Results 171 to 180 of about 5,662 (212)

Collodion baby and lamellar ichthyosis

Journal of Cutaneous Pathology, 1998
It is important to differentiate the collodion baby from harlequin ichthyosis as the latter rarely survives past the first few days of life. Occasionally, babies share features of both disorders and defy a clinical diagnosis. We recently encountered such a baby who initially presented with harlequin‐like features, but evolved into lamellar ichthyosis ...
B, Sandler, K, Hashimoto
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Cyclosporine in lamellar ichthyosis.

Archives of dermatology, 1989
In an open trial, five patients with lamellar ichthyosis showed no response to four weeks of treatment with oral cyclosporine (cyclosporine A) (6 mg/kg/d). Histologic examination of lamellar ichthyosis revealed hyperkeratosis; psoriasiform acanthosis; dilated, tortuous capillaries; and a slight perivascular lymphocytic infiltrate.
V C, Ho, A K, Gupta, C N, Ellis, K D, Cooper, B J, Nickoloff, J J, Voorhees   +5 more
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Lamellar ichthyosis with bilateral ectropion

Nigerian Journal of Ophthalmology, 2015
Lamellar ichthyosis is a rare congenital disorder with ocular manifestation resulting from the cicatrization of anterior lamella of eyelids. Early diagnosis and management of ectropion can prevent the most severe complications such as severe dry eyes, corneal perforation, and possible loss of the eye.
Jain, Gunjan, Jain, Vaibhav Kumar, Sharma, Reena, Sharma, Indra Kumar, Verma, Ganesh Kumar   +4 more
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Lamellar Ichthyosis

Pediatrics In Review, 1981
Congenital ichthyoses represent a heterogeneous group of rare skin diseases. The disorders are heritable and have in common a varying degree of hyperkeratosis. During the years there has been much confusion regarding the classification of the ichthyoses.
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Lamellar Ichthyosis and Psoriasis

Archives of Dermatology, 1973
To the Editor.— The following is an unusual presentation of two epidermal disorders in one patient. Report of a Case A 21-year-old man with a past history of lamellar ichthyosis was first seen in the University Hospital at San Diego with a three week history of a papulosquamous eruption on the trunk, extremities (including the elbows), and scalp. At
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Cicatricial Ectropion Associated With Lamellar Ichthyosis

Archives of Ophthalmology, 1973
An 8-year-old boy with lamellar ichthyosis had bilateral cicatricial ectropion of the lower eyelids. His entire body was affected including the palms and soles. Post auricular grafts were successfully used to repair the ectropion. Of the four categories of ichthyosis, the lamellar type is associated with the presence of ectropion and the resultant ...
R D, Shindle, C R, Leone
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Lamellar ichthyosis with laminated membrane structures

British Journal of Dermatology, 1993
Summary We review the published classifications of autosomal recessive congenital ichthyosis. and report a newcase of congenital ichthyosis which presents the characteristics of ichthyosis congenita type III.In 1988 Arnold cm/.' de.scribed a new type of congenitalichthyosis (ichthyosis congenita.
A, Patrizi, I, Neri, V, Di Lernia, G, Pasquinelli, L, Badiali de Giorgi   +4 more
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Lamellar Ichthyosis in a Saudi Kindred

SKINmed: Dermatology for the Clinician, 2007
A series of 20 patients aged 4–16 years presented with lamellar ichthyosis at the dermatology unit of King Faisal Hospital at Taif in western Saudi Arabia. Though they had come from different families, they all belonged to the same tribe that was confined to a rural area in the precincts of Taif. The tribe is known for consanguineous marriages.
Daifullah, Al Aboud, Khalid, Al Aboud, V, Ramesh, Joginder, Kumar   +3 more
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Ocular Manifestations of Congenital Lamellar Ichthyosis

European Journal of Ophthalmology, 2005
Purpose To describe the ophthalmic manifestations in a series of children with congenital lamellar ichthyosis. These cases presented with varying types of eyelid abnormality associated with the systemic disease. The clinical features and ophthalmic management were studied.
A J, Singh, P L, Atkinson
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Genetics of lamellar ichthyosis

Egyptian Journal of Dermatology and Venereology
Ichthyosis is a dermatological condition that causes the skin in a wide range of integumentary regions of the body to become dry, rough, and scaly. Ichthyosis affect 5–10/100 000 people worldwide. Lamellar ichthyosis (LI) is part of autosomal recessive congenital ichthyosis and is a significant type of inherited ichthyosis in no-syndromic form ...
Ziske Maritska, Sandria Sandria, Nunung Noviyanti, Ulfa M. Lubis, Maretha W. Astria, Merta A. Prastika, Priya A. Chandra, Raden Satria Surya Chandra   +7 more
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