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"Histiocytosis X" – A Rare Case Report [PDF]
Histiocytosis X is an idiopathic disease, characterized by a disorder of the reticulo-endothelial system in the human body. Histopathological studies carried out right from the 1800s have seen a significant similarity in the pathologic process of ...
Emmanuel Dhiravia Sargunam Azariah+4 more
doaj +4 more sources
Histiocytosis x: Recurrent isolated mandibular lesion (case report) [PDF]
Histiocytosis X usually affects children and adolescents. In our case, a 54-year-old woman was admitted to hospital for evaluating and treatment of an isolated, painless swelling of the left side of the mandible.
Basta-Jovanović Gordana M.+3 more
doaj +5 more sources
Unusual presentation of histiocytosis X in the cranial vault: A rare case report [PDF]
Langerhans histiocytosis or histiocytosis X is an oligo-clonal proliferation of Langerhans cells. We report the case of an 11-month-old infant who had presented with a parieto-occipital swelling since birth, which progressively increased in volume ...
Dahmane El Hairech, MD, PhDs+1 more
doaj +3 more sources
Histiocytosis X of the temporal bone [PDF]
de Brito Macedo Ferreira, Lidiane Maria+3 more
core +5 more sources
Langerhans Cell Histiocytosis With <i>MAP2K1<sup>E102_I103del</sup></i> Mutation Successfully Treated With Trametinib. [PDF]
ABSTRACT The discovery of the MAPK pathway mutations in lesions of patients with Langerhans cell histiocytosis (LCH) has made targeted therapy an important therapeutic approach for these patients. Theoretically, the RAF‐independent mutation MAP2K1E102_I103del is naturally resistant to allosteric MEK inhibitors.
Lang M, Chang L, Cao XX.
europepmc +2 more sources
Erdheim-Chester Disease Manifesting Without Long Bone Involvement. [PDF]
We present an atypical case of Erdheim–Chester Disease (ECD) due to the absence of skeletal involvement despite widespread infiltration of other organs. ABSTRACT Erdheim–Chester Disease (ECD) is an extremely rare, non‐Langerhans cell histiocytosis characterised by the proliferation of foamy histiocytes infiltrating various organs.
Sivasubramanian D+6 more
europepmc +2 more sources
A Case of Langerhans Cell Histiocytosis With a Neck Mass as the First Symptom. [PDF]
This article presents a case of Langerhans cell histiocytosis with a neck mass as the first symptom, summarizing the symptoms, signs, and imaging manifestations of the disease, in order to provide implications for the future clinical diagnosis and treatment of this disease..
Xie Y, Kang X, Liu X, Wang Z, Jing Q.
europepmc +2 more sources
Rosai-Dorfman Disease in a 4-Month-Old Female Presenting With Cervical Lymphadenopathy. [PDF]
ABSTRACT Rosai‐Dorfman disease is a rare histiocytic disorder that can mimic malignancies. This case highlights the importance of immunohistochemistry in distinguishing RDD from lymphoproliferative neoplasms, ensuring accurate diagnosis and management.
Khan A+5 more
europepmc +2 more sources
Histiocytosis X (Langerhan’s cell granulomatosis) is a disease of unknown aetiology, but viral origin has been implicated.1 It is a clinicopathologic entitycharacterized by proliferation of Langerhan’s cell (which are not primarily phagocytic) in an ...
Ahmed, SA+4 more
core +5 more sources
Progress in understanding the pathogenesis of Langerhans cell histiocytosis: back to Histiocytosis X? [PDF]
Berres ML, Merad M, Allen CE.
europepmc +2 more sources