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Hereditary angioedema [PDF]

International Journal of Emergency Medicine, 2021
A 14-year-old African American female presented to the emergency department with spontaneous, sudden-onset lip swelling for 1 h. On examination, there was significant water-bag edema of the upper lip extending to the philtrum and premaxilla ...
Helen Lesser, Jason E. Cohn
doaj   +4 more sources

Idiopathic Thrombocytopenic Purpura Misdiagnosed as Hereditary Angioedema [PDF]

Case Reports in Dermatological Medicine, 2015
Hereditary angioedema is a rare, but potentially life-threatening genetic disorder that results from an autosomal dominant trait. It is characterized by acute, recurrent attacks of severe local edema, most commonly affecting the skin and mucosa. Swelling
Michelle Fog Andersen, Anette Bygum
doaj   +6 more sources

The international WAO/EAACI guideline for the management of hereditary angioedema – the 2017 revision and update [PDF]

Allergy. European Journal of Allergy and Clinical Immunology, 2018
Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and appropriate therapy are essential. This update and revision of the global guideline for HAE provides up-to-date consensus recommendations for the management of HAE.
Aabom, Abdel-Karim, Agostoni, Alexander Nast, Anete S. Grumach, Antonio, Aygoren-Pursun, Aygoren-Pursun, Banerji, Banerji, Banta, Bas, Bas, Berkel, Bernstein, Bernstein, Bernstein, Bernstein, Betschel, Binkley, Black, Blackmore, Blohme, Boccon-Gibod, Bonnekoh, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bouillet, Bouillet, Bouillet, Bouillet, Bowen, Bowen, Bowen, Bowen, Boyle, Brackertz, Brozek, Brozek, Bruce Ritchie, Bruce Zuraw, Brunskill, Bygum, Bygum, Caballero, Caballero, Caballero, Caballero, Caballero, Caballero, Caldwell, Caliskaner, Christiansen, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Constance Katelaris, Craig, Craig, Craig, Craig, Craig, Craig, Craig, Cronin, Crowther, Czaller, de Maat, de Rojas Hernandez Fernandez, De Serres, Dewald, Dinkelacker, Donaldson, Donaldson, Donaldson, Dumitru Moldovan, Emel Aygören-Pürsün, Erikson, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farrell, Fernando, Fields, Forrest, Fox, Frank, Frank, Fust, Galan, Germenis, Gilad, Gobert, Gompels, Gonzalez-Quevedo, Gorman, Greve, Grumach, Guyatt, Halbmayer, Hedner, Henriette Farkas, Henrik Balle Boysen, Hilary Longhurst, Hochberg, Hofstra, Ignacio Ansotegui, Inmaculada Martinez-Saguer, Jacques, Jurado-Palomo, Kalaria, Kaplan, Kaplan, Kaplan, Karim, Kohalmi, Konrad Bork, Kreuz, Kunschak, Lang, Lanny Rosenwasser, Levy, Li, Longhurst, Longhurst, Longhurst, Lopez-Lera, Lumry, Lumry, Lumry, Magerl, Magerl, Magerl, Marc Riedl, Marcus Maurer, Mario Sánchez-Borges, Markus Magerl, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Maurer, Maurer, Maurer, Michihiro Hide, Moldovan, Moldovan, Muhlberg, Nanda, Nasr, Nathani, Nielsen, Nussberger, Ogston, Pappalardo, Pappalardo, Paul Potter, Pedrosa, Peveling-Oberhag, Rahal, Rasmussen, Reshef, Richard Lockey, Riedl, Riedl, Riedl, Riedl, Rocha, Rosen, Rosen, Ruby Pawankar, Saule, Schreiber, Schulz, Sheffer, Sheffer, Spath, Speletas, Staubach, Stephen Betschel, Tarzi, Terpstra, Thoufeeq, Timothy Craig, Toh, Tom Bowen, Tourangeau, Tuong, van Doorn, van Veen, Visy, Waytes, Weiler, Wentz, Whalley, Whalley, William R. Lumry, Wilson, Wu, Yuxiang Zhi, Zanichelli, Zanichelli, Zanichelli, Zilberberg, Zotter, Zotter, Zotter, Zuberbier, Zuraw, Zuraw, Zuraw, Zuraw, Zuraw, Zuraw, Ärzteschaft   +238 more
core   +3 more sources

New treatments addressing the pathophysiology of hereditary angioedema [PDF]

