Results 51 to 60 of about 6,813 (202)

Meningiomas in Lymphangioleiomyomatosis [PDF]

JAMA, 2001
Lymphangioleiomyomatosis (LAM), a cystic lung disease associated with progressive respiratory failure, is found predominantly in women of childbearing age and therefore has been treated with progesterone and other hormonal agents. However, meningiomas have progesterone receptors, and progesterone is believed to be a mitogen for meningioma cells in ...
J, Moss, R, DeCastro, N J, Patronas, A, Taveira-DaSilva   +3 more
openaire   +2 more sources

An entity that poses continuous challenge despite treatment attempt: lymphangioleiomyomatosis

The Pan African Medical Journal, 2020
In May of 2016, a 37-years-old Hispanic female, with no significant past medical history was brought to our hospital with right-sided chest pain. Chest X ray revealed large right pneumothorax (A) and she underwent chest tube placement.
Munish Sharma, Salim Surani
doaj   +1 more source

Lymphangioleiomyomatosis in a Male [PDF]

The Annals of Thoracic Surgery, 2015
We report a 17-year-old male with a histopathologic diagnosis of lymphangioleiomyomatosis after surgery for a pneumothorax. In general, lymphangioleiomyomatosis has been considered a female-specific disease. However, there are a few lymphangioleiomyomatosis cases reported in males, and our patient is the youngest case reported. Spontaneous pneumothorax
Kazuhiro, Wakida, Yui, Watanabe, Toshio, Kumasaka, Kuniaki, Seyama, Keiko, Mitani, Tsubasa, Hiraki, Go, Kamimura, Toshiyuki, Nagata, Yoshihiro, Nakamura, Masami, Sato   +9 more
openaire   +2 more sources

Recognizing, Diagnosing, and Treating Lymphangioleiomyomatosis

, 2022
Objective: To review the clinical features, diagnostic approach, and treatment of lymphangioleiomyomatosis (LAM). The presenting symptoms of LAM are common complaints seen in family medicine.
Smiley, Shelby L
core   +1 more source

Tuberous sclerosis complex presenting as pulmonary lymphangioleiomyomatosis - a clinicoradiological diagnosis

The Pan African Medical Journal, 2015
Tuberous sclerosis complex (TSC) manifests predominantly as a neurocutaneous disorder. Lymphangioleiomyomatosis (LAM) is a rare pulmonary manifestation of TSC.
Kamini Gupta, Amit Goyal, Kavita Saggar, Avik Banerjee   +3 more
doaj   +1 more source

Brazilian Thoracic Association recommendations for the management of lymphangioleiomyomatosis [PDF]

Jornal Brasileiro de Pneumologia
Lymphangioleiomyomatosis (LAM) is a rare disease, characterized as a low-grade neoplasm with metastatic potential that mainly affects women of reproductive age, in which there is proliferation of atypical smooth muscle cells (LAM cells) and formation of ...
Bruno Guedes Baldi, Paulo Henrique Ramos Feitosa, Adalberto Sperb Rubin, Alexandre Franco Amaral, Carolina Salim Gonçalves Freitas, Cláudia Henrique da Costa, Eliane Viana Mancuzo, Ellen Caroline Toledo do Nascimento, Mariana Sponholz Araujo, Marcelo Jorge Jacó Rocha, Martina Rodrigues de Oliveira, Tatiana Senna Galvão, Pedro Paulo Teixeira e Silva Torres, Carlos Roberto Ribeiro Carvalho   +13 more
doaj   +1 more source

Cathepsin-k expression in pulmonary lymphangioleiomyomatosis

, 2009
Lymphangioleiomyomatosis is a rare and progressive lung cystic disease, caused by the infiltration of lung parenchyma by mesenchymal cells characterized by co-expression of contractile proteins and melanocytic markers.
CHILOSI, Marco, BONETTI, Franco, MARTIGNONI, Guido, BRUNELLI, Matteo, GOBBO, Stefano, Pea M., Poletti V.   +6 more
core   +1 more source

Safety and Efficacy of Combined Resveratrol and Sirolimus in Lymphangioleiomyomatosis

, 2023
BACKGROUND: A critical need exists to develop remission-inducing therapies for lymphangioleiomyomatosis. RESEARCH QUESTION: Is the addition of resveratrol safe and more efficacious than sirolimus alone in patients with lymphangioleiomyomatosis?
McCormack, Francis X, Robbins, Nathan, Swigris, Jeffrey, Jeffrey Swigris, Adam G. Cole, Gupta, Nishant, Susan McMahan, Singla, Abhishek, Marina K. Holz, Zhou, Yuan, McMahan, Susan, Abhishek Singla, Nishant Gupta, Kopras, Elizabeth J, Holz, Marina K, Cole, Adam G, Yuan Zhou, Nathan Robbins, Zhang, Bin, Francis X. McCormack, Bin Zhang, Rebecca Ingledue, Elizabeth J. Kopras, Ingledue, Rebecca   +23 more
core   +1 more source

Extrapulmonary lymphangioleiomyomatosis mimicking lymphoma metastatic to uterus

, 2015
Lymphangioleiomyomatosis is a very rare disease that primarily affects the lungs. The atypical smooth muscle cells in these tumors stain both with smooth muscle markers and melanocytic markers characteristically like their counterparts in other members ...
Iyibozkurt, A. Cem, Sozen, Hamdullah, Vatansever, Dogan, Topuz, Samet, Yavuz, Ekrem, Comba, Cihan   +5 more
core   +1 more source

Evolution of lung pathology in lymphangioleiomyomatosis: associations with disease course and treatment response

The Journal of Pathology: Clinical Research, 2020
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease with a variable clinical course. The lungs are infiltrated by nodules of LAM cells, stromal cells and inflammatory cells, causing lung cysts and respiratory failure. We used immunohistochemical
Suzanne Miller, Iain D Stewart, Debbie Clements, Irshad Soomro, Roya Babaei‐Jadidi, Simon R Johnson   +5 more
doaj   +1 more source