Listy klinicke logopedie, 2020 Inner ear malformation comprises a broad group of disorders, the main symptom of which is hearing loss. The disorder occurs during the embryonic development of the auditory system. Only about 20 % of malformations can be diagnosed radiologically. Hearing
Dagmar Hošnová, Milan Urík
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Recurrent Meningitis in Congenital Inner Ear Malformation [PDF]
Ear, Nose & Throat Journal, 2021 Spontaneous cerebrospinal fluid otorrhea is very rare. Because of nonspecific symptoms, it is usually diagnosed when complications such as meningitis occur.
Aleksander Zwierz MD, PhD +2 more
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Simultaneous closure of a perilymphatic fistula and placement of cochlear implant in a case of complex inner ear malformation [PDF]
Clinical Case ReportsKey Clinical Message In young infants, under the age of one‐year, cochlear malformation with profound hearing loss complicated by a perilymphatic fistula (PLF), presents a serious clinical challenge, warranting immediate audiological and surgical ...
Hanan Almuzaini +4 more
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Failed cochlear implant followed by auditory brainstem implant in a patient with Mondini malformation and uncontrolled otomastoiditis: a case report [PDF]
Journal of Medical Case ReportsBackground Cochlear implant (CI) implantation is the standard intervention for children with severe-to-profound hearing loss, including those with inner ear malformations, such as Mondini malformation.
Arthaya Pongsupatt +5 more
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Genetics of Inner Ear Malformations: A Review [PDF]
Audiology Research, 2021 Inner ear malformations are present in 20% of patients with sensorineural hearing loss. Although the first descriptions date to the 18th century, in recent years the knowledge about these conditions has experienced terrific improvement. Currently, most of these conditions have a rehabilitative option.
Davide Brotto +6 more
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Comparing the Patients with or without Inner Ear Malformations in Terms of Intra and Postoperative Complications of Cochlear Implantation [PDF]
Iranian Journal of Otorhinolaryngology, 2023 Introduction:Since 20% of the patients with sensorineural hearing loss have confirmed radiographically inner ear malformation, this study aimed to compare the incidence rate of intra and postoperative complications of cochlear implantation amongst the ...
Adib Molaei Sisakht +2 more
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Recurrent bacterial meningitis caused by incomplete Type I inner ear malformation: A case report [PDF]
IbrainTao Liang
exaly +2 more sources
Cochlear and Vestibular Volumes in Inner Ear Malformations
Otology & Neurotology, 2022 Objective A “gold standard” for quantitatively diagnosing inner ear malformations (IEMs) and a consensus on normative measurements are lacking. Reference ranges and cutoff values of inner ear dimensions may add in distinguishing IEM types.
Breitsprecher, Tabita M +11 more
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Common molecular etiologies are rare in nonsyndromic Tibetan Chinese patients with hearing impairment. [PDF]
PLoS ONE, 2012 Thirty thousand infants are born every year with congenital hearing impairment in mainland China. Racial and regional factors are important in clinical diagnosis of genetic deafness.
Yongyi Yuan +10 more
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Imaging of inner ear malformations: a primer for radiologists [PDF]
La radiologia medica, 2021 AbstractIn the multidisciplinary management of patients with inner ear malformations (IEMs), the correct diagnosis makes the differences in terms of clinical and surgical treatment. The complex anatomical landscape of the inner ear, comprising several small structures, makes imaging of this region particularly challenging for general radiologists ...
Feraco, Paola +2 more
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