Results 21 to 30 of about 279,908 (354)
Trends in Cardiovascular Medicine, 1992 The familial long-QT syndrome (LQTS) is an infrequently occurring disorder in which affected family members have QT prolongation on the ECG, often associated with recurrent syncope and fatal ventricular arrhythmias. Autosomal recessive and autosomal dominant modes of inheritance were suggested by the pattern of occurrence of this disorder in the first ...
Arthur J. Moss, Jennifer L. Robinson
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Drug-induced Fatal Arrhythmias: Acquired long QT and Brugada Syndromes [PDF]
, 2017 Since the early 1990s, the concept of primary “inherited” arrhythmia syndromes or ion channelopathies has evolved rapidly as a result of revolutionary progresses made in molecular genetics.
Ai, Tomohiko +3 more
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Long QT syndrome in a neonate [PDF]
, 2015 Congenital long QT syndrome (cLQTS) is a channelopathy characterized by ventricular repolarization disturbances. The clinical presentation varies from an asymptomatic patient to a patient with recurrent syncopes, seizures, and even sudden death.
Morales Rodríguez, Idelma Berenise +3 more
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Annals of Noninvasive Electrocardiology, 1998 Major progress has taken place, and at a very rapid pace, in the understanding of the congenital long QT syndrome (LQTS). This has been the direct consequence of the identification of several of the genes responsible for LQTS and of the studies that have followed, at both basic and clinical levels.
Silvia G. Priori, Peter J. Schwartz
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Circulation, 2020 Supplemental Digital Content is available in the text. Background: Long QT syndrome (LQTS) is a rare genetic disorder and a major preventable cause of sudden cardiac death in the young.
N. Lahrouchi +105 more
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Meta-analysis of T peak –T end and T peak –T end /QT ratio for risk stratification in congenital long QT syndrome [PDF]
, 2018 Background and objectives: Congenital long QT syndrome (LQTS) predisposes affected individuals to ventricular tachycardia/fibrillation (VF/VF), potentially resulting in sudden cardiac death.
Baranchuk, Adrian M. +12 more
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Pediatria i Medycyna Rodzinna, 2014 Resting electrocardiogram is a basic diagnostic tool used to identify myocardial diseases caused by a genetic defect of ion channels that results in bioelectric instability of cardiomyocytes and the risk of a complex induction of life-threatening ...
Zbigniew Krenc
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Prevalencia de patrones electrocardiográficos asociados a muerte súbita en la población española de 40 años o más. Resultados del estudio OFRECE [PDF]
, 2017 [Abstract] Introduction and objectives. Some electrocardiographic patterns are associated with an increased risk of sudden cardiac death due to ventricular arrhythmias. There is no information on the prevalence of these patterns in the general population
Alonso Martín, Joaquín Jesús +11 more
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QT correction using Bazett’s formula remains preferable in long QT syndrome type 1 and 2
Annals of Noninvasive Electrocardiology, 2020 The heart rate (HR) corrected QT interval (QTc) is crucial for diagnosis and risk stratification in the long QT syndrome (LQTS). Although its use has been questioned in some contexts, Bazett's formula has been applied in most diagnostic and prognostic ...
P. Dahlberg +4 more
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Outcome by Sex in Patients With Long QT Syndrome With an Implantable Cardioverter Defibrillator
Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease, 2020 Background Sex differences in outcome have been reported in patients with congenital long QT syndrome. We aimed to report on the incidence of time‐dependent life‐threatening events in male and female patients with long QT syndrome with an implantable ...
Arwa Younis +11 more
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