Results 31 to 40 of about 16,441 (215)
Journal of Cancer Research and Practice, 2017 Hemophagocytic lymphohistiocytosis (HLH) is a rare clinical syndrome characterized by excessive macrophage function. The diagnosis of HLH in adults is challenging because initial signs and symptoms of HLH mimic common infections.
I-Hsuan Huang +2 more
doaj +1 more source
AIDS Research and Therapy, 2020 Background AIDS-related KS generally involves cutaneous lesions, that slowly progress over months to years. Neither rapidly progressing of KS nor KS complicated with hemophagocytic syndrome (HPS) has rarely been reported.
Pingzheng Mo +4 more
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Hemophagocytic Syndromes and Infection [PDF]
Emerging Infectious Diseases, 2000 Hemophagocytic lymphohistiocytosis (HLH) is an unusual syndrome characterized by fever, splenomegaly, jaundice, and the pathologic finding of hemophagocytosis (phagocytosis by macrophages of erythrocytes, leukocytes, platelets, and their precursors) in bone marrow and other tissues.
openaire +3 more sources
Heliyon, 2023 Hemophagocytic Lymphohistiocytosis (HLH) is an uncommon, diverse and rare genetic hyper-inflammatory syndrome. HLH associated with tuberculosis (TB-HLH) has been described as a clinical and diagnostic quandary.
Disha Gautam +5 more
doaj +1 more source
Approach to Hemophagocytic Syndromes [PDF]
Hematology, 2011 AbstractHemophagocytic lymphohistiocytosis (HLH) is a potentially fatal hyperinflammatory condition. It may occur as a primary (genetic) condition due to mutations in genes important in the cytolytic secretory pathway that cause perforin and granzymes to induce apoptosis in target cells.
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Hemophagocytic Syndrome in Children and Adults [PDF]
Archivum Immunologiae et Therapiae Experimentalis, 2014 Hemophagocytic syndrome, also known as hemophagocytic lymphohistiocytosis (HLH), is a heterogenic syndrome, which leads to an acute, life-threatening inflammatory reaction. HLH occurs both in children and adults, and can be triggered by various inherited as well as acquired factors.
Malinowska, Iwona +5 more
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Haematologica, 2015 The hyperinflammatory syndrome hemophagocytic lymphohistiocytosis can occur in the context of malignancies. Malignancy-triggered hemophagocytic lymphohistiocytosis should be regarded seperately from hemophagocytic lymphohistiocytosis during ...
Kai Lehmberg +9 more
doaj +1 more source
Disseminated Mycobacterium Kansasii Infection Associated with Hemophagocytic Syndrome
, 2011 Disseminated infections with hemophagocytic syndrome caused by non- tuberculous mycobacteria (NTM) are rare. A 60-year- old woman, who presented with fever, chills, anorexia, and right upper quadrant pain, was admitted to our hospital. Hepatosplenomegaly,
CHOU, YU-HSIANG;HSU, MENG-SHIUAN;SHENG, WANG-HUEI;CHANG, SHAN-CHWEN +1 more
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, 2010 Background: Familial hemophagocytosis (FHL) is a rare disease associated with defects in proteins involved in CD8+ T-cell cytotoxicity. Hyperactivation of immune cells results in a perilous, Th1-driven cytokine storm. We set out to explore the regulation
Nold Marcel F. +23 more
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The Role of Hematopoietic Cell Transplantation in Ataxia‐Telangiectasia
Pediatric Blood &Cancer, EarlyView.ABSTRACT Background Ataxia‐telangiectasia (A‐T) is a DNA repair disorder characterized by neurodegeneration, immunodeficiency, and cancer predisposition. Hematopoietic cell transplantation (HCT) is an established therapy in related disorders such as Fanconi anemia (FA) and Nijmegen breakage syndrome (NBS), but its role in A‐T is unclear.
Laila Alkhouli +3 more
wiley +1 more source