Gamma heavy chain disease: a retrospective analysis of 6 cases [PDF]
Orphanet Journal of Rare Diseases, 2023 Long Chang, Dao-bin Zhou, Xin-xin Cao
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Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. [PDF]
Mediterranean Journal of Hematology and Infectious Diseases, 2023 Heavy chain diseases are rare B-cell neoplasms consisting of the production of a monoclonal immunoglobulin composed of the only heavy chain without corresponding light chains.
Maria Laura Bisegna +5 more
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Mu heavy chain disease with MYD88 L265P mutation: an unusual manifestation of lymphoplasmacytic lymphoma [PDF]
Diagnostic Pathology, 2022 Background Mu heavy chain disease is a rare lymphoid neoplasm characterized by vacuolated bone marrow plasma cells and secretion of defective mu immunoglobulin heavy chains. The biological basis of mu heavy chain disease is poorly understood.
Vandana Baloda +9 more
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Gamma heavy chain disease associated with rheumatoid arthritis: a case report [PDF]
Journal of Medical Case Reports, 2021 Background Gamma heavy chain disease (γ-HCD) is a monoclonal gammopathy defined by an abnormal clonal and isolated production of incomplete heavy chain gamma (γ), unable to bind with light chains kappa or lambda.
Gwenvaël Danic +5 more
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Blood, 2019 ![Figure][1] A 78-year-old woman from Sudan with presumed tuberculous lymphadenitis without preexisting autoimmune disease presented with fatigue, persistent fever, hepatosplenomegaly, and generalized lymphadenopathy.
Vidya, Nagrale, Lois, Richard
openaire +3 more sources
Two Cases of γ-Heavy Chain Disease and a Review of the Literature [PDF]
Case Reports in Hematology, 2018 Gamma heavy chain disease (γ-HCD) is a rare lymphoproliferative disorder characterised by the production of a truncated immunoglobulin heavy chain. Fewer than 200 cases have been reported in the literature. In some cases, γ-HCD occurs with other lymphoid
I. Ramasamy, Z. Rudzki
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A case of heavy-chain deposition disease with good long-term renal survival and a literature review [PDF]
BMC NephrologyBackground Monoclonal immunoglobulin deposition disease (MIDD) is characterized by the deposition of nonamyloid monoclonal immunoglobulin and its free fragment light chain and/or heavy chain in systemic tissues and organs, and the kidney is most ...
Xiaoqing Cai +4 more
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Monoclonal Gammopathy of Renal Significance with Deposits of Infrequent Morphology: Two Case Reports of Light and Heavy Chain Deposition Disease with Atypical Presentation and Literature Review [PDF]
Medicines, 2023 Background: Monoclonal immunoglobulin deposition disease (MIDD) includes three entities: light chain deposition disease (LCDD), heavy chain deposition disease (HCDD) and light and heavy chain deposition disease (LHCDD).
José C. De La Flor +10 more
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Gamma heavy-chain disease presenting with hypercalcaemia and ascites
European Journal of Case Reports in Internal MedicineGamma heavy-chain disease (gHCD) is a rare lymphoproliferative disorder characterised by the production of truncated gamma heavy chains that are not associated with light chains.
Imane El Boutahiri +3 more
doaj +3 more sources
Acta Medica LituanicaHeavy chain diseases (HCDs) are rare B-cell/plasma cell disorders characterized by secretion of truncated immunoglobulin heavy chains without light chains. Pulmonary involvement has been described but is typically limited to interstitial or infiltrative
Konstantinos Dodos +2 more
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