Lymphatic Abnormalities on Magnetic Resonance Imaging in Single‐Ventricle Congenital Heart Defects Before Glenn Operation [PDF]
Journal of the American Heart Association, 2023 Background In the palliative pathway of single‐ventricle physiology, lymphatic abnormalities on T2‐weighted magnetic resonance imaging have been shown after the Glenn operation.
Rasmus Kristensen +2 more
exaly +4 more sources
Serial T2-Weighted Thoracic and Abdominal Lymphatic Imaging in Fontan Patients—New Insights into Dynamics of Lymphatic Abnormalities after Total Cavopulmonary Connection [PDF]
Journal of Cardiovascular Development and Disease, 2022 Lymphatic congestion in single-ventricle patients has been associated with increased morbidity and poor outcomes. Little is known about the dynamics of lymphatic abnormalities over time, on their association with clinical presentation or response to ...
Julia Moosmann +2 more
exaly +4 more sources
MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome [PDF]
Scientific Reports, 2022 Noonan syndrome is associated with complex lymphatic abnormalities. We report dynamic-contrast enhanced MR lymphangiography (DCMRL) findings in children and adults with Noonan syndrome to further elucidate this complex disease spectrum.
Claus Christian Pieper +1 more
exaly +3 more sources
Lymphatic Abnormalities in Fontan [PDF]
JACC: Case ReportsPlastic bronchitis is a rare but severe complication in Fontan patients. Central lymphatic evaluation may direct therapy for these complications. We present a 22-year-old mn post-Fontan who presented with bronchial casts. Initial medical management failed to reduce cast formation.
Yoav Dori +2 more
exaly +5 more sources
Case Report: Progressive central conducting lymphatic abnormalities in the RASopathies. Two case reports, including successful treatment by MEK inhibition [PDF]
Frontiers in Genetics, 2022 The RASopathies are a group of genetic conditions resulting from mutations within the RAS/mitogen-activated protein kinase (RAS-MAPK) pathway. Lymphatic abnormalities are commonly associated with these conditions, however central conducting lymphatic ...
Kristiana Gordon +12 more
doaj +2 more sources
Lymphatic abnormalities in Alagille's syndrome. [PDF]
Heart, 1991 Chylous pleural effusions developed in a patient with Alagille's syndrome who had dysplasia of the lymphatic system. Lymphatic abnormalities are not a recognised feature of Alagille's syndrome.
D P Dutka
exaly +3 more sources
Phenotypic Analysis of Embryos in a Noonan Syndrome Model Mouse With the Rit1 A57G Mutation [PDF]
Molecular Genetics & Genomic MedicineBackground Noonan syndrome is a congenital genetic disorder characterized by distinctive craniofacial features, short stature, and congenital heart disease.
Dai Suzuki +4 more
doaj +2 more sources
Time lag between functional and structural lymphatic changes after lymphadenectomy: Insights from ICG lymphography and lymphatic ultrasound. [PDF]
PLoS ONEPostoperative lower limb lymphedema is a common complication following pelvic or para-aortic lymphadenectomy for gynecologic cancers. Early detection of lymphatic dysfunction is crucial, but the temporal relationship between functional and structural ...
Hisako Hara +4 more
doaj +2 more sources
Complex Lymphatic Anomaly Presenting with Chylothorax, Chylous Ascites, and Generalized Subcutaneous Edema in a Young Cat: Comparative Insights Based on the Human ISSVA Classification [PDF]
Veterinary SciencesIn human medicine, the 2025 International Society for the Study of Vascular Anomalies (ISSVA) classification distinguishes localized lymphatic malformations from systemic disorders referred to as complex lymphatic anomalies (CLAs), including generalized ...
Kazuyuki Terai +6 more
doaj +2 more sources
Sequential MRI Evaluation of Lymphatic Abnormalities over the Course of Fontan Completion [PDF]
Radiology: Cardiothoracic ImagingBenjamin Kelly +2 more
exaly +2 more sources