Results 21 to 30 of about 18,669 (233)
Causes of death and mortality trends related to hemophilia in Brazil, 1999 to 2016
Hematology, Transfusion and Cell Therapy, 2021 Introduction: Multiple cause of death methodology enhances mortality studies beyond the traditional underlying cause of death approach. Aim: This study aims to describe causes of death and mortality issues related to haemophilia with the use of multiple ...
Augusto Hasiak Santo
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JMS SKIMS, 2016 Haemophilia is a group of inherited blood disorders in which blood does not clot properly. Bleeding disorders are due to defect in blood vessels, the coagulation mechanism or the blood platelets. Blood coagulation mechanism is a process which transforms blood from a liquid into solid and involves different clotting factors that generates fibrin fibers ...
Sabita Yograj, Neena Sharma
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Orphanet Journal of Rare Diseases, 2022 Background Gene therapy has the potential to change the life experience of people with haemophilia and family members. Few studies have sought to explore the impact of gene therapy on both individuals and families.
Simon Fletcher +4 more
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Scientific Reports, 2017 Haemophilia B, a congenital haemorrhagic disease caused by mutations in coagulation factor IX gene (F9), is considered an appropriate target for genome editing technology.
Tsukasa Ohmori +10 more
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Seroprevalence of Hepatitis B and Hepatitis C in People with Haemophilia at a Tertiary Care Centre, Assam, India: A Cross-sectional Study [PDF]
Journal of Clinical and Diagnostic ResearchIntroduction: Prior to the advent of recombinant factor products, the treatment of haemophilia was mainly based on the administration of direct blood products like whole blood, Fresh Frozen Plasma (FFP), and cryoprecipitates. This led to a high incidence
Anupam Dutta +2 more
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Gene therapy in haemophilia: literature review and regional perspectives for Turkey
Therapeutic Advances in Hematology, 2022 Haemophilia is an X-linked lifelong congenital bleeding disorder that is caused by insufficient levels of factor VIII (FVIII; haemophilia A) or factor IX (FIX; haemophilia B) and characterized by spontaneous and trauma-related bleeding episodes.
Kaan Kavaklı +9 more
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Prevention of spontaneous bleeding in dogs with haemophilia A and haemophilia B
Haemophilia, 2010 Summary. Dogs with haemophilia A or haemophilia B exhibit spontaneous bleeding comparable with the spontaneous bleeding phenotype that occurs in humans with severe haemophilia. The phenotypic and genotypic characteristics of haemophilic dogs have been well‐described, and such dogs are suitable for testing prophylactic protein replacement therapy and ...
T C, Nichols +9 more
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PERAWATAN GIGI DAN MULUT PENDERITA HEMOFILIA
Journal of Dentistry Indonesia, 2015 Haemophilia is a congenital haemorrhagic disorders passed down by the x linked recessive, divided into two: Haemophilia A caused by deficiency of factor VIII and Haemophilia B caused by deficiency of factor IX.
Siti Marhamah
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Intracranial haemorrhage in haemophilia A and B [PDF]
British Journal of Haematology, 2007 SummaryIn countries with a good standard of health care, intracranial haemorrhage (ICH) during the neonatal period affects 3·5–4·0% of all haemophilia boys, which is considerably (40–80 times) higher than expected in the normal population. ICHs are also frequent after the neonatal period, affecting 3–10% of the haemophilia population who are mainly ...
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An Update on Laboratory Diagnostics in Haemophilia A and B
Hämostaseologie, 2022 AbstractHaemophilia A (HA) and B (HB) are X-linked hereditary bleeding disorders caused by lack of activity of coagulation factors VIII (FVIII) or IX (FIX), respectively. Besides conventional products, modern replacement therapies include FVIII or FIX concentrates with an extended half-life (EHL-FVIII/FIX).
Müller, Jens +5 more
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