Results 1 to 10 of about 27,455 (284)

Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia – a novel mouse model providing insights into geleophysic dysplasia [PDF]

Disease Models & Mechanisms, 2015
Mutations in the secreted glycoprotein ADAMTSL2 cause recessive geleophysic dysplasia (GD) in humans and Musladin–Lueke syndrome (MLS) in dogs. GD is a severe, often lethal, condition presenting with short stature, brachydactyly, stiff skin, joint ...
Dirk Hubmacher, Lauren W. Wang, Robert P. Mecham, Dieter P. Reinhardt, Suneel S. Apte   +4 more
doaj   +5 more sources

Direct Measurement of Plant Cellulose Microfibril and Bundles in Native Cell Walls

Frontiers in Plant Science, 2020
Plants use rigid cellulose together with non-cellulosic matrix polymers to build cell walls. Cellulose microfibrils comprise linear β(1,4)-glucan chains packed through inter- and intra-chain hydrogen-bonding networks and van der Waals forces.
Bo Song, Shuai Zhao, Shuai Zhao, Shuai Zhao, Wei Shen, Wei Shen, Cynthia Collings, Cynthia Collings, Shi-You Ding, Shi-You Ding   +9 more
doaj   +2 more sources

Collagen VI microfibril structure reveals mechanism for molecular assembly and clustering of inherited pathogenic mutations [PDF]

Nature Communications
Collagen VI links the cell surface to the extracellular matrix to provide mechanical strength to most mammalian tissues, and is linked to human diseases including muscular dystrophy, fibrosis, cardiovascular disease and osteoarthritis.
Alan R. F. Godwin, Mark H. Becker, Rana Dajani, Matthew Snee, Alan M. Roseman, Clair Baldock   +5 more
doaj   +2 more sources

Multiscale approach including microfibril scale to assess elastic constants of cortical bone based on neural network computation and homogenization method [PDF]

International Journal for Numerical Methods in Biomedical Engineering, 2013
The complexity and heterogeneity of bone tissue require a multiscale modelling to understand its mechanical behaviour and its remodelling mechanisms.
Alexander, Allen, Ascenzi, Bailey, Barkaoui, Barkaoui, Barkaoui, Baselt, Benezra Rosena, Beno, Benveniste, Bhowmik, Biltz, Boxberger, Brynk, Budyn, Buehler, Buehler, Catanese, Chou, Cowin, Currey, Currey, Deuerling, Dong, Dorozhkin, Dubey, Eberhardsteiner, Eyre, Fan, Fratzl, Fritsch, Fritsch, Gautieri, Gelse, Ghanbari, Gong, Grynpas, Gupta, Habelitz, Hambli, Hambli, Hambli, Hamed, Hellmich, Hellmich, Hellmich, Hellmich, Hoffler, Holmes, Jager, Jenkins, Ji, Jonvaux, Katz, Katz, Knott, Knowles, Kotha, Kotha, Landis, Lees, Liu, Martínez-Reina, Morin, Nemat-Nasser, Nikolov, Nyman, Olszta, Orgel, Orgel, Pidaparti, Porter, Posner, Rafiq, Raspanti, Rho, Rubin, Saito, Sansalone, Sasaki, Sasaki, Sasaki, Sevostianov, Shen, Siegmund, Smith, Suvorov, Tang, Topping, Turner, Uzel, Van der Rijt, Vashishth, Vashishth, Wagner, Wang, Weiner, Wilson, Wu, Yang, Yoon, Yoon, Yoon, Yoon, Yuan, Zysset   +106 more
core   +9 more sources

Resonant soft X-ray scattering reveals cellulose microfibril spacing in plant primary cell walls

Scientific Reports, 2018
Cellulose microfibrils are crucial for many of the remarkable mechanical properties of primary cell walls. Nevertheless, many structural features of cellulose microfibril organization in cell walls are not yet fully described.
Dan Ye, Sarah N. Kiemle, Sintu Rongpipi, Xuan Wang, Cheng Wang, Daniel J. Cosgrove, Esther W. Gomez, Enrique D. Gomez   +7 more
doaj   +2 more sources

Microfibril orientation dominates the microelastic properties of human bone tissue at the lamellar length scale. [PDF]

PLoS ONE, 2013
The elastic properties of bone tissue determine the biomechanical behavior of bone at the organ level. It is now widely accepted that the nanoscale structure of bone plays an important role to determine the elastic properties at the tissue level.
Mathilde Granke, Aurélien Gourrier, Fabienne Rupin, Kay Raum, Françoise Peyrin, Manfred Burghammer, Amena Saïed, Pascal Laugier   +7 more
doaj   +2 more sources

SANS investigation of fungal loosenins reveals substrate-dependent impacts of protein action on the inter-microfibril arrangement of cellulosic substrates [PDF]

Biotechnology for Biofuels and Bioproducts
Background Microbial expansin-related proteins include fungal loosenins, which have been previously shown to disrupt cellulose networks and enhance the enzymatic conversion of cellulosic substrates.
Deepika Dahiya, Zsuzsanna Péter-Szabó, Manjula Senanayake, Sai Venkatesh Pingali, Wellington C. Leite, James Byrnes, Garry W. Buchko, Pramod Sivan, Francisco Vilaplana, Emma R. Master, Hugh O’Neill   +10 more
doaj   +2 more sources

Isolation of cellulose microfibrils - An enzymatic approach [PDF]

BioResources, 2006
Isolation methods and applications of cellulose microfibrils are expanding rapidly due to environmental benefits and specific strength properties, especially in bio-composite science. In this research, we have success-fully developed and explored a novel
Sain, M., Janardhnan, S., and
doaj   +1 more source

Nanoscale Mechanism of Moisture-Induced Swelling in Wood Microfibril Bundles

Nano letters (Print), 2022
Understanding nanoscale moisture interactions is fundamental to most applications of wood, including cellulosic nanomaterials with tailored properties. By combining X-ray scattering experiments with molecular simulations and taking advantage of computed ...
A. Paajanen, A. Zitting, Lauri Rautkari, J. Ketoja, P. Penttilä   +4 more
semanticscholar   +1 more source

Deswelling of microfibril bundles in drying wood studied by small-angle neutron scattering and molecular dynamics

Cellulose, 2021
Structural changes of cellulose microfibrils and microfibril bundles in unmodified spruce cell wall due to drying in air were investigated using time-resolved small-angle neutron scattering (SANS). The scattering analysis was supported with dynamic vapor
A. Zitting, A. Paajanen, Lauri Rautkari, P. Penttilä   +3 more
semanticscholar   +1 more source