"Histiocytosis X" – A Rare Case Report [PDF]
Histiocytosis X is an idiopathic disease, characterized by a disorder of the reticulo-endothelial system in the human body. Histopathological studies carried out right from the 1800s have seen a significant similarity in the pathologic process of ...
Emmanuel Dhiravia Sargunam Azariah +4 more
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Unusual presentation of histiocytosis X in the cranial vault: A rare case report [PDF]
Langerhans histiocytosis or histiocytosis X is an oligo-clonal proliferation of Langerhans cells. We report the case of an 11-month-old infant who had presented with a parieto-occipital swelling since birth, which progressively increased in volume ...
Dahmane El Hairech, MD, PhDs +1 more
doaj +2 more sources
Pulmonary Langerhans Cell Histiocytosis Presenting as Multiple Obstructing Bronchial Lesions and Pulmonary Masses. [PDF]
We describe a case of PLCH presenting as multiple obstructing bronchial lesions and pulmonary masses in a 36‐year‐old man. To our knowledge, this is the first report of PLCH presenting as bilateral hilar masses and airway obstructive lesions. ABSTRACT Pulmonary Langerhans cell histiocytosis is a rare lung disease, which was previously classified as ...
Fan J, Liu C, Yang Z, Sun D.
europepmc +2 more sources
Langerhans Cell Histiocytosis Associated With Chronic Myeloid Leukemia: A Pediatric Case Report. [PDF]
ABSTRACT Background Langerhans cell histiocytosis (LCH) is a rare clonal neoplasm driven by activating mutations in the MAPK pathway, leading to accumulation of pathological Langerhans cells in various tissues. LCH is increasingly associated with secondary malignancies, including leukemias, lymphomas, and solid tumors. However, chronic myeloid leukemia
Latifi A, Yousefian S.
europepmc +2 more sources
Efficacy, safety, and relapse outcomes of MAPK inhibitors in pediatric Langerhans cell histiocytosis: A real-world study. [PDF]
What's new? Mitogen‐activated protein kinase (MAPK) inhibitors are promising treatments for pediatric Langerhans cell histiocytosis (LCH), a rare heterogeneous neoplasm that often affects multiple organ systems. Which MAPK inhibitors are most effective against LCH remains uncertain.
Tang X +5 more
europepmc +2 more sources
Multisystem Langerhans cell histiocytosis: Literature review and case report
Langerhans cell histiocytosis (LCH) refers to a group of diseases of unknown etiology, typically discovered in childhood, characterized by the accumulation of Langerhans cells (white blood cells with large cell nuclei that may contain cytoplasmic ...
Cung-Van Cong, MD, PhD +2 more
doaj +1 more source
Langerhans cell histiocytosis (histiocytosis x) – in the mandible
This article reports a case of 65 year-old man consultedin a private radiology dental clinic for a panoramicradiography, where was indicated a radiolucent area,extending into the periapical region of the teeth 35 to 43 to the base of the mandible ...
Angela Jordão Camargo +5 more
doaj +1 more source
Hand-Schüller-Christian disease
Langerhan cell histiocytosis, formerly known as histiocytosis X, traditionally denotes a group of diseases that stem from proliferative reticuloendothelial disturbances.The etiology and pathogenesis of the disease remain debatable.
Deepak Bhargava +3 more
doaj +1 more source
Histiocytosis X and Bronchopulmonary Adenocarcinoma: A Rare Coexistence
There exists a rarely observed association between pulmonary histiocytosis X and bronchopulmonary cancer. However, the frequency of bronchopulmonary cancer in these patients is higher than in the general population.
Akýn Kaya +5 more
doaj +1 more source
Histiocytosis x: Recurrent isolated mandibular lesion (case report) [PDF]
Histiocytosis X usually affects children and adolescents. In our case, a 54-year-old woman was admitted to hospital for evaluating and treatment of an isolated, painless swelling of the left side of the mandible.
Basta-Jovanović Gordana M. +3 more
doaj +1 more source

