Results 31 to 40 of about 6,796 (202)

HEMOPHAGOCYTOSIS SECONDARY TO PHARYNGEAL ABSCESS IN AN IMMUNOCOMPETENT PATIENT (case report) [PDF]

, 2018
Background. Hemophagocytosis is a rare, potentially fatal disorder, comprising pancytopenia, liver dysfunction, hepatosplenomegaly, hypertriglyceridemia, and hyperferritinemia presenting as fever, lympha­denopathy and skin rashes. Objective.
Khan, S., Malik, M., Gupta, S., Sawarat, E., Khan, I. D., Banerjee, P., Gazala, S., Rajmohan, K. S., Brijwal, M., Aguinaga, M. S., Panda, P. S., Kahkasha, K.   +11 more
core   +1 more source

A Multifaceted Interplay Among Hemophagocytosis, Interleukin-18, and Type I Interferon Distinguishes Still Disease From Other Autoinflammatory Diseases. [PDF]

Arthritis Rheumatol
Objective The unknown pathophysiology and the lack of specific features for systemic juvenile idiopathic arthritis and adult‐onset Still disease (collectively known as Still disease; SD) delay diagnosis and appropriate treatment. The goal of this study was to identify features and mechanisms that distinguish SD from other systemic autoinflammatory ...
Mueller YM, Girard C, van de Werken HJG, Erkeland SJ, Grashof DGB, Vaillant L, den Dekker RJH, van Zuijen I, Veenbergen S, Coffin F, Bindels E, Jamilloux Y, Laskari K, Soumelis V, Fautrel B, Gabay C, Katsikis PD.   +16 more
europepmc   +2 more sources

Hemophagocytic Syndromes and Infection

Emerging Infectious Diseases, 2000
Hemophagocytic lymphohistiocytosis (HLH) is an unusual syndrome characterized by fever, splenomegaly, jaundice, and the pathologic finding of hemophagocytosis (phagocytosis by macrophages of erythrocytes, leukocytes, platelets, and their precursors) in ...
David N. Fisman
doaj   +1 more source

Dengue Virus-Associated Hemophagocytic Syndrome and Dyserythropoiesis: A Case Report

Kaohsiung Journal of Medical Sciences, 2005
A 33-year-old man had dengue hemorrhagic fever with initial presentation of fever, leukocytosis, and thrombocytopenia. The cause of the subsequent rapid decline in red cell counts without evidence of intravascular hemolysis or massive bleeding was ...
Po-Liang Lu, Hui-Hwa Hsiao, Jih-Jin Tsai, Tun-Chieh Chen, Tyen-Po Chen, Sheng-Fung Lin   +5 more
doaj   +1 more source

Intravascular Lymphoma as an Uncommon Cause of Anasarca

European Journal of Case Reports in Internal Medicine, 2016
Objectives: To report a case of intravascular lymphoma (IVL) in a Caucasian patient who presented with anasarca as his sole clinical sign. Material and Methods: A man presented with anasarca-type oedema and fatigue.
Eleni Mylona, Styliani Golfinopoulou, Pelagia Sfakianaki, George Kyriakopoulos, Ioannis Tsonis, Theofanis Apostolou, Christina Vourlakou, Athanasios Skoutelis   +7 more
doaj   +1 more source

Precision immunomodulation for pediatric hemophagocytic lymphohistiocytosis in intensive care

Pediatric Investigation, EarlyView.
This review presents a bedside framework for recognizing pediatric hemophagocytic lymphohistiocytosis and cytokine storm, stabilizing organ dysfunction, identifying the underlying phenotype, selecting targeted immunomodulation, considering extracorporeal adjuncts, and reassessing response within 24–72 h. ABSTRACT Hemophagocytic lymphohistiocytosis (HLH)
Weerapong Lilitwat, Prakreeti Bhandari
wiley   +1 more source

Primary Cutaneous Gamma‐Delta T‐Cell Lymphoma Complicating Long‐Standing Immunosuppressed Dermatomyositis

Journal of Cutaneous Pathology, EarlyView.
ABSTRACT Primary cutaneous gamma‐delta T‐cell lymphoma (PCGD‐TCL) is a rare cytotoxic lymphoma with key oncogenic drivers in the JAK/STAT pathway. Also primarily involving the subcutaneous adipose tissue, subcutaneous panniculitis‐like T‐cell lymphoma (SPTCL) is more frequently encountered in scenarios of autoimmune disorders.
Bennett Christie‐Nguyen, Youn H. Kim, David F. Fiorentino, Danielle Tartar, Ryanne Brown, Robert A. Novoa, Kerri E. Rieger   +6 more
wiley   +1 more source

Cutaneous lymphomas – an update

Histopathology, EarlyView.
Primary cutaneous lymphomas and lymphoproliferative disorders are defined by integrated clinical, histopathological, immunophenotypic and genetic features as diagnostic criteria also in the 5th edition of the WHO classification of haematolymphoid tumors.
Werner Kempf, Christina Mitteldorf
wiley   +1 more source

ICSH Guidance on Bone Marrow Examination and Reporting

International Journal of Laboratory Hematology, EarlyView.
ABSTRACT Examination of the bone marrow (BM) remains fundamental to the diagnosis, classification, prognostication, and monitoring of hematolymphoid and other disorders affecting blood cell production. Since publication of the International Council for Standardization in Haematology (ICSH) guideline in 2008, advances in diagnostic technologies, disease
Wendy N. Erber, Alexandar Tzankov, Olga Pozdnyakova, Hiromichi Matsushita, Gina Zini, Leonie Saft, on behalf of the International Council for Standardization in Haematology   +6 more
wiley   +1 more source

Pure Erythroid Leukemia with Hemophagocytosis

Internal Medicine, 2009
A 53-year-old man was admitted with pancytopenia, fever and splenomegaly. Biochemistry showed increased ferritin levels. Bone marrow examination revealed increased erythrocytic precursors (94.9%) and active hemophagocytosis. Pure erythroid leukemia with hemophagocytic syndrome (HPS) was diagnosed.
Kitagawa, Junichi, Hara, Takeshi, Tsurumi, Hisashi, Oyama, Masami, Moriwaki, Hisataka   +4 more
openaire   +3 more sources