Results 31 to 40 of about 13,250 (289)
Quantifying spatial and dynamic lung abnormalities with 3D PREFUL FLORET UTE imaging: A feasibility study. [PDF]
Magn Reson MedAbstract Purpose Pulmonary MRI faces challenges due to low proton density, rapid transverse magnetization decay, and cardiac and respiratory motion. The fermat‐looped orthogonally encoded trajectories (FLORET) sequence addresses these issues with high sampling efficiency, strong signal, and motion robustness, but has not yet been applied to phase ...
Klimeš F +12 more
europepmc +2 more sources
Long-term clinical course and outcomes in patients with lymphangioleiomyomatosis
Respiratory Research, 2022 Background Lymphangioleiomyomatosis (LAM) is a rare multisystemic disorder with various clinical manifestations. Despite the recognition of several prognostic factors, the long-term clinical course and prognosis of patients with LAM in the era of ...
H. Yoon, H. J. Kim, J. Song
semanticscholar +1 more source
A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]
, 2018 Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M. +3 more
core +1 more source
VATS therapy of chylothorax caused by leiomyomatosis complicated with tuberous sclerosis complex
Journal of Minimal Access Surgery, 2013 Lymphangioleiomyomatosis with tuberous sclerosis complex is a rare disease. One of the most frequent complications of lymphangioleiomyomatosis is pleural effusion (chylothorax) wich can be treated with the use of VATS.
Adrienn Csiszkó +5 more
doaj +1 more source
Analysis of a Mouse Skin Model of Tuberous Sclerosis Complex. [PDF]
PLoS ONE, 2016 Tuberous Sclerosis Complex (TSC) is an autosomal dominant tumor suppressor gene syndrome in which patients develop several types of tumors, including facial angiofibroma, subungual fibroma, Shagreen patch, angiomyolipomas, and lymphangioleiomyomatosis ...
Yanan Guo +5 more
doaj +1 more source
Archivos de Bronconeumología ((English Edition)), 2011 Lymphangioleiomyomatosis (LAM) is a rare disease that mainly affects women, particularly at fertile age. It is sporadic or associated with tuberous sclerosis complex. It is characterised by an abnormal proliferation of immature smooth muscle cells (SMC), which grow aberrantly in the airway, parenchyma, lymphatics and pulmonary blood vessels and which ...
Ansotegui Barrera, Emilio +3 more
openaire +3 more sources
LAM Cells as Potential Drivers of Senescence in Lymphangioleiomyomatosis Microenvironment
International Journal of Molecular Sciences, 2022 Senescence is a stress-response process characterized by the irreversible inhibition of cell proliferation, associated to the acquisition of a senescence-associated secretory phenotype (SASP), that may drive pathological conditions ...
C. Bernardelli +9 more
semanticscholar +1 more source
Cellular antiseizure mechanisms of everolimus in pediatric tuberous sclerosis complex, cortical dysplasia, and non-mTOR-mediated etiologies. [PDF]
, 2018 The present study was designed to examine the potential cellular antiseizure mechanisms of everolimus, a mechanistic target of rapamycin (mTOR) pathway blocker, in pediatric epilepsy cases. Cortical tissue samples obtained from pediatric patients (n
Barry, Joshua +8 more
core +2 more sources
Management of lymphangioleiomyomatosis [PDF]
F1000Prime Reports, 2014 Lymphangioleiomyomatosis (LAM), a multisystem disease affecting almost exclusively women, is characterized by cystic lung destruction and presents with dyspnea, recurrent pneumothoraxes, chylous effusions, lymphangioleiomyomas, and angiomyolipomas.
Angelo M. Taveira-DaSilva, Joel Moss
openaire +3 more sources
Physiotherapy in lymphangioleiomyomatosis: a systematic review
Annals medicus, 2022 Background Lymphangioleiomyomatosis (LAM) is associated with progressive dyspnoea and exercise intolerance, but despite the central role of physiotherapy on pulmonary rehabilitation, there is a huge lack of physiotherapy approaches used specifically for ...
Victoria Maria Garcia de Medeiros +5 more
semanticscholar +1 more source