Results 31 to 40 of about 56,324 (305)
A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M.+3 more
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Langerhans cell histiocytosis (histiocytosis X) [PDF]
Summary There has been a renewed interest in Langerhans cell histiocytosis in recent years due both to advances in basic research and to improvements in diagnostic and treatment approaches. In this article, we review the various aspects of the disease and the potential implications of these recent scientific researches for our ...
openaire +3 more sources
Rare Presentation of a Rare Orthopedic Pathology: Erdheim Chester Disease [PDF]
In 1930, William Chester and pathologist Jakob Erdheim discovered the pathology currently known as Erdheim Chester disease. There are only approximately 249 histologically confirmed patients to have been diagnosed with this disease as noted in the ...
Samona J, Owen J, Martin S
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Pulmonary Langerhans cell histiocytosis causing spontaneous bilateral pneumothorax in a child
Bilateral pneumothorax is very rare in childhood. Moreover, if it is due to pulmonary involvement of Langerhans cell histiocytosis, it is even rarer in childhood.
Anupam Patra+3 more
doaj +1 more source
Intracranial Rosai-Dorfman Disease: pathophysiology, diagnosis and treatment
Introduction and purpose: Rosai-Dorfman Disease (RDD), known also as sinus histiocytosis with massive lymphadenopathy(SHML) is a benign histiocytic proliferative syndrome. The etiology and pathogenesis of RDD remains unclear.
Michał Szymoniuk+3 more
doaj +1 more source
Langerhans cell histiocytosis in adults: Advances in pathophysiology and treatment
Langerhans cell histiocytosis (LCH) is a rare systemic disorder characterized by the accumulation of CD1a+/Langerin+ LCH cells and wide‐ranging organ involvement.
Masayuki Kobayashi, A. Tojo
semanticscholar +1 more source
BackgroundPituitary stalk thickening (PST) is a rare abnormality in the pediatric population. Its etiology is heterogeneous. The aim of the study was to identify important clinical, radiological and endocrinological manifestations of patients with PST ...
Elżbieta Moszczyńska+5 more
doaj +1 more source
Deciphering the role of Epstein-Barr virus in the pathogenesis of T and NK cell lymphoproliferations [PDF]
Epstein-Barr virus (EBV) is a highly successful herpesvirus, colonizing more than 90% of the adult human population worldwide, although it is also associated with various malignant diseases.
Fox, Christopher P+2 more
core +2 more sources
Langerhans cell histiocytosis is a rare clonal disease characterized by the proliferation of CD1a-positive immature dendritic cells. The purpose of this article was to present an updated review of recent advances in the pathogenesis, clinical features ...
Michalina Jezierska+4 more
semanticscholar +1 more source
Objective: Langerhans cell histiocytosis is an unusual disorder of unknown etiology with heterogeneous clinical behaviors and variable outcomes. It can involve one or more organs or systems, but to our best knowledge, parotid glands involvement in ...
Xiaojun Yuan+4 more
doaj +1 more source