Results 101 to 110 of about 22,368 (237)
Histopathology, Volume 88, Issue 3, Page 698-709, February 2026.We evaluated the diagnostic utility of GPNMB immunohistochemistry in LAM. GPNMB showed strong expression in LAM cells, while the differential diagnostic mimics showed no or only low expression. Based on its 100% sensitivity and specificity in our cohort, GPNMB is a highly reliable immunohistochemical marker for the diagnosis of LAM.
Fatime Szalai +6 more
wiley +1 more source
Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
Case Reports in Hematology, 2011 Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man.
Peter G. Pavlidakey +3 more
doaj +1 more source
Case Reports in Nephrology and Dialysis, 2017 Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus.
Farid Arman +4 more
doaj +1 more source
A Rare Case of a Systemic Non-Langerhans Histiocytosis Presenting with Diabetes Insipidus and a Tentorial Mass [PDF]
, 2015 Introduction The histiocytoses are a group of clinically diverse diseases distinguished from one another based on the specific immunophenotype of the lesional cells, implying derivation from the same precursor cell.
Barros, MS, Guilherme +5 more
core +2 more sources
Clinical Case Reports, Volume 14, Issue 1, January 2026.ABSTRACT Ruptured hydatid cyst should be considered when encountering spontaneous pneumothorax and pneumomediastinum, especially in young patients in regions with high prevalence of hydatid cyst. Awareness of atypical signs ensures instant diagnosis, guiding appropriate surgical and medical treatment to prevent serious complications.
Farzaneh Akbari +5 more
wiley +1 more source
Thoracic, abdominal and musculoskeletal involvement in Erdheim-Chester disease: CT, MR and PET imaging findings. [PDF]
, 2014 BACKGROUND: Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis with characteristic radiological and histological features. This entity is defined by a mononuclear infiltrate consisting of lipid-laden, foamy histiocytes that stain
Antunes, C, Donato, P, Graça, B
core +1 more source
ALK‐Positive Histiocytosis With Unilateral Breast Involvement: A Case Report
Clinical Case Reports, Volume 14, Issue 1, January 2026.ABSTRACT APH is a rare disorder characterized by the proliferation of ALK‐expressing histiocytes with variable anatomical involvement; however, mammary involvement is exceptionally rare. A 32‐year‐old woman presented with a painless right breast mass. Ultrasound identified a 9 × 8 mm hypoechoic nodule, categorized as BI‐RADS 4A.
Xuechun Liu, Dong Ren, Yanfang Liang
wiley +1 more source
Xanthoma Disseminatum with Tumor-Like Lesion on Face
Case Reports in Dermatological Medicine, 2014 Xanthoma disseminatum (XD) is a rare benign mucocutaneous xanthomatosis that is classified as a benign non-Langerhans cell histiocytosis. We report a 62-year-old man who presented with widespread yellow-brown papulonodular and tumoral lesions on face ...
Habib Ansarin +3 more
doaj +1 more source
Altano-axial subluxation with torticollis secondary to Langerhans cell histocytosis
Interdisciplinary Neurosurgery, 2017 Langerhans Cell Histiocytosis is a rare disease featuring aberrant proliferation of dendritic cells that can infiltrate the bony skeleton. The authors report a case of six-year-old female presenting with torticollis. She was found to have extensive lytic
Joshua Y. Chua, MD +5 more
doaj +1 more source
Caso para diagnóstico Case for diagnosis
Anais Brasileiros de Dermatologia, 2011 Relatamos um caso de histiocitose cefálica benigna em uma criança do sexo masculino, de um ano e três meses de idade que desenvolveu múltiplas pápulas na região malar bilateralmente, sem outros comemorativos associados.
Maria de Fátima Guimarães Scotelaro Alves +4 more
doaj +1 more source