Results 11 to 20 of about 3,389 (251)
Cardiovascular Abnormalities Associated with Heterotaxy Syndrome: A Case Series
Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging, 2023 Heterotaxy syndromes result from the failure of normal lateralization, resulting in the abnormal arrangement of cardiothoracic and abdominal viscera. These are associated with a disproportionate morbidity and mortality rate, mandating early diagnosis ...
Shraddha Joshi +3 more
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Heterotaxy polysplenia syndrome in an adult female with complete endocardial cushion defect
Radiology Case Reports, 2021 Heterotaxy syndrome is a rare condition characterized by the abnormal arrangement of thoracoabdominal organs across the left-right axis of the body.It is generally classified as right and left atrial isomerism or asplenia and polysplenia syndrome, even ...
Habib Ahmad Esmat +2 more
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Clinical Case Reports, 2021 Heterotaxy syndrome is associated with asplenia/polysplenia and complex congenital heart disease. Facial palsy in heterotaxy is very rare. The management is still challenging with a poor prognosis. Proper counseling to the family about the disease course,
Sanjeev Kharel +6 more
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, 2018 Mutation of ZIC3 causes X-linked heterotaxy, a syndrome in which the laterality of internal organs is disrupted. Analysis of model organisms and gene expression during early development suggests ZIC3-related heterotaxy occurs due to defects at the earliest stage of left-right axis formation.
Bellchambers, Helen M. +1 more
openaire +2 more sources
Biventricular Repair in Heterotaxy Patients [PDF]
World Journal for Pediatric & Congenital Heart Surgery, 2015 Smita Mishra +2 more
exaly +3 more sources
International Journal of Cardiology Congenital Heart Disease, 2023 Background: Heterotaxy syndromes encompass left and right atrial isomerism (LAI and RAI respectively) and are associated with variable cardiac and non-cardiac anomalies which greatly influence outcomes.
Bradley MacDonald +4 more
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Heterotaxy syndrome: This is the left, right?
South African Journal of Radiology, 2015 Heterotaxy syndrome is a rare and complex disorder of the chest and abdominal organ arrangements, and presents a diagnostic challenge to the radiologist.
Lili Huang +4 more
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Heterotaxy Syndrome with Polysplenia, Fused Adrenal Glands, and Diabetes Mellitus
Clinical Medicine Insights: Cardiology, 2022 Heterotaxy syndrome is a rare congenital heart disease with a disarrangement of the heart and abdominal organs. We present a young African female with features of heart failure, diffuse irregular cardiac murmurs, and palpable, tender epigastric mass.
Abid M Sadiq, Adnan M Sadiq
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Annals of Pediatric Cardiology, 2022 Pulmonary arteriovenous malformations after the Kawashima procedure causing severe hypoxemia are treated by Fontan surgery that redirects hepatic venous blood to the pulmonary circulation.
Kothandam Sivakumar
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Frontiers in Pediatrics, 2022 ObjectiveCardiac and extra-cardiac anomalies in 46 pre-natally diagnosed cases of heterotaxy were compared to post-natal anatomical patterns in order to reveal discordant findings.
Elisabeth Seidl-Mlczoch +9 more
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