Results 1 to 10 of about 91,456 (234)
Idiopathic pulmonary fibrosis [PDF]
Orphanet Journal of Rare Diseases, 2008 Idiopathic pulmonary fibrosis (IPF) is a non-neoplastic pulmonary disease that is characterized by the formation of scar tissue within the lungs in the absence of any known provocation. IPF is a rare disease which affects approximately 5 million persons worldwide.
Paul W. Noble, Eric B. Meltzer
openaire +5 more sources
[Idiopathic pulmonary fibrosis].
Medecine sciences : M/S, 2022 Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive and fatal lung disease of unknown origin. It is characterized by aberrant scarring of the alveolar epithelium leading to an accumulation of extracellular matrix (ECM). Fibroblastic foci, consisting of fibroblasts and myofibroblasts, are responsible for the excessive production of ECM.
Hennion, Nathan +4 more
+10 more sources
Idiopathic pulmonary fibrosis [PDF]
Thorax, 2011 Idiopathic pulmonary fibrosis is a progressive lung disease that carries a poor prognosis and for which there are no effective therapies. Although the excessive deposition of extracellular matrix, combined with evidence of recurrent injury to the alveolar epithelium, are well-described there is a pressing need to understand these processes better at a ...
Moira K. B. Whyte, Zhe Hui Hoo
openaire +5 more sources
The Lancet, 2017 Idiopathic pulmonary fibrosis is a prototype of chronic, progressive, and fibrotic lung disease. Healthy tissue is replaced by altered extracellular matrix and alveolar architecture is destroyed, which leads to decreased lung compliance, disrupted gas exchange, and ultimately respiratory failure and death.
Luca Richeldi +3 more
+12 more sources
Cough in Idiopathic Pulmonary Fibrosis [PDF]
Frontiers in Rehabilitation Sciences, 2021 Chronic cough is experienced by most patients with idiopathic pulmonary fibrosis (IPF). It is often the first symptom and is associated with reduced quality of life, increased rates of depression and anxiety, more severe physiological impairment, and disease progression.
Jennifer Mann +11 more
openaire +4 more sources
Cough in idiopathic pulmonary fibrosis [PDF]
European Respiratory Review, 2016 Many patients with idiopathic pulmonary fibrosis (IPF) complain of chronic refractory cough. Chronic cough is a distressing and disabling symptom with a major impact on quality of life. During recent years, progress has been made in gaining insight into the pathogenesis of cough in IPF, which is most probably “multifactorial” and influenced by ...
Van Manen MJ +6 more
openaire +6 more sources
La Presse Médicale, 2023 Idiopathic pulmonary fibrosis (IPF) is a progressive devastating lung disease with substantial morbidity. It is associated with cough, dyspnea and impaired quality of life. If left untreated, IPF has a median survival of 3 years. IPF affects ∼3 million people worldwide, with increasing incidence in older patients. The current concept of pathogenesis is
Thomas Koudstaal, Marlies S. Wijsenbeek
openaire +2 more sources
Is It Idiopathic Pulmonary Fibrosis or Not? [PDF]
The Journal of the American Board of Family
Medicine, 2018 Pulmonary fibrosis is not uncommon. Usual interstitial pneumonitis (UIP)/idiopathic pulmonary fibrosis (IPF) is the most common of the idiopathic pulmonary fibrotic diseases and has the worst prognosis with a mean life expectancy of 3.8 years.
Genta Ishikawa +2 more
openaire +3 more sources
Management of Idiopathic Pulmonary Fibrosis [PDF]
Clinics in Chest Medicine, 2012 Idiopathic pulmonary fibrosis (IPF) is a deadly progressive lung disease without an effective standard treatment approach. Because of the complexity and uncertainties of IPF treatment, therapeutic decisions need to be tailored to the individual patient, after discussing the potential benefits and pitfalls.
CERRI, Stefania +3 more
openaire +6 more sources
Pulmonary fibrosis: “idiopathic” is not “cryptogenic” [PDF]
European Respiratory Journal, 2019 The additional argument advanced by Professor Cottin for retention of the term “idiopathic pulmonary fibrosis” is highly persuasivehttp://ow.ly ...
Wells, Athol U +5 more
openaire +3 more sources