Successful management of refractory pleural effusion due to systemic immunoglobulin light chain amyloidosis by vincristine adriamycin dexamethasone chemotherapy: a case report [PDF]
Journal of Medical Case Reports, 2010 Introduction Refractory pleural effusion in systemic immunoglobulin light chain amyloidosis without cardiac decompensation is rarely reported and has a poor prognosis in general (a median survival of 1.6 months).
Mima Akira +13 more
doaj +4 more sources
Hereditary systemic immunoglobulin light-chain amyloidosis [PDF]
, 2015 Several members of a family died from renal failure as a result of systemic amyloidosis. Extensive studies to detect previously documented gene mutations associated with amyloidosis failed to identify a causative factor.
Benson, Merrill D. +2 more
core +3 more sources
Púrpura: manifestação de amiloidose sistémica primária. [PDF]
Acta Médica Portuguesa, 2009 Primary Systemic Amyloidosis (AL) is the most frequent form of systemic amyloidosis and its morbilility is associated with immunoglobulin light chains deposition in vital organs. The mucocutaneous manifestations occur in about 30-40% of the cases and are
Sara Lestre +4 more
doaj +2 more sources
Amyloid cranial polyneuropathy: A rare neurological presentation of immunoglobulin light‐chain amyloidosis [PDF]
Aging Medicine, 2021 Amyloidosis, a disease with extracellular tissue deposition of fibrils, results in clinical manifestations based on deposition of these fibrils in multiple organ systems.
Abhinav Agarwal +4 more
doaj +2 more sources
Supportive Care and Symptom Management for Patients With Immunoglobulin Light Chain (AL) Amyloidosis [PDF]
Frontiers in Oncology, 2022 Immunoglobulin light chain (AL) amyloidosis is a disorder of clonal plasma cells characterized by deposition of amyloid fibrils in a variety of tissues, leading to end-organ injury.
Christopher E. Jensen +5 more
semanticscholar +2 more sources
Immunoglobulin Light-Chain Amyloidosis: Clinical Presentations and Diagnostic Approach. [PDF]
J Adv Pract Oncol, 2019 Systemic immunoglobulin light-chain (AL) amyloidosis is a rare disorder arising from a plasma cell clone that produces misfolded immunoglobulin light chains, which are deposited in various tissues and organs as amyloid fibrils.
Hwa YL +6 more
europepmc +2 more sources
Recent advances in understanding and treating immunoglobulin light chain amyloidosis [version 1; referees: 2 approved] [PDF]
F1000Research, 2018 Immunoglobulin (Ig) light chain (AL) amyloidosis is a clonal plasma cell disorder characterized by misfolded Ig light chain deposition in vital organs of the body, resulting in proteotoxicity and organ dysfunction.
Talha Badar +2 more
doaj +2 more sources
Oxidative damage in immunoglobulin light chain and transthyretin cardiac amyloidosis – a closer look
Redox Experimental MedicineHeart failure is a progressive disease, representing a growing cause of morbidity, hospitalization, and mortality. An increasingly common type of heart failure with preserved ejection fraction (HFpEF) is an immunoglobulin light chain and transthyretin ...
Elena Cavallone +5 more
doaj +2 more sources
Immunoglobulin light chain amyloidosis presenting as Budd-Chiari syndrome. [PDF]
Hepatol Forum, 2021 Ozercan M +5 more
europepmc +3 more sources
Budd-Chiari Syndrome as the Presenting Feature of Systemic Immunoglobulin Light Chain Amyloidosis. [PDF]
Eur J Case Rep Intern MedMiranda JL +6 more
europepmc +2 more sources