Macrophage Activation Syndrome as Onset of Systemic Lupus Erythematosus: A Case Report and a Review of the Literature [PDF]
, 2015 Macrophage activation syndrome (MAS) is a potentially fatal condition. It is a rare complication of several autoimmune disorders, including systemic lupus erythematosus (SLE) and systemic juvenile idiopathic arthritis (sJIA).
Didona, Dario +4 more
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CD30 as a Target Molecule in the Diagnosis and Therapy of Lymphomas
American Journal of Hematology, Volume 101, Issue 1, Page 110-128, January 2026.ABSTRACT The tumor necrosis factor (TNF)‐receptor superfamily 8 receptor CD30 molecule is expressed in all tumor cells of Hodgkin lymphoma and anaplastic large cell lymphoma but is only weakly expressed in a small subset of large lymphoid cells in normal peripheral lymphoid tissues.
Harald Stein, Brunangelo Falini
wiley +1 more source
Pulmonary langerhans cell granulomatosis (histiocytosis X)
Туберкулез и болезни лёгких, 2014 Pulmonary Langerhans cell granulomatosis is a rare disease. Its causes are unknown and accurate data on its prevalence are lacking. This disease is characterized by the formation of lung tissue granulomas consisting of activated Langerhans cells ...
A. A. Sadovnikov, K. I. Panchenko
doaj
Clinical experience in an infant with Langerhans cell histiocytosis
Universidad Médica Pinareña, 2021 Introduction: Langerhans cell histiocytosis (LCH) or Histiocytosis X is a benign proliferative disease affecting dendritic cells. It presents a wide clinical spectrum, from isolated eosinophilic bone granuloma to multisystem involvement with multiple ...
Yamilka Pita Barrios +2 more
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Secondary aneurysmal bone cyst in Langerhans cell histiocytosis: Case report, literature review
European Journal of Radiology Open, 2019 Langerhans cell histiocytosis (LCH) is a rare disease of the myeloid precursor cells, it predominantly occurs in the skull and long bones as unifocal bone lesions. Aneurysmal bone cysts (ABC) are benign, expansive and lytic bone. Reports of secondary ABC
P. Lomoro +6 more
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Histiocytosis X: Langerhans’ Cell Histiocytosis
Hematology/Oncology Clinics of North America, 1987 Histiocytosis X is a complex and poorly understood entity. Nevertheless, it would appear as if certain themes are found recurrently throughout the literature dealing with this disease and a review of them serves as a useful summary. 1. Problems with Nomenclature.
openaire +2 more sources
Localized Langerhans cell histiocytosis masquerading as Brodie s abscess in a 2-year-old child: a case report [PDF]
, 2016 Langerhans cell histiocytosis (LCH), formerly known as histiocytosis X, refers to a spectrum of diseases characterized by idiopathic proliferation of histiocytes that produce either focal (localized LCH) or systemic manifestations (Hand–Schüller ...
Chang, Wei-Fang +4 more
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Expert Perspective: Diagnosis and Treatment of Castleman Disease
Arthritis &Rheumatology, Volume 78, Issue 1, Page 12-25, January 2026.Castleman disease (CD) is a major diagnostic challenge for rheumatologists. Unicentric CD (UCD) involves one enlarged lymph node region, whereas multicentric CD (MCD) involves multiple enlarged lymph node regions. Both UCD and MCD may exhibit a wide range of symptoms that overlap with other immune‐mediated conditions.
Luke Y. C. Chen +2 more
wiley +1 more source
Langerhans Cell Histiocytosis (LCH) and Diabetes Insipidus with Mandibular lesion
Electronic Physician, 2012 Langerhans cell histicytosis (LCH) is a rare disorder that primarily affects children. Its occurrence in adult is very rare. We report a case of 42 year old female patient who presented polyuria and polydipsia, loosing teeth and diplopia added to symptom
Sayeh Alizad jahani +3 more
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Eosinophilic Granuloma of the Spine With and Without Vertebra Plana: Long-term Follow-up of Six Cases (Cast Reports) [PDF]
, 1993 Vertebral eosinophilic granuloma is a rare condition frequently associated with vertebra plana. In this paper we present six patients with eosinophilic granuloma of the spine; three were without vertebra plana, which represents a diagnostic
Barrios, R.H. (Raúl H.) +3 more
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