Results 41 to 50 of about 12,349 (241)

The international WAO/EAACI guideline for the management of hereditary angioedema – the 2017 revision and update [PDF]

, 2018
Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and appropriate therapy are essential. This update and revision of the global guideline for HAE provides up-to-date consensus recommendations for the management of HAE.
Aabom, Abdel-Karim, Agostoni, Alexander Nast, Anete S. Grumach, Antonio, Aygoren-Pursun, Aygoren-Pursun, Banerji, Banerji, Banta, Bas, Bas, Berkel, Bernstein, Bernstein, Bernstein, Bernstein, Betschel, Binkley, Black, Blackmore, Blohme, Boccon-Gibod, Bonnekoh, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bouillet, Bouillet, Bouillet, Bouillet, Bowen, Bowen, Bowen, Bowen, Boyle, Brackertz, Brozek, Brozek, Bruce Ritchie, Bruce Zuraw, Brunskill, Bygum, Bygum, Caballero, Caballero, Caballero, Caballero, Caballero, Caballero, Caldwell, Caliskaner, Christiansen, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Constance Katelaris, Craig, Craig, Craig, Craig, Craig, Craig, Craig, Cronin, Crowther, Czaller, de Maat, de Rojas Hernandez Fernandez, De Serres, Dewald, Dinkelacker, Donaldson, Donaldson, Donaldson, Dumitru Moldovan, Emel Aygören-Pürsün, Erikson, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farkas, Farrell, Fernando, Fields, Forrest, Fox, Frank, Frank, Fust, Galan, Germenis, Gilad, Gobert, Gompels, Gonzalez-Quevedo, Gorman, Greve, Grumach, Guyatt, Halbmayer, Hedner, Henriette Farkas, Henrik Balle Boysen, Hilary Longhurst, Hochberg, Hofstra, Ignacio Ansotegui, Inmaculada Martinez-Saguer, Jacques, Jurado-Palomo, Kalaria, Kaplan, Kaplan, Kaplan, Karim, Kohalmi, Konrad Bork, Kreuz, Kunschak, Lang, Lanny Rosenwasser, Levy, Li, Longhurst, Longhurst, Longhurst, Lopez-Lera, Lumry, Lumry, Lumry, Magerl, Magerl, Magerl, Marc Riedl, Marcus Maurer, Mario Sánchez-Borges, Markus Magerl, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Martinez-Saguer, Maurer, Maurer, Maurer, Michihiro Hide, Moldovan, Moldovan, Muhlberg, Nanda, Nasr, Nathani, Nielsen, Nussberger, Ogston, Pappalardo, Pappalardo, Paul Potter, Pedrosa, Peveling-Oberhag, Rahal, Rasmussen, Reshef, Richard Lockey, Riedl, Riedl, Riedl, Riedl, Rocha, Rosen, Rosen, Ruby Pawankar, Saule, Schreiber, Schulz, Sheffer, Sheffer, Spath, Speletas, Staubach, Stephen Betschel, Tarzi, Terpstra, Thoufeeq, Timothy Craig, Toh, Tom Bowen, Tourangeau, Tuong, van Doorn, van Veen, Visy, Waytes, Weiler, Wentz, Whalley, Whalley, William R. Lumry, Wilson, Wu, Yuxiang Zhi, Zanichelli, Zanichelli, Zanichelli, Zilberberg, Zotter, Zotter, Zotter, Zuberbier, Zuraw, Zuraw, Zuraw, Zuraw, Zuraw, Zuraw, Ärzteschaft   +238 more
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Classification, diagnosis, and approach to treatment for angioedema: Consensus report from the Hereditary Angioedema International Working Group [PDF]

, 2014
Angioedema is defined as localized and self-limiting edema of the subcutaneous and submucosal tissue, due to a temporary increase in vascular permeability caused by the release of vasoactive mediator(s). When angioedema recurs without significant wheals,
Adam, Agostoni, Agostoni, Agostoni, Alsenz, Alsenz, Bafunno, Bas, Beltrami, Benson, Bentsianov, Binkley, Blais, Blanch, Blohme, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bork, Bouillet-Claveyrolas, Bowen, Bowen, Branellec, Brasher, Brecy, Bright, Brown, Brown, Burkhart, Bygum, Bygum, Byrd, Byrd, Caballero, Caldwell, Campo, Castelli, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cicardi, Cichon, Cocchio, Colas, Corso, Corte, Craig, Craig, Cugno, Cugno, Cugno, Cugno, Cupido, D'Incan, Dean, Dewald, Dobbels, Donaldson, Donaldson, Donaldson, Du-Thanh, Duan, Farkas, Farkas, Fields, Frank, Gelee, Gelfand, Gompels, Grant, Hassan, Hauptmann, Hauptmann, He, Jackson, Jackson, Jackson, Kalmar, Kalmar, Kaplan, Kiss, Kostis, Kostis, Lam, Levi, Lin, Longhurst, Longhurst, Lopez-Lera, Lopez-Lera, Lumry, Makani, Mandle, Marcos, Martin, Martinez-Saguer, Messerli, Miller, Molinaro, Montinaro, Nielsen, Nussberger, Nussberger, Osler, Pappalardo, Pappalardo, Patel, Pellacani, Quinke, Roche, Roche, Rosen, Rye Rasmussen, Sanchez-Borges, Sanchez-Cano, Sands, Schreiber, Slater, Steinbach, Stray-Pedersen, Tarzi, Tedeschi, Thelwel, Toh, Tosi, Vitrat-Hincky, Wagenaar-Bos, Waytes, Weller, Wilson, Zanichelli, Zanichelli, Ziakas, Zingale, Zingale, Zuberbier, Zuraw, Zuraw, Zuraw, Zuraw, Zuraw   +151 more
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findings from the Icatibant Outcome Survey [PDF]

