Transcriptional inhibition of type I collagen gene expression in scleroderma fibroblasts by the antineoplastic drug ecteinascidin 743. [PDF]
, 2003 We previously showed that COL1A1 expression is up-regulated at the transcriptional level in systemic sclerosis (SSc) fibroblasts and that the CCAAT-binding factor (CBF) is involved in this increased expression.
Herrick, David J +3 more
core +2 more sources
Linear atrophoderma of Moulin: a case report and review of the literature
Dermatology Practical & Conceptual, 2013 Linear atrophoderma of Moulin is a rare, acquired, linear dermatosis. We present a 17-year-old girl with multiple asymptomatic brownish atrophic plaques in a zosteriform distribution on the left side of the trunk.
Aikaterini Patsatsi +3 more
doaj +1 more source
Evaluation of estimated glomerular filtration rate and clinical variables in systemic sclerosis patients [PDF]
, 2016 Objectives: The most important renal complication of systemic sclerosis (SSc) is scleroderma renal crisis (SRC). Many patients demonstrate less severe renal complications, most likely associated with reduced renal blood flow and a consequent reduction in
Amoroso, Antonio +7 more
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Optimal management strategies for paediatric morphea – insights from a case series
Pediatria PolskaJuvenile localized scleroderma, or morphea, is a rare chronic inflammatory disease primarily affecting the skin and subcutaneous tissue. Treatment options for paediatric cases are diverse, with a lack of standardised guidelines.
Kinga Łagosz +6 more
doaj +1 more source
Parry-Romberg syndrome: A case with a possible association with lyme disease [PDF]
, 2015 Parry-Romberg syndrome is an acquired slowly progressive disease characterized by an atrophy mostly involving half of the face. The pathogenesis of this disfiguring condition is still controversial.
Di Meo, N. +4 more
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En coup de sabre morphea: An uncommon condition in Africa
Dermatology Reports, 2022 The term en coup de sabre morphea refers to a lesion of linear morphea typically located in the frontoparietal scalp and/or the paramedian forehead, often resembling a strike with a sword.
Lehlohonolo Makhakhe +3 more
doaj +1 more source
Scleroderma and dentistry: Two case reports [PDF]
, 2016 © 2016 The Author(s).Background: Scleroderma is a chronic connective tissue disorder with unknown etiology. It is characterized by excessive deposition of extracellular matrix in the connective tissues causing vascular disturbances which can result in ...
Bornstein, Michael M. +4 more
core +1 more source
Prognostic impact of coronary microcirculation abnormalities in systemic sclerosis: a prospective study to evaluate the role of non-invasive tests [PDF]
, 2013 INTRODUCTION: Microcirculation dysfunction is a typical feature of systemic sclerosis (SSc) and represents the earliest abnormality of primary myocardial involvement.
CAULI, ALBERTO +9 more
core +1 more source
Journal of Medical Case Reports, 2019 Background Parry–Romberg syndrome, also known as progressive hemifacial atrophy, is a rare degenerative disorder with numerous distinctive clinical presentations. It is usually slowly progressive, occurring more in females, and affects primarily one side
Jimmy Girgis William Abdelnour +3 more
doaj +1 more source
Atypical Neuroimaging Manifestations of Linear Scleroderma "en coup de sabre". [PDF]
Iran J Child Neurol, 2015 M Allmendinger A +4 more
europepmc +2 more sources