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Anesthesia for muscle biopsy to test susceptibility to malignant hyperthermia [PDF]

open access: diamondBrazilian Journal of Anesthesiology, 2019
Introduction: Malignant hyperthermia is an autosomal dominant pharmacogenetic disorder, characterized by hypermetabolic crisis triggered by halogenated anesthetics and/or succinylcholine.
Helga Cristina Almeida da Silva   +5 more
doaj   +3 more sources

Profile of malignant hyperthermia susceptibility reports confirmed with muscular contracture test in Brazil [PDF]

open access: diamondBrazilian Journal of Anesthesiology, 2019
Background and objectives: Malignant hyperthermia is an autosomal dominant hypermetabolic pharmacogenetic syndrome, with a mortality rate of 10%–20%, which is triggered by the use of halogenated inhaled anesthetics or muscle relaxant 10%–20 ...
Helga Cristina Almeida da Silva   +7 more
doaj   +3 more sources

Acute postoperative sepsis mimicking symptomology suspicious for malignant hyperthermia: case report [PDF]

open access: diamondBrazilian Journal of Anesthesiology, 2019
Background: Sepsis is a life-threatening organ dysfunction with non-specific clinical features that can mimic other clinical conditions with hyper metabolic state such as malignant hyperthermia.
Vendhan Ramanujam   +3 more
doaj   +3 more sources

Susceptibilidade à hipertermia maligna em três pacientes com síndrome maligna por neurolépticos [PDF]

open access: goldArquivos de Neuro-Psiquiatria, 2000
A hipertermia maligna caracteriza-se por hipertermia, rigidez muscular, rabdomiólise, acidose e insuficiência de múltiplos órgãos. A hipertermia maligna anestésica decorre da exposição a halogenados e/ou relaxantes musculares despolarizantes.
HELGA C. A. SILVA   +5 more
doaj   +8 more sources

Identificación y tratamiento oportuno exitoso de hipertermia maligna [PDF]

open access: diamondRevista Chilena de Anestesia, 2023
Alexander García Castañeda   +2 more
doaj   +4 more sources

Predictive factors of the contracture test for diagnosing malignant hyperthermia in a Brazilian population sample: a retrospective observational study [PDF]

open access: yesBrazilian Journal of Anesthesiology, 2023
Introduction: Malignant Hyperthermia (MH) is a pharmacogenetic, hereditary and autosomal dominant syndrome triggered by halogenates/succinylcholine.
Jean Marcel de Mello   +6 more
doaj   +2 more sources

Fatigue, depression, and physical activity in patients with malignant hyperthermia: a cross-sectional observational study [PDF]

open access: yesBrazilian Journal of Anesthesiology, 2023
Background: Malignant Hyperthermia (MH) is a pharmacogenetic disorder triggered by halogenated anesthesia agents/succinylcholine and characterized by hypermetabolism crisis during anesthesia, but also by day-to-day symptoms, such as exercise intolerance,
P..mela Vieira de Andrade   +5 more
doaj   +2 more sources

Hipertermia maligna [PDF]

open access: bronzeRECIMUNDO, 2022
La hipertermia maligna es una miopatía metabólica, cuyos pacientes portadores tienen una respuesta diferente a la población general ante la presencia de un agente desencadenante como a los analgésicos volátiles y relajantes musculares despolarizantes. Su incidencia varía entre 1:10.000 a 1: 250.000 anestesias. Su mortalidad actual usando el tratamiento
Janet Gloria Ortiz-Bautista   +2 more
  +4 more sources

Estratégia educativa com profissionais de enfermagem sobre hipertermia maligna em um centro cirúrgico cardiovascular [PDF]

open access: diamondRevista SOBECC, 2020
Objetivo: Avaliar o conhecimento da equipe de enfermagem do centro cirúrgico sobre hipertermia maligna, antes e após aula expositiva e implantar kit padronizado para tratamento, junto aos anestesiologistas.
Elisabete Silvana de Oliveira Sene   +3 more
doaj   +2 more sources

Evaluation of anesthesiology residents in the diagnosis and control of malignant hyperthermia: comparison of three scenarios of realistic simulation ‒ a cross-sectional controlled study [PDF]

open access: yesBrazilian Journal of Anesthesiology
Introduction: Simulation-based training is particularly beneficial for rare and life-threatening diseases such as Malignant Hyperthermia (MH). In addition, cognitive aids, including flowcharts and checklists, can be used as guidance in crisis, reducing ...
Mariana F.L. Neville   +10 more
doaj   +2 more sources

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