Results 21 to 30 of about 58,815 (317)

Primary Langerhans Cell Histiocytosis of the Extrahepatic Bile Duct Occurring in an Adult Patient

Balkan Medical Journal, 2018
Background: Langerhans cell histiocytosis is characterized by an abnormal proliferation of neoplastic Langerhans cells. Langerhans cell histiocytosis commonly affects the pediatric population, whereas presentation in adults remains a rare event.
Ifeyinwa E. Obiorah, Alicia Henao Velasquez, Bhaskar Kallakury, Metin Özdemirli   +3 more
doaj   +1 more source

A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]

, 2018
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M., Karaman, Engin, Ufuk, F., Yavaş, H.G.   +3 more
core   +1 more source

Challenges in the diagnosis of hemophagocytic lymphohistiocytosis: Recommendations from the North American Consortium for Histiocytosis (NACHO)

Pediatric Blood & Cancer, 2019
Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic immune activation, often associated with genetic defects of lymphocyte cytotoxicity.
M. Jordan, C. Allen, Jay Greenberg, Michael M. Henry, M. Hermiston, Ashish R. Kumar, M. Hines, O. Eckstein, S. Ladisch, K. Nichols, C. Rodríguez-Galindo, B. Wistinghausen, K. McClain   +12 more
semanticscholar   +1 more source

Langerhans cell histiocytosis on the penis: a case report

BMC Urology, 2006
Background Langerhans cell histiocytosis affects mainly young children and features an accumulation of CD1a+ dendritic Langerhans cells in the bone, skin, and other organs.
Kuroda Isao, Ashimine Satoshi, Ueno Munehisa, Hagiuda Jun, Ishizawa Keisuke, Deguchi Nobuhiro   +5 more
doaj   +1 more source

Vemurafenib for Refractory Multisystem Langerhans Cell Histiocytosis in Children: An International Observational Study

Journal of Clinical Oncology, 2019
PURPOSE Off-label use of vemurafenib (VMF) to treat BRAFV600E mutation–positive, refractory, childhood Langerhans cell histiocytosis (LCH) was evaluated. PATIENTS AND METHODS Fifty-four patients from 12 countries took VMF 20 mg/kg/d. They were classified
J. Donadieu, I. Larabi, M. Tardieu, J. Visser, C. Hutter, E. Sieni, N. Kabbara, M. Barkaoui, Jean Miron, F. Chalard, Paul Milne, J. Haroche, F. Cohen, Z. Hélias‐Rodzewicz, N. Simon, M. Jehanne, A. Kolenová, A. Pagnier, N. Aladjidi, P. Schneider, G. Plat, A. Lutun, Anne Sonntagbauer, T. Lehrnbecher, A. Ferster, V. Efremova, M. Ahlmann, Laurence Blanc, J. Nicholson, A. Lambilliote, H. Boudiaf, A. Lissat, K. Svojgr, Fanette Bernard, S. Elitzur, M. Golan, D. Evseev, M. Maschan, A. Idbaih, Olga Slater, M. Minkov, V. Taly, M. Collin, J. Alvarez, J. Emile, S. Héritier   +45 more
semanticscholar   +1 more source

Paraneoplastic cerebellar degeneration associated with lymphoepithelial carcinoma of the tonsil [PDF]

, 2013
Background: Paraneoplastic cerebellar degeneration (PCD) is a classical tumor-associated, immune-mediated disease typically associated with gynecological malignancies, small-cell lung-cancer or lymphoma.
Hartmann, Sylvia, Henke, Christian, Middendorp, Marcus, Rieger, Johannes, Steinmetz, Helmuth, Ziemann, Ulf   +5 more
core   +1 more source

Neurodegenerative central nervous system disease as late sequelae of Langerhans cell histiocytosis. Report from the Japan LCH Study Group

Haematologica, 2008
Clinical features, brain magnetic resonance imaging findings and EDSS scores of 11 patients with neurodegenerative central nervous system Langerhans cell histiocytosis were analyzed in Japan.
Shinsaku Imashuku, Yoko Shioda, Ryoji Kobayashi, Gaku Hosoi, Hisanori Fujino, Shiro Seto, Hisashi Wakita, Akira Oka, Nagisa Okazaki, Naoto Fujita, Toshinori Minato, Kenichi Koike, Yukiko Tsunematsu, Akira Morimoto   +13 more
doaj   +1 more source

Cerebral manifestation and diagnostic dilemma of Rosai-Dorfman disease

CNS Oncology, 2023
Rosai-Dorfman disease (RDD) is a rare, S100-positive histiocytic proliferation, that can cause both nodal and extranodal illness. We present a case of a 53-year-old male patient.
Szintia Almási, Tamás Pancsa, László Tiszlavicz, Anita Sejben   +3 more
doaj   +1 more source

Langerhans cell histiocytosis [PDF]

, 1998
The authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations.
Atallah, Álvaro Nagib, Chauffaille, Maria de Lourdes Lopes Ferrari, Diniz, Cybelle Maria Costa, Enokihara, Silva, Ferreira, Karin Ventura, Hassun, Karine Marques, Kerbauy, José, Martinez, José Antônio Baddini, Michalany, Nylceo, Simões, Milvia Maria, Valério, Rosana M.   +10 more
core   +2 more sources

Langerhans cell histiocytosis (histiocytosis X) [PDF]

Postgraduate Medical Journal, 1997
Summary There has been a renewed interest in Langerhans cell histiocytosis in recent years due both to advances in basic research and to improvements in diagnostic and treatment approaches. In this article, we review the various aspects of the disease and the potential implications of these recent scientific researches for our ...
openaire   +3 more sources