Results 21 to 30 of about 1,619 (168)

CURRENT THERAPIES PRIMARY LANGERHANS CELL HYSTIOCYTOSIS

Hematology, Transfusion and Cell Therapy, 2023
Langerhans cell histiocytosis (LCH) is a neoplastic histiocytic disorder that most commonly affects bones and skin, but it can also involve the bone marrow, liver, spleen, lungs, pituitary gland/central nervous system, and other organs.
Deniz Tuğcu
doaj   +1 more source

Assessment of Hemophagocytic Lympho-Histiocytosis (HLH) in the Setting of Adult Acute Liver Failure. [PDF]

J Viral Hepat
ABSTRACT Hemophagocytic lympho‐histiocytosis (HLH) is a life‐threatening disease, only occasionally presenting as acute liver failure (ALF) in adults. HLH is challenging to diagnose. We reviewed the ALF Study Group (ALFSG) registry for suspected HLH subjects, as well as 184 with other ALF etiologies for cases that might have been missed, assessing ...
Anouti A, Dahshi H, Rule J, Wysocki C, Lee WM, Tujios SR.   +5 more
europepmc   +2 more sources

Frequent NPM1 mutation, monoblastic/monocytic origin and prognostic significance of organ and system involvement in myeloid sarcoma: a multicenter study. [PDF]

J Pathol Clin Res
Abstract Myeloid sarcoma (MS) is a tumorous extramedullary proliferation of blast or blast equivalent cells (e.g., promonocytes or promyelocytes). The most frequent cutaneous presentation is often referred to as leukemia cutis (LC). These lesions, especially without the clinical context of a known bone marrow disease, pose a differential diagnostic ...
Jenei A, Kajtár B, László T, Juratli HA, Vida L, Szepesi Á, Mózes R, Timár B, Halter J, Dirnhofer S, Tzankov A.   +10 more
europepmc   +2 more sources

BRAF V600E mutations in urine and plasma cell-free DNA from patients with Erdheim-Chester disease. [PDF]

, 2014
Erdheim-Chester disease (ECD) is a rare histiocytosis with a high prevalence of BRAF V600E mutation (>50% of patients). Patients with BRAF-mutant ECD can respond to BRAF inhibitors.
Cabrilo, Goran, Erlander, Mark G, Hassaine, Latifa, Holley, Veronica R, Janku, Filip, Kosco, Karena, Kurzrock, Razelle, Leppin, Lorieta, Lin, Patrick P, Meric-Bernstam, Funda, Poole, Jason C, Stepanek, Vanda M, Vibat, Cecile Rose T   +12 more
core   +3 more sources

Indeterminate cell histiocytosis that presented clinically as benign cephalic histiocytosis [PDF]

Dermatology Online Journal, 2015
Indeterminate cell histiocytosis (ICH) is a rare, heterogeneous disorder that is characterized by immunophenotypic features of both Langerhans cell histiocytosis (LCH) and non-LCH. We describe a 12-month-old boy with a four-month history of asymptomatic, small, pink-tan papules on his face.
Haimovic, Adele, Chernoff, Karen, Hale, Christopher S, Meehan, Shane A, Schaffer, Julie V   +4 more
openaire   +4 more sources

BRAF V600E-Positive Multisite Langerhans Cell Histiocytosis in a Preterm Neonate [PDF]

, 2013
Hemorrhagic pustules with a “blueberry muffin” appearance accompanied by respiratory failure in a neonate present a challenging differential diagnosis that includes infections and neoplasms.
Aslam, Muhammad, Badalian-Very, Gayane, Bates, Sara V., Degar, Barbara A., Fleck, Patricia, Green, Adam L., Lakshmanan, Ashwini, Rollins, Barrett J., Terry, Jefferson   +8 more
core   +3 more sources

Malignant histiocytosis: A reassessment of cases formerly classified as histiocytic neoplasms and review of the literature [PDF]

, 1995
Malignant histiocytosis (MH) and true histiocytic lymphoma (THL) are hematopoietic malignancies of the mononuclear phagocytic system distinguished from each other by clinical presentation and presumed cell of origin.
Egeler, R.M. (Maarten), Mannival, C. (C.), Nesbit, M.E. (M.), Schmitz, L. (L.), Sonneveld, P. (Pieter)   +4 more
core   +1 more source

Indeterminate Cell Histiocytosis

Archives of Pathology & Laboratory Medicine, 2003
Abstract Indeterminate cell histiocytosis is a rare disorder involving altered homing mechanisms of the cutaneous histiocytic/dendritic system. It has been described predominantly in adults, with less than a dozen cases in children. A 13-year-old adolescent girl presented with a 4-year history of asymptomatic erythematous nodules and ...
Rodolfo Rodríguez-Jurado, Helena Vidaurri-de la Cruz, Carola Durán-Mckinster, Ramón Ruíz-Maldonado   +3 more
openaire   +1 more source

EPSTEIN-BARR-VIRUS ASSOCIATED SYNDROMES IN IMMUNOSUPPRESSED LIVER-TRANSPLANT RECIPIENTS - CLINICAL PROFILE AND RECOGNITION ON ROUTINE ALLOGRAFT BIOPSY [PDF]

, 1990
The clinical profile and histopathologic changes in needle biopsies of the liver were studied in 10 cases of acute Epstein-Barr virus infection occurring in liver transplant recipients.
DEMETRIS, AJ, MARKIN, RS, RANDHAWA, PS, STARZL, TE   +3 more
core   +1 more source

LANGERHANS CELLS HISTIOCYTOSIS [PDF]

, 2023
Langerhans cell histiocytosis (LCH) merupakan salah satu penyakit terbanyak dari histiositosis dengan 2,0–5,4 kasus/100 juta populasi diseluruh dunia ...
Murti, Krisna, Ulfa, Maria
core   +2 more sources