La hemofilia adquirida es un trastorno hemostático causado por la presencia de autoanticuerpos inhibidores contra el F VIII de la coagulación. Clínicamente se presenta como sangrado espontáneo, principalmente en piel y tejidos blandos, y a diferencia de la hemofilia congénita, la hemartrosis es rara.
Alexis Antonio Benítez Espinola +2 more
core +6 more sources
Prevalencia de la hemofilia a en la provincia Bolívar
Introducción: la hemofilia es un trastorno hereditario que se caracteriza por la deficiencia de los factores de coagulación, las deficiencias del factor VIII (Hemofilia A) y del factor IX (Hemofilia B) son una de las patologías más frecuentes y conocidas
Génesis Alejandra Castro Naranjo +1 more
semanticscholar +3 more sources
Variabilitas Pola Perdarahan Anak Hemofilia A yang Mendapat Terapi On-demand di Rumah Sakit Cipto Mangunkusumo [PDF]
Latar belakang. Gejala perdarahan pada hemofilia A bergantung pada kadar faktor VIII, namun pada kadar faktor koagulasi yang sama dapat terjadi perbedaan karakteristik dan luaran klinis. Tujuan.
Novie Amelia Chozie +2 more
doaj +2 more sources
Perdarahan Intrakranial pada Hemofilia: Karakteristik, Tata Laksana, dan Luaran
Latar belakang. Perdarahan intrakranial merupakan salah satu penyebab mortalitas tertinggi pada hemofilia dan morbiditas berupa gangguan neurologis.
Novie Amelia C +3 more
doaj +2 more sources
Effectiveness of progressive moderate-vigorous intensity elastic resistance training on quality of life and perceived functional abilities in people with hemophilia: Secondary analysis of a randomized controlled trial. [PDF]
Abstract Introduction and Aim Strength exercise training is advised for people with hemophilia (PWH); however, few studies have been published and have methodological limitations. The purpose of this study was to evaluate the effectiveness of progressive elastic resistance training on quality of life and perceived functional abilities in PWH.
Cruz-Montecinos C +9 more
europepmc +2 more sources
Hemofilia A neonatal: reporte de un caso en Sincelejo (Colombia)
La hemofilia es una enfermedad hemorrágica hereditaria caracterizada por la deficiencia funcional o cuantitativa del factor VIII (hemofilia A ) o del factor IX (hemofilia B ) de la coagulación.
Jorge Mendoza-Herrera +3 more
doaj +3 more sources
Prophylaxis and hemophilia care in LATAM: Baring it all-Highlights from the CLAHT 2021 symposium. [PDF]
Abstract A large group of countries constitute Latin American (LATAM) countries, where hemophilia care is as varied as the landscape of this region. To better understand the care provided to persons with bleeding disorders, especially hemophilia, a symposium was organized as part of the CLAHT Congress 2021 in Colombia to highlight the issues of ...
DiMinno GG +6 more
europepmc +2 more sources
Genética comunitária e hemofilia em uma população brasileira
A hemofilia é uma doença hemorrágica importante no Brasil, afetando cerca de um em cada dez mil indivíduos do sexo masculino. A autopercepção do portador a respeito da hemofilia e a sua interação com a comunidade são relevantes na abordagem clínica dessa
Caio Vânia Maria +3 more
doaj +1 more source
Safety and Efficacy of Damoctocog Alfa Pegol in Previously Treated Children Aged 7 to < 12 Years With Severe Haemophilia A in the Phase 3, Open Label Alfa-PROTECT Main Study. [PDF]
ABSTRACT Background In the earlier PROTECT VIII Kids study (NCT01775618), damoctocog alfa pegol was efficacious for prevention and treatment of bleeds in children aged < 12 years with severe haemophilia A. Objective Assess the safety of damoctocog alfa pegol, including hypersensitivity and loss of efficacy (LoE) due to an immune response to ...
Ozelo MC +13 more
europepmc +2 more sources

