lilling, R, Fischer, Z, Argov   +3 more
openaire   +2 more sources

Differentiated structure of synthetic glycogen-like particle by the combined action of glycogen branching enzymes and amylosucrase

International Journal of Biological Macromolecules, 2022
Glycogen-like particles (GLPs) were built up from sucrose by applying de novo one-pot enzymatic process of amylosucrase (ASase; 6 U·mL-1) and glycogen branching enzymes (GBEs; 0.001 and 0.005 U·mL-1). Due to different chain-length transferring patterns of GBEs, structurally differentiated GLPs were synthesized.
Daeyeon, Lee, Sang-Dong, Park, Su-Jin, Jun, Jong-Tae, Park, Pahn-Shick, Chang, Sang-Ho, Yoo   +5 more
openaire   +2 more sources

The glgB-encoded glycogen branching enzyme is essential for glycogen accumulation in Corynebacterium glutamicum

Microbiology, 2011
Corynebacterium glutamicum transiently accumulates glycogen as carbon capacitor during the early exponential growth phase in media containing carbohydrates. In some bacteria glycogen is synthesized by the consecutive action of ADP-glucose pyrophosphorylase (GlgC), glycogen synthase (GlgA) and glycogen branching enzyme (GlgB).
Gerd M, Seibold, Katrin J, Breitinger, Raoul, Kempkes, Leonard, Both, Matthias, Krämer, Stefan, Dempf, Bernhard J, Eikmanns   +6 more
openaire   +2 more sources

Glycogen brain branching enzyme.

Cellular and molecular biology (Noisy-le-Grand, France), 1998
Rat brain glycogen branching enzyme was partially purified in order to elucidate its mechanism of action. The alpha1,4-alpha1,6-glucan polysaccharide was synthesized using rat brain branching enzyme under two different elongation conditions: Glc-1-P and phosphorylase or UDP-Glc and glycogen synthase.
D S, Tolmasky, C, Labriola, C R, Krisman
openaire   +1 more source

Production of highly branched α-limit dextrins with enhanced slow digestibility by various glycogen-branching enzymes

Carbohydrate Polymers, 2023
α-Limit dextrins (α-LDx) are slowly digestible carbohydrates that attenuate postprandial glycemic response and trigger the secretion of satiety-related hormones. In this study, more highly branched α-LDx were enzymatically synthesized to enhance the slowly digestible property by various origins of glycogen branching enzyme (GBE), which catalyzes the ...
Ye-Eun, Shim, Young-Bo, Song, Sang-Ho, Yoo, Byung-Hoo, Lee   +3 more
openaire   +2 more sources

Characterization of the branching patterns of glycogen branching enzyme truncated on the N-terminus

Archives of Biochemistry and Biophysics, 2003
Truncation of 112 amino acids at the N-terminus (Nd(1-112)) changes the chain transfer pattern of the Escherichia coli glycogen branching enzyme (GBE) [Arch. Biochem. Biophys. 397 (2002) 279]. We investigated further the role of the N-terminus by engineering other truncated GBEs and analyzing the branching pattern by high-performance anion-exchange ...
Claire H, Devillers, Mary E, Piper, Miguel A, Ballicora, Jack, Preiss   +3 more
openaire   +2 more sources

Neonatal type IV glycogen storage disease associated with “null” mutations in glycogen branching enzyme 1

The Journal of Pediatrics, 2004
The fatal neonatal form of type IV glycogen storage disease (GSD IV) was diagnosed on light and electron microscopy and by analysis of GBE1 , the gene encoding glycogen branching enzyme. We report two novel truncating mutations, as well as the first genomic mutational analysis of GBE1 using denaturing high performance liquid chromatography.
Janecke, Andreas R., Dertinger, Susanne, Ketelsen, Uwe-Peter, Bereuter, Lothar, Simma, Burkhard, Müller, Thomas F., Vogel, Wolfgang, Offner, Felix A.   +7 more
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New approach to prepare fluorogenic branched dextrins for assaying glycogen debranching enzyme

Glycoconjugate Journal, 2020
Glycogen debranching enzyme (GDE), together with glycogen phosphorylase (GP), is responsible for the complete degradation of glycogen. GDE has distinct catalytic sites for 4-α-glucanotransferase and amylo-α-1,6-glucosidase. For the GDE sensitive assay, we previously developed the GP limit fluorogenic branched dextrin Glcα1-4Glcα1-4Glcα1-4Glcα1-4(Glcα1 ...
Miyu Sakaguchi, Yasushi Makino, Hiroshi Matsubara   +2 more
openaire   +2 more sources

Human Skeletal Muscle Glycogen Branching Enzyme Activities with Exercise and Training

Canadian Journal of Physiology and Pharmacology, 1974
Sixteen healthy male subjects classified as sedentary (8) or active (8), exercised to exhaustion on a bicycle ergometer at a load requiring 70% of their maximal aerobic capacity. Biopsy samples of the vastus lateralis muscle were taken at rest and at the time of fatigue.
A W, Taylor, J, Stothart, M A, Booth, R, Thayer, S, Rao   +4 more
openaire   +2 more sources

Glycogen Synthetase (and Branching Enzyme)

1975
The second enzyme capable of the synthesis of α-1,4 linkages of glycogen is glycogen synthetase*. Unlike phosphorylase, it is synthetic both in vitro and in vivo, it seems to have similar properties in all tissues including CNS, and can not degrade glycogen; it is now proved to be the only synthetic enzyme under normal in vivo conditions.
openaire   +1 more source