Results 71 to 80 of about 341,590 (292)

Expression of interferon-regulated genes in juvenile dermatomyositis versus Mendelian autoinflammatory interferonopathies

open access: yesArthritis Research & Therapy, 2020
Background Juvenile dermatomyositis (JDM) is a systemic autoimmune disease with a prominent interferon (IFN) signature, but the pathogenesis of JDM and the etiology of its IFN signature remain unknown.
Hanna Kim   +12 more
semanticscholar   +1 more source

Comparison between treatment naive juvenile and adult dermatomyositis muscle biopsies: difference of inflammatory cells phenotyping

open access: yesAdvances in Rheumatology, 2018
Background Different inflammatory cells (i.e., CD4, CD8, CD20 and CD68) are involved in pathogenesis of DM muscle. In this context, the aim of this study was to assess and compare these inflammatory cell phenotyping in muscle samples of treatment naive ...
Samuel Katsuyuki Shinjo   +5 more
doaj   +1 more source

Juvenile amyopathic dermatomyositis

open access: yesDermatology Online Journal, 2005
A 3-year-old girl presented with a 6-month history of multiple, light-pink, flat-topped papules over the dorsal aspects of the metacarpophalangeal and interphalangeal joints of the hands and feet. Nailfold telangiectases, ragged cuticles, and a heliotrope color of the upper eyelids were also evident, but there was no clinical evidence of muscle ...
Henning, J Scott   +3 more
openaire   +5 more sources

Design of the muscles in motion study: a randomized controlled trial to evaluate the efficacy and feasibility of an individually tailored home-based exercise training program for children and adolescents with juvenile dermatomyositis [PDF]

open access: yes, 2012
BACKGROUND: Juvenile dermatomyositis (JDM) is a rare, often chronic, systemic autoimmune disease of childhood, characterized by inflammation of the microvasculature of the skeletal muscle and skin. Prominent clinical features include significant exercise
Anneli C Langbroek-Amersfoort   +4 more
core   +2 more sources

Porto‐sinusoidal vascular disorder in a pediatric patient with prolidase deficiency: A case report

open access: yesJPGN Reports, EarlyView.
Abstract Prolidase deficiency (PD) is a rare autosomal recessive disorder affecting collagen turnover, leading to diverse clinical manifestations including dermatologic lesions, hepatosplenomegaly, and vascular anomalies. Liver involvement in PD is poorly understood, with few reported cases.
Melissa Castro   +5 more
wiley   +1 more source

Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases

open access: yesClinical Dermatology Review
Dermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as ...
Mrunali Anil Joshi   +4 more
doaj   +1 more source

The effect of blended tube feeding compared to conventional formula on clinical outcomes in adults: A systematic review

open access: yesNutrition &Dietetics, EarlyView.
Abstract Aim To explore the effect of blended tube feeding compared to conventional formulas on nutritional status, quality of life, anthropometry, diarrhoea and tube blockages in adults receiving tube feeding. Methods The protocol was registered (PROSPERO CRD42022372443).
Lina Breik   +3 more
wiley   +1 more source

Case Report: IVIG causing bilateral papilledema and increased intracranial hypertension in patients with anti-TIF-1γ antibody-positive JDM

open access: yesFrontiers in Pediatrics
Juvenile dermatomyositis is a systemic autoimmune disease characterized by progressive proximal muscle weakness, pathognomonic rashes, and often the presence of myositis-specific antibodies.
Sarah Baluta   +3 more
doaj   +1 more source

Inflammatory Myopathies with Cutaneous Involvement: from Diagnosis to Therapy

open access: yesFolia Medica, 2017
The group of idiopathic inflammatory myopathies (IIM) include various disorders of skeletal muscles with or without skin involvement. The most common types are dermatomyositis (DM), polymyositis (PM), inclusion body myositis (IBM) and necrotizing ...
Dourmishev Lyubomir A.
doaj   +1 more source

Disease course, frequency of relapses and survival of 73 patients with juvenile or adult dermatomyositis [PDF]

open access: yes, 2005
Objective Our aim is to present the disease course, frequency of relapses and survival of juvenile and adult dermatomyositis (JDM/DM) patients. Methods Analysis was performed using data on 73 patients. The median follow-up for 38 JDM patients was
Balogh, Zsolt   +9 more
core  

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