, 2017
Background Patients with hereditary angioedema (HAE) due to C1-inhibitor deficiency (C1-INH-HAE) experience recurrent attacks of cutaneous or submucosal edema that may be frequent and severe; prophylactic treatments can be prescribed to prevent attacks ...
Aberer, Werner, Andresen, Irmgard, Bouillet, Laurence, Caballero, Teresa, Longhurst, Hilary J., Maurer, Marcus, Perrin, Amandine, Zanichelli, Andrea   +7 more
core   +1 more source

Hereditary angioedema: Not an allergy

Indian Journal of Dermatology, 2012
Hereditary angioedema is a genetic disorder due to a deficiency or malfunction of C1 esterase inhibitor. We herein describe a case of 25-year-old male who presented with swelling over face since one day.
Sanjay Bhivgade, Shubha Melkote, Smita Ghate, H R Jerajani   +3 more
doaj   +1 more source

Pediatric hereditary angioedema [PDF]

Pediatric Allergy and Immunology, 2013
Abstract Hereditary angioedema ( HAE ) is a lifelong illness characterized by recurrent swelling of the skin, intestinal tract, and, ominously, the upper airway. It is caused by inadequate activity of the protein C1‐inhibitor, with dysfunction in the kallikrein/bradykinin ...
openaire   +3 more sources

A Case Report of Angioedema and Anaphylactic Shock Induced by Ingestion of Polyethylene Glycol [PDF]

, 2020
Introduction: We report one of few documented cases of a severe anaphylactic reaction with angioedema to polyethylene glycol (PEG).Case Report: The patient presented 30 minutes after onset of his symptoms and quickly developed hypoxia and hypotension ...
Osborn, Lesley, Rossi, Amy
core  

Secreted phospholipases A2 in hereditary angioedema with C1-inhibitor deficiency [PDF]

, 2018
BackgroundHereditary angioedema (HAE) caused by deficiency (type I) or dysfunction (type II) of the C1 inhibitor protein (C1-INH-HAE) is a disabling, potentially fatal condition characterized by recurrent episodes of swelling. We have recently found that
Andrea Zanichelli, Angelica Petraroli, Anne Lise Ferrara, Chiara Suffritti, Francesco Borriello, Francesco Borriello, Francescopaolo Granata, Gianni Marone, Gianni Marone, Gilda Varricchi, Gérard Lambeau, Henriette Farkas, Marco Cicardi, Maria Bova, Maria Rosaria Galdiero, Nóra Veszeli, Stefania Loffredo   +16 more
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"They are closely interconnected, complement each other and pass into each other, there are no clear boundaries between them". Case report

Кардиоваскулярная терапия и профилактика, 2023
Hereditary angioedema is a rare (1:50,000) hereditary chronic disease from the group of primary immunodeficiencies, which manifests in the form of recurrent skin and mucous membrane edema of the respiratory tract and gastrointestinal tract.Pathogenesis ...
E. A. Rogozhkina, A. I. Ershova, E. Yu. Andreenko, S. A. Beregovskaya   +3 more
doaj   +1 more source

[Hereditary angioedema].

Tidsskrift for den Norske laegeforening : tidsskrift for praktisk medicin, ny raekke, 1989
Hereditary angioedema is a rare disease, transmitted as an autosomal dominant trait. The disease usually manifests as acute subcutaneous or submucosal swellings and abdominal pain of two to five days duration. When localized to head or throat, life-threatening edema of the larynx may occur. The disease is caused by reduced amount of active C1 inhibitor.
A, Sabbah, I, Marsollier, V, Trouillard
  +6 more sources

Remission of hereditary angioedema attacks associated with starting teriflunomide in a patient with multiple sclerosis

European Journal of Case Reports in Internal Medicine, 2023
Background: Hereditary angioedema is a rare hereditary and potentially life-threatening disorder characterized by recurrent attacks of cutaneous and submucosal swelling. In spite of the advances made in terms of pathophysiology, underlying mechanisms are
Ana López, Diego Fernández Romero
doaj   +1 more source