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Lymphangioleiomyomatosis [PDF]
European Respiratory Journal, 2006 Lymphangioleiomyomatosis (LAM) is a rare disease of the lungs and lymphatics, which can occur sporadically or in association with tuberous sclerosis. LAM almost exclusively affects females, generally developing before the menopause.The disease is characterised by progressive pulmonary cystic change, recurrent pneumothorax, chylous pleural collections ...
Simon R. Johnson
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Brazilian Thoracic Association recommendations for the management of lymphangioleiomyomatosis [PDF]
Jornal Brasileiro de PneumologiaLymphangioleiomyomatosis (LAM) is a rare disease, characterized as a low-grade neoplasm with metastatic potential that mainly affects women of reproductive age, in which there is proliferation of atypical smooth muscle cells (LAM cells) and formation of ...
Bruno Guedes Baldi +13 more
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Uterine lymphangioleiomyomatosis in a premenopausal woman with tuberous sclerosis: A case report [PDF]
Case Reports in Women's HealthLymphangioleiomyomatosis is a rare disease characterized by abnormal smooth muscle cell growth. It primarily occurs in the lungs but can also rarely occur in other organs, in which case it is classified as extrapulmonary lymphangioleiomyomatosis.
Eun Min Lee +3 more
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Lung transplantation for lymphangioleiomyomatosis. N [PDF]
Journal of Bronchology, 1997 Lymphangioleiomyomatosis is a rare disease of unknown origin that usually leads to progressive deterioration of lung function and eventual death from respiratory failure. It occurs in women of reproductive age and people with tuberous sclerosis. Lung transplantation is a recent therapeutic approach.We conducted a retrospective study by questionnaire of
A. Boehler +3 more
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Presse medicale (Paris, France : 1983), 2010 Lymphangioleiomyomatosis is caused by mutations (usually sporadic, sometimes in tuberous sclerosis) of the TSC1 or TSC2 genes and results in cystic destruction of the lungs, with CT features being sufficiently characteristic to establish the diagnosis in many cases. Two-thirds of patients suffer pneumothoraces.
Yusra Sheikh, Andrew Dixon
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A challenging convergence of conditions in a patient with thalassemia major presenting with thymoma and lymphangioleiomyomatosis: a case report [PDF]
Journal of Medical Case ReportsBackground β-Thalassemia major is a complex, multisystemic condition. Effective transfusion programs, optimal iron chelation therapy, and progresses in magnetic resonance imaging have significantly improved patient survival.
Aldo Carnevale +6 more
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Pulmonary Lymphangioleiomyomatosis [PDF]
Pneumologie, 2002 U. Costabel, J. Guzman
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Abdominal lymphangioleiomyomatosis in a man presenting with gastrointestinal hemorrhage as the first manifestation: a case report [PDF]
Frontiers in MedicineLymphangioleiomyomatosis (LAM) is a rare, low-grade malignant condition that typically affects women of childbearing age and primarily involves the lungs. While cases involving males and affecting the gastrointestinal tract are exceedingly uncommon. This
Ying Zi, Yuchen Shi, Rongjie Shi
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La Presse Médicale, 2023 Lymphangioleiomyomatosis (LAM) is an ultra-rare, slowly progressive neoplastic cystic disease, belonging to the group of PEComas. It can occur sporadically or associated to tuberous sclerosis complex disease and affects mainly women in child-birth age.
Elia, Davide +4 more
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Lymphangioleiomyomatosis [PDF]
Klinicka Onkologie, 2019 Lymphangioleiomyomatosis (LAM) is a rare systemic disease that occurs sporadically (S/LAM) or as part of tuberous sclerosis (TS/LAM). LAM is characterized by proliferation of abnormal smooth muscle cells. This disease clinically manifests as dyspnea on exertion and pneumothorax.
Martina, Doubková +4 more
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