Results 41 to 50 of about 609,847 (198)

IgG4-related disease [PDF]

, 2008
IgG4関連疾患は21世紀になって提唱された新しい疾患である｡組織学的にはIgG4陽性形質細胞やリンパ球浸潤が涙腺, 唾液腺, 後腹膜, 膵臓, 胆管などで起こり, 臨床的にはMikulicz病, 後腹膜線維症, 自己免疫膵炎, 糖尿病, 原発性硬化性胆管炎類似の胆管病変などを呈する全身性疾患であり, ステロイド治療に対する良好な反応性を認める｡その診断基準は確立されておらず, われわれは, ①血清IgG4の高値, ②本疾患に特徴的な臓器の障害(唾液腺,涙腺, 膵臓, 後腹膜 ...
Nakamura, Sukio, Hiramatsu, Kazuhisa, Matsushita, Koki, Miyoshi, Tomoko, Mizushima, Takaaki, Ochi, Koji, Asano, Motoi, Mitsunobu, Fumihiro, Koide, Norio, Kataoka, Hitomi   +9 more
core   +1 more source

IgG4-related lymphadenopathy – a difficult diagnosis

Surgical and Experimental Pathology, 2020
Background The IgG4-related disease (IgG4-RD) is a systemic immune-mediated non-neoplastic disease associated with IgG4 positive plasma cells and fibrosis that often presents as a mass lesion.
Balan Louis Gaspar
doaj   +1 more source

Natural history and pathogenesis of IgG4-related disease

, 2015
IgG4-related disease (IgG4-RD) is a systemic fibro-inflammatory condition characterised by elevated serum IgG4 and an abundance of IgG4 plasma cells in involved organs.
Culver, Emma L, Emma L Culver
core   +1 more source

THU0588 CLINICAL PHENOTYPES OF IGG4-RELATED DISEASE IN SPAIN

, 2019
Background: Recently, several clinical phenotypes in IgG4-related disease have been described in a multinational and ethnically variate cohort1. Objectives: To assess the clinical presentation of IgG4-related disease (IgG4-RD) in Spanish patients and ...
Iago Carballo, Blanca Pinilla, Toledano-Macias, M., María Toledano-Macías, Andreu Fernandez-Codina, De Miguel-Campo, B., Martinez-Valle, F., Luis Sáez-Comet, José Hernández-Rodríguez, Saez-Comet, L., Fernandez-Codina, A., Carballo Fernández, Iago, Fernando Martínez-Valle, Borja De Miguel-Campo, Hernandez-Rodriguez, J., Pinilla, B.   +15 more
core   +1 more source

Serial Salivary Gland Ultrasound Monitoring of Treatment Efficacy in IgG4-RD: A Case Report

Journal of Clinical Rheumatology and Immunology
IgG4-related disease (IgG4-RD) is a rare, multisystem, fibroinflammatory disorder with characteristic histopathology. Ongoing research continues to define optimal disease evaluation and management.
Amy Trang, Jennifer K. King, Howard H. Yang   +2 more
doaj   +1 more source

IgG4-related kidney disease [PDF]

Kidney International, 2014
IgG4-related kidney disease (IgG4-RKD) is a comprehensive term for renal lesions associated with IgG4-related disease, which is a recently recognized clinical entity characterized by a dense lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells with fibrosis affecting several organs.
Takako, Saeki, Mitsuhiro, Kawano
openaire   +2 more sources

Case Report: A case of primary IgG4-related skin disease presenting initially with skin papules and abscesses

Frontiers in Immunology
BackgroundImmunoglobulin G (IgG) type 4-related disease (IgG4-RD) is a rare, chronic fibroinflammatory condition that can affect multiple organ systems. Cutaneous involvement in IgG4-RD is even rarer. Moreover, the clinical manifestations of primary IgG4-
Xing-Yue Chen, Jun Chen, Lei Lv, Da-Wei Jiang, Kun-Lan Long, Li-Jia Zhi   +5 more
doaj   +1 more source

IgG4-related disease in patients with newly diagnosed idiopathic retroperitoneal fibrosis: a population-based Danish study

, 2019
Objectives: IgG4-related disease (IgG4-RD) may present as ‘idiopathic’ retroperitoneal fibrosis (IRPF). We aimed to determine the occurrence of IgG4-retroperitoneal fibrosis (IgG4-RPF) in a nationwide study on patients with newly diagnosed IRPF, and to ...
N Lomborg (6531722), CS Bode (6531728), M Jakobsen (6531725), P Junker (3104853)   +3 more
core   +1 more source

Membranoproliferative glomerulonephritis following tubulointerstitial nephritis is a late manifestation of IgG4-related kidney disease: A distinctive case

Human Pathology: Case Reports, 2019
IgG4-related kidney disease (IgG4RKD) generally presents as an active and chronic fibrosing tubulointerstitial nephritis. Recent reports have described glomerular lesions, typically with IgG4 containing subepithelial/membranous deposits as part of ...
Joichi Usui, Steven P. Salvatore, Mourhege Alsaloum, Alla Goldberg, Sheng Kuo, Surya V. Seshan   +5 more
doaj   +1 more source

Immunoglobulin G4-Related Disease Mimicking Asthma

Canadian Respiratory Journal, 2013
Immunoglobulin (Ig) G4-related disease (also known as ‘IgG4-related sclerosing disease’, ‘IgG4-related systemic disease’ or ‘hyper-IgG4-disease’) is a recently recognized systemic fibroinflammatory disease associated with IgG4-positive plasma cells in ...
Hiroshi Sekiguchi, Ryohei Horie, Timothy R Aksamit, Eunhee S Yi, Jay H Ryu   +4 more
doaj   +1 more source