Results 31 to 40 of about 6,813 (202)
Non-pharmacological therapies for patients with lymphangioleiomyomatosis: a systematic review and meta-analysis [PDF]
Frontiers in Rehabilitation SciencesObjectivesThis study aims to systematically review non-pharmacological therapies for patients with lymphangioleiomyomatosis (LAM), and synthesize the effects of non-pharmacological therapies on 6-minute walking distance test (6MWDT), pulmonary function ...
Yingwen Yu, Fang Lei, Huizi Wang
doaj +2 more sources
Although the diagnosis of tuberous sclerosis complex-lymphangioleiomyomatosis (TSC-LAM) is rare in adolescents, emerging data suggest that its true incidence, particularly among females with TSC, may be underestimated.
Alexander J. Towbin +3 more
core +3 more sources
Lymphangioleiomyomatosis [PDF]
Seminars in Respiratory and Critical Care Medicine, 2020 AbstractLymphangioleiomyomatosis (LAM) is a slow albeit progressive rare neoplastic disease featured with diffuse thin-walled cysts in lungs and angiomyolipomas in kidneys. LAM affects almost exclusively women and has one of the strongest gender predispositions of any extragenital human disease. Two forms of LAM present clinically, sporadic (S-LAM) and
Kai-Feng, Xu +9 more
openaire +3 more sources
Effectiveness of pulmonary rehabilitation in lymphangioleiomyomatosis
Indian Journal of Respiratory Care, 2021 Lymphangioleiomyomatosis (LAM) is a cystic lung disease frequently associated with reduced exercise capacity, mostly affecting young women. The disease is characterized by progressive pulmonary cystic change, recurrent pneumothorax, chylous pleural ...
Manivel Arumugam +3 more
doaj +1 more source
Lymphangioleiomyomatosis [PDF]
Klinicka Onkologie, 2019 Lymphangioleiomyomatosis (LAM) is a rare systemic disease that occurs sporadically (S/LAM) or as part of tuberous sclerosis (TS/LAM). LAM is characterized by proliferation of abnormal smooth muscle cells. This disease clinically manifests as dyspnea on exertion and pneumothorax.
Martina, Doubková +4 more
openaire +2 more sources
Lymphangioleiomyomatosis and Langerhans cell histiocytosis - two case reports from our practice [PDF]
Srpski Arhiv za Celokupno Lekarstvo, 2022 Introduction. Lymphangioleiomyomatosis and pulmonary Langerhans cell histiocytosis are the most common pulmonary cystic diseases. Although they differ in pathogenesis, they share several features.
Milenković Ana +4 more
doaj +1 more source
Human Pathology: Case Reports, 2020 A 47 yo woman underwent resection of an endometrial adenocarcinoma with pelvic lymph node biopsies. She was found to have incidental nodal lymphangioleiomyomatosis (LAM).
Charles M. Lombard
doaj +1 more source
Advanced Science, 2023 Lymphangioleiomyomatosis (LAM) is a rare disease involving cystic lung destruction by invasive LAM cells. These cells harbor loss‐of‐function mutations in TSC2, conferring hyperactive mTORC1 signaling. Here, tissue engineering tools are employed to model
Adam Pietrobon +17 more
doaj +1 more source
Airspace Enlargement with Fibrosis in a Young Heavy Smoker Mimicking Diffuse Cystic Lung Disease
Medicina, 2022 The widespread use of computed tomography (CT) has led to the increased recognition of cystic lung lesions. Multiple pulmonary cysts can be observed in heterogeneous disorders called diffuse cystic lung diseases (DCLDs), which include pulmonary ...
Kyungsoo Bae +2 more
doaj +1 more source
Lymphangioleiomyomatosis [PDF]
Archivos de Bronconeumología ((English Edition)), 2011 Lymphangioleiomyomatosis (LAM) is a rare disease that mainly affects women, particularly at fertile age. It is sporadic or associated with tuberous sclerosis complex. It is characterised by an abnormal proliferation of immature smooth muscle cells (SMC), which grow aberrantly in the airway, parenchyma, lymphatics and pulmonary blood vessels and which ...
Ansotegui Barrera, Emilio +3 more
openaire +4 more sources