Results 51 to 60 of about 3,332 (178)

Selective deletion of PPARβ/δ in fibroblasts causes dermal fibrosis by attenuated LRG1 expression. [PDF]

, 2018
Connective tissue diseases of the skin are characterized by excessive collagen deposition in the skin and internal organs. Fibroblasts play a pivotal role in the clinical presentation of these conditions.
Chan, JSK, Chen, J.P., Chiba, S., Koh, NJN, Ng, X.R., Pal, M., Phua, T., Sng, M.K., Tan, C.K., Tan, EHP, Tan, N.S., Teo, Z., Tnay, Y.L., Tong, BMK, Wahli, W., Wang, X., Wee, JWK, Zhu, P.   +17 more
core   +4 more sources

Juvenile localized scleroderma

Sri Lanka Journal of Child Health, 2019
No abstract available Sri Lanka Journal of Child Health, 2019; 48(4): 364 ...
Luis Zavaleta-Medina, P. W. Sánchez G., Karen E. Sánchez Ramirez, Diego A. Cedamanos Alva, Jose Caballero   +4 more
openaire   +2 more sources

Ultrasonography, MRI and classic radiography of skin and MSK involvement in juvenile scleroderma

Journal of Ultrasonography, 2020
Scleroderma is a rare, autoimmune, chronic condition that affects the connective tissue by excessive collagen production. If diagnosed before the age of 16, it is referred to as juvenile scleroderma.
Idzior Marta, Sotniczuk Maria, Michalski Emil, Gietka Piotr, Sudoł-Szopińska Iwona   +4 more
doaj   +1 more source

Factors associated with adherence to treatment in children and adolescents with chronic rheumatic diseases [PDF]

, 2012
OBJECTIVE: There are several factors that contribute to poor adherence to treatment in children and adolescents with chronic rheumatic diseases, worsening their quality of life and prognosis.
Barbosa, Cassia Maria Passarelli Lupoli, Bugni, Vanessa Miotto, Hilário, Maria Odete Esteves, Len, Claudio Arnaldo, Okamoto, Karine Yoshiye Kajiyama, Ozaki, Luciana da Silva, Terreri, Maria Teresa Ramos Ascensão   +6 more
core   +3 more sources

Localized scleroderma in a newborn (case report) [PDF]

РМЖ. Мать и дитя, 2022
N.I. Akhmina1, P.S. Utkin2, M.P. Shalatonin3, Zh.L. Chabaidze1, A.A. Dement’ev1, A.L. Zaplatnikov1 1Russian Medical Academy of Continuous Professional Education, Moscow,   Russian Federation 2Children’s Infectious Clinical Hospital
N.I. Akhmina, P.S. Utkin, M.P. Shalatonin, Zh.L. Chabaidze, A.A. Dementiev, A.L. Zaplatnikov   +5 more
doaj  

“You can't do this, you've arthritis":Exploring the experiences of education and employment of young people with arthritis [PDF]

, 2018
Introduction: Vocational development is an integral component of adolescence with several key educational transitions occurring during this stage of life.
Farre, Albert, McDonagh, Janet E., McNiven, Abigail, Ryan, Sara, Ziebland, Sue   +4 more
core   +2 more sources

Clinical Profile of Methotrexate-resistant Juvenile Localised Scleroderma

Acta Dermato-Venereologica, 2019
Methotrexate has demonstrated its efficiency for the treatment of juvenile localized scleroderma but some patients may be resistant. The aim of our study was to define the profile of such patients.
Juliette Hardy, Franck Boralevi, Stéphanie Mallet, Natalia Cabrera, Alexandre Belot, Alice Phan, Sébastien Barbarot, Audrey Duriez-Lasek, Christine Chiaverini, Thomas Hubiche, Emmanuel Mahé, Edouard Bégon, Emmanuelle Bourrat, Olivia Boccara, Hélène Aubert, Martine Grall Lerosey, Catherine Droitcourt, Maryam Piram, Juliette Mazereeuw-Hautier, Research Group of the French Society of Paediatric Dermatology (SDFP in French)   +19 more
doaj   +1 more source

The frequency of pulmonary hypertension in patients with juvenile scleroderma

Biomolecules & Biomedicine, 2015
Juvenile scleroderma (JS) represents a rarely seen group of connective tissue diseases with multiple organ involvement. Cardiac involvement in JSS is well known and, although rare in children, it may be an important cause of mortality and morbidity ...
Amra Adrovic, Funda Oztunc, Kenan Barut, Aida Koka, Refet Gojak, Sezgin Sahin, Tuncalp Demir, Ozgur Kasapcopur   +7 more
doaj   +1 more source

Systemic sclerosis : state of the art on clinical practice guidelines [PDF]

, 2018
Systemic sclerosis (SSc) is an orphan disease characterised by autoimmunity, fibrosis of the skin and internal organs, and vasculopathy. SSc may be associated with high morbidity and mortality.
Airo, Paolo, Alexander, Tobias, Allanore, Yannick, Bombardieri, Stefano, Bruni, Cosimo, Burmester, Gerd, Codullo, Veronica, Cutolo, Maurizio, Dalm, Virgil, De Vries-Bouwstra, Jeska, Della Rossa, Alessandra, Distler, Oliver, Eurico, Fonseca João, Frank, Charissa, Galetti, Ilaria, Hachulla, Eric, Houssiau, Frederic, Launay, David, Lepri, Gemma, Mathian, Alexis, Matucci-Cerinic, Marco, Mosca, Marta, Mouthon, Luc, Mueller-Ladner, Ulf, Ruaro, Barbara, Schneider, Matthias, Scirè, Carlo Alberto, Smith, Vanessa, Sulli, Alberto, Talarico, Rosaria, Tincani, Angela, Van den Hoogen, Frank, van Laar, Jacob M, Van Vollenhoven, Ronald, Vandecasteele, Els, Vanhaecke, Amber, Vanthuyne, Marie, Vieira, Ana, Voskuyl, Alexandre E, Zanatta, Elisabetta   +39 more
core   +4 more sources

An i2b2-based, generalizable, open source, self-scaling chronic disease registry [PDF]

, 2014
Objective: Registries are a well-established mechanism for obtaining high quality, disease-specific data, but are often highly project-specific in their design, implementation, and policies for data use.
Bousvaros, Athos, Ilowite, Norman T, Inman, Christi J, Mandl, Kenneth D, Marsolo, Keith, McMurry, Andrew J, Natter, Marc D, Ortiz, David M, Quan, Justin, Sandborg, Christy I, Schanberg, Laura E, Wallace, Carol A, Warren, Robert W, Weber, Griffin M   +13 more
core   +1 more source