Clinical and Molecular Allergy, 2008
Hereditary angioedema is a serious medical condition caused by a deficiency of C1-inhibitor. The condition is the result of a defect in the gene controlling the synthesis of C1-inhibitor, which regulates the activity of a number of plasma cascade systems.
Davis Alvin E
doaj   +2 more sources

Prediction of hereditary angioedema during attacks in patients with recurrent angioedema: Awareness at a glance with the hereditary angioedema prediction score [PDF]

Clinical and Translational Allergy
Background/Aim Misdiagnosis of hereditary angioedema (HAE) leads to inappropriate management of the attacks. A scoring system that anticipates diagnosis can be beneficial for clinicians who are unfamiliar with angioedema.
Semra Demir, Müge Olgaç, Osman Ozan Yeğit, İlkim Deniz Toprak, Mehmet Erdem Çakmak, Merve İğde Hormet, Nida Öztop, Pelin Korkmaz, Şule Kamacı Çelik, Deniz Eyice Karabacak, Nevzat Kahveci, Işıl Göğem İmren, Bircan Erden, Raif Coşkun, Pelin Karadağ, Derya Ünal, Aslı Gelincik   +16 more
doaj   +2 more sources

Effect of Fresh Frozen Plasma Infusion on Hospital Length of Stay for Patients With Hereditary Angioedema [PDF]

Journal of Health Economics and Outcomes Research
# Background Patients with hereditary angioedema treated with fresh frozen plasma (FFP) infusion face complications and risk of side effects. # Objective To study the effect of FFP infusion on hospital length of stay for patients with hereditary ...
Subhan Khalid, Alan T. Hitch
doaj   +3 more sources

Treatment of hereditary angioedema with plasma-derived C1 inhibitor

Therapeutics and Clinical Risk Management, 2008
Michael J Prematta, Tracy Prematta, Timothy J CraigSection of Allergy and Immunology, Penn State University, Milton S. Hershey Medical Center, PA, USABackground: Plasma-derived C1 inhibitor (C1-INH) concentrate is a treatment option for acute hereditary ...
Michael J Prematta, Tracy Prematta, Timothy J Craig   +2 more
doaj   +3 more sources

Elevated level of circulating VEGF in Chinese patients with hereditary angioedema and its correlation with disease status [PDF]

Orphanet Journal of Rare Diseases
Background Hereditary angioedema (HAE) is a rare inherited disease characterized by recurrent, potentially life-threatening angioedema. The vascular endothelium dysfunction is reported to play a role in angioedema episodes.
Ruoyu Ji, Yijing Xu, Yuxiang Zhi
doaj   +2 more sources

Peri-operative management of a pregnant patient with hereditary angioedema submitted to a cesarean-section: case report [PDF]

Revista Brasileira de Anestesiologia, 2020
Hereditary angioedema is an autosomal dominant disorder, presenting as sudden and recurring episodes of variable severity of subcutaneous and mucosa edema that may occur spontaneously or in response to triggers.
Teresa Maria Ramos Nunes Estevens, Angel Serrano, Solange Amaro, João Ribeiro   +3 more
doaj   +5 more sources

The international WAO/EAACI guideline for the management of hereditary angioedema – The 2021 revision and update

The World Allergy Organization Journal, 2022
Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and appropriate therapy are essential. This update and revision of the global guideline for HAE provides up-to-date consensus recommendations for the management of HAE.
M. Maurer, M. Magerl, S. Betschel, W. Aberer, I. Ansotegui, E. Aygören‐Pürsün, A. Banerji, N. Bara, I. Boccon-Gibod, K. Bork, L. Bouillet, H. Boysen, N. Brodszki, P. Busse, A. Bygum, T. Caballero, M. Cancian, A. Castaldo, D. Cohn, D. Csuka, H. Farkas, M. Gompels, R. Gower, A. Grumach, G. Guidos-Fogelbach, M. Hide, H. Kang, A. Kaplan, C. Katelaris, S. Kiani-Alikhan, Wei‐Te Lei, R. Lockey, H. Longhurst, W. Lumry, A. MacGinnitie, A. Malbrán, I. Martinez Saguer, J. M. Matta Campos, A. Nast, D. Nguyen, S. Nieto‐Martinez, R. Pawankar, J. Peter, G. Porębski, N. Prior, A. Reshef, M. Riedl, B. Ritchie, Farrukh R. Sheikh, William B. Smith, P. Spaeth, M. Stobiecki, E. Toubi, L. Varga, K. Weller, A. Zanichelli, Y. Zhi, B. Zuraw, T. Craig   +58 more
semanticscholar   +1 more source