Results 41 to 50 of about 6,813 (202)
Refractory chylous effusions in lymphangioleiomyomatosis patient post lung transplant
SAGE Open Medical Case Reports, 2020 Lymphangioleiomyomatosis is a rare systemic disorder of unknown etiology that affects young women almost exclusively. Chylous effusions are known to be associated with lymphangioleiomyomatosis and may be difficult to treat.
Samuel Jacob +6 more
doaj +1 more source
Frontiers in Medicine, 2021 Background: The desaturation–distance ratio (DDR), the ratio of the desaturation area to the distance walked, is a promising, reliable, and simple physiologic tool for functional evaluation in subjects with interstitial lung diseases ...
Douglas Silva Queiroz +8 more
doaj +1 more source
Sporadic Lymphangioleiomyomatosis Disease: A Case Report [PDF]
Iranian Journal of Medical Sciences, 2023 Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease of the lung and lymphatic system that primarily affects women of childbearing age. LAM is a progressive disease with a terrible prognosis, which worsens over time and is extremely difficult to ...
Yousef Nikmanesh +6 more
doaj +1 more source
VATS therapy of chylothorax caused by leiomyomatosis complicated with tuberous sclerosis complex
Journal of Minimal Access Surgery, 2013 Lymphangioleiomyomatosis with tuberous sclerosis complex is a rare disease. One of the most frequent complications of lymphangioleiomyomatosis is pleural effusion (chylothorax) wich can be treated with the use of VATS.
Adrienn Csiszkó +5 more
doaj +1 more source
Differential diagnosis of chylothorax in therapeutic practice
Терапевтический архив, 2021 The article is devoted to the differential diagnosis of chylous pleural effusion. The spectrum of traumatic and non-traumatic causes of chylothorax is discussed in detail.
Marina A. Makarova +2 more
doaj +1 more source
Lymphangioleiomyomatosis [PDF]
European Respiratory Journal, 2006 Lymphangioleiomyomatosis (LAM) is a rare disease of the lungs and lymphatics, which can occur sporadically or in association with tuberous sclerosis. LAM almost exclusively affects females, generally developing before the menopause.The disease is characterised by progressive pulmonary cystic change, recurrent pneumothorax, chylous pleural collections ...
openaire +2 more sources
French recommendations for the diagnosis and management of lymphangioleiomyomatosis
, 2023 International audienceBackgroundThe present article is an English-language version of the French National Diagnostic and Care Protocol, a pragmatic tool to optimize and harmonize the diagnosis, care pathway, management and follow-up of ...
Turquier, Ségolène +116 more
core +1 more source
Frontiers in Medicine, 2021 Background: Lymphangioleiomyomatosis (LAM) is a rare systemic disease that generally leads to a progressive decline in pulmonary function. Experience, especially from the Asian population, including combined drug therapy before and after lung ...
Ji Zhang +13 more
doaj +1 more source
Annals of Thoracic Medicine, 2014 Lymphangioleiomyomatosis (LAM) is a rare disease that leads to airways and lymphatic channels obstruction due to abnormal smooth muscle proliferation. It presents with dyspnea, pneumothorax or chylothorax.
Mohammed Hussein +3 more
doaj +1 more source
Management of lymphangioleiomyomatosis [PDF]
F1000Prime Reports, 2014 Lymphangioleiomyomatosis (LAM), a multisystem disease affecting almost exclusively women, is characterized by cystic lung destruction and presents with dyspnea, recurrent pneumothoraxes, chylous effusions, lymphangioleiomyomas, and angiomyolipomas.
Taveira-DaSilva, Angelo M., Moss, Joel
openaire +2 more sources