HISTORICAL AND MODERN ASPECTS OF CYSTIC FIBROSIS IN RUSSIA
Педиатрическая фармакология, 2013 The article is dedicated to historical and modern trials in the sphere of mucoviscidosis in Russia, peculiarities of clinical manifestations, pathophysiological and pathomorphological disorders and of the disease course with the analysis of the first ...
N. I. Kapranov +4 more
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Severe episodes of extra cellular dehydration : an atypical adult presentation of cystic fibrosis [PDF]
, 2008 Cystic fibrosis (CF) is usually diagnosed during childhood by respiratory or gastro-intestinal symptoms. Hyponatremic hypochloremic dehydration with metabolic alkalosis is a rare but typical presentation of CF in infants.
F. Illouz +5 more
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Tüdőtranszplantáció magyar betegek számára [PDF]
, 2013 When conservative treatment fails, lung transplantation often remains the only therapeutic option for patients with end stage parenchymal or vascular lung diseases.
Czebe K +3 more
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PECULIARITIES OF DORNASE ALFA AND KINESITHERAPY USE IN CHILDREN WITH CYSTIC FIBROSIS
Педиатрическая фармакология, 2013 The article is dedicated to modern treatment of mucoviscidosis. The article covers issues of pathogenesis and emphasizes importance of mucociliary clearance and anatomic-physiological peculiarities of respiratory tract’s structure in childhood in the ...
O. I. Simonova
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PRIMARY HEMOSTATIC SYSTEM CONDITION IN MUCOVISCIDOSIS IN CHILDREN
Педиатрическая фармакология, 2014 The article presents results of a study of platelet hemostasis in children with mucoviscidosis. Motionless and viscous mucus becomes infected with various pathogenic and opportunistic microbes in the setting of disturbed mucociliary clearance; when ...
O. B. Gordeeva +7 more
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Assembly and functional analysis of an S/MAR based episome with the cystic fibrosis transmembrane conductance regulator gene [PDF]
, 2018 Improving the efficacy of gene therapy vectors is still an important goal toward the development of safe and efficient gene therapy treatments. S/MAR (scaffold/matrix attached region)-based vectors are maintained extra-chromosomally in numerous cell ...
Ascenzioni, Fiorentina +10 more
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Distal intestinal obstruction syndrome as unusual manifestation of cystic fibrosis. Report of a case
Acta Pediátrica de México, 2014 Introduction: Distal intestinal obstruction syndrome (DIOS) or “meconium ileus equivalent” is a blockage of the terminal ileum or of the ascending colon caused by inspissated stools in patients with cystic fibrosis (CF) beyond the neonatal period.
Gómez Ruiz Alejandro +2 more
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Making It Last: Storage Time and Temperature Have Differential Impacts on Metabolite Profiles of Airway Samples from Cystic Fibrosis Patients. [PDF]
, 2017 Metabolites of human or microbial origin have the potential to be important biomarkers of the disease state in cystic fibrosis (CF). Clinical sample collection and storage conditions may impact metabolite abundances with clinical relevance.
John J. LiPuma +5 more
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COMPLEX THERAPY OF CHILDREN WITH MUCOVISCIDOSIS. RECOMMENDATIONS OF A PEDIATRICIAN
Педиатрическая фармакология, 2006 Treatment of children's mucoviscidosis is a multicomponent complex of medical and non medicamental types of therapy. The earlier the basic mucoviscidosis treatment has started, the more favourable the diagnosis for the patient will be.
O.I. Simonova
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ROLE OF THE KNOWN MUCOLYTICS IN MUCOVISCIDOSIS THERAPY
Педиатрическая фармакология, 2014 The primary objective in the mucoviscidosis therapy is to ensure normal rheology of respiratory secretion for effective evacuationthereof from the bronchial tree and nasal sinuses.
O. I. Simonova, Yu. V. Gorinova
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