Results 61 to 70 of about 6,813 (202)
The lung microbiome in end-stage Lymphangioleiomyomatosis
, 2021 Lymphangioleiomyomatosis (LAM) is a progressive cystic lung disease with mortality driven primarily by respiratory failure. Patients with LAM frequently have respiratory infections, suggestive of a dysregulated microbiome.
Lesa Begley +17 more
core +1 more source
Lymphangioleiomyomatosis: Searching for potential biomarkers [PDF]
, 2023 Biomarkers; Lymphangioleiomyomatosis; MetalloproteinasesBiomarcadores; Linfangioleiomiomatosis; MetaloproteinasasBiomarcadors; Limfangioleiomiomatosi; MetaloproteinasesBackground: Vascular endothelial growth factor-D (VEGF-D) is the most commonly used ...
Arjona Perís, Marta Vicenta +21 more
core +1 more source
Pulmonary Lymphangioleiomyomatosis
Archives of Pathology & Laboratory Medicine, 2010 Abstract Lymphangioleiomyomatosis is an uncommon lung disease primarily affecting women of childbearing age. It is characterized by the progressive proliferating and infiltrating smooth musclelike cells (lymphangioleiomyomatosis cells), which lead to the cystic destruction of the lung parenchyma; obstruction of ...
Xuchen, Zhang, William D, Travis
openaire +2 more sources
Analysis of a Mouse Skin Model of Tuberous Sclerosis Complex. [PDF]
PLoS ONE, 2016 Tuberous Sclerosis Complex (TSC) is an autosomal dominant tumor suppressor gene syndrome in which patients develop several types of tumors, including facial angiofibroma, subungual fibroma, Shagreen patch, angiomyolipomas, and lymphangioleiomyomatosis ...
Yanan Guo +5 more
doaj +1 more source
Respirology Case Reports, Volume 14, Issue 9, September 2026.A 50‐year‐old woman presented with recurrent spontaneous pneumothorax and bilateral pulmonary cysts. Whole‐exome sequencing identified a pathogenic FLCN variant, confirming Birt‐Hogg‐Dubé (BHD) syndrome 15 years after symptom onset. This case highlights BHD as an underrecognized cause of diffuse cystic lung disease.
Chia‐Ni Liu +2 more
wiley +1 more source
Lung transplantation for lymphangioleiomyomatosis.
, 1996 BACKGROUND Lymphangioleiomyomatosis is a rare disease of unknown origin that usually leads to progressive deterioration of lung function and eventual death from respiratory failure.
Weder W, Speich R, Russi EW, Boehler A
core +1 more source
Physiotherapy in lymphangioleiomyomatosis: a systematic review
, 2022 BACKGROUND: Lymphangioleiomyomatosis (LAM) is associated with progressive dyspnoea and exercise intolerance, but despite the central role of physiotherapy on pulmonary rehabilitation, there is a huge lack of physiotherapy approaches used specifically for
Victoria Maria Garcia de Medeiros +11 more
core +1 more source
Lymphatic Endothelial Cells in Health and Disease
MedComm, Volume 7, Issue 8, August 2026.Lymphatic endothelial cells (LECs) are dynamic regulators of tissue homeostasis and disease remodeling. In the healthy state, LECs coordinate interstitial fluid drainage, intestinal lipid transport, and immune trafficking and tolerance. Across disease settings, however, these same programs become maladaptively reprogrammed, contributing to barrier ...
Du Tang +5 more
wiley +1 more source
Lymphangioleiomyomatosis (LAM) [PDF]
Breathe, 2017 LAM is characterised by lung cysts (air-filled sacs which gradually destroy the lung), changes to the lymphatic system and tumours in the kidneys.
openaire +2 more sources
A rare lung disease diagnosed by CT in a young pregnant woman
Clinical Case Reports, 2021 Lymphangioleiomyomatosis (LAM) is an unusual lung disease which can be diagnosed by its characteristic appearance on a high‐resolution CT, and may not always require a biopsy.
Sunil Persad +3 more
doaj +1 more source