Results 1 to 10 of about 123 (103)
Neurofibroma plexiforme gigante da região lombar com transformação hemorrágica – Relato de caso
A neurofibromatose tipo 1 é uma facomatose que apresenta, entre outras características, tumores oriundos da bainha dos nervos como o neurofibroma plexiforme. Neste artigo é relatado o caso de um paciente que sofreu transformação hemorrágica espontânea de
João Candido Araujo
exaly +3 more sources
UN PEQUEÑO DOLOR CON UNA GRAN EXPLICACIÓN: NEUROFIBROMA PLEXIFORME CUTÁNEO
RESUMEN La neurofibromatosis tipo 1 es una entidad poco frecuente, pero con gran cantidad de complicaciones que pueden ocasionar un gran impacto en la calidad de vida.
virginia González Hidalgo +1 more
exaly +3 more sources
Introducción: La neurofibromatosis tipo 1 NF1, es un síndrome genético autosómico dominante resultado de una mutación del gen supresor tumoral NF1, puede evidenciarse manifestaciones como lo son los neurofibromas plexiformes, que son tumores malignos de ...
Anggie Ariza Alvis +3 more
exaly +3 more sources
Plexiform neurofibromas represent an uncommon variant (30%) of neurofibromatosis type 1 (NF-1) in which neurofibromas arise from multiple nerves as bulging and deforming masses involving also connective tissue and skin folds.We report a rare case of a 30-year-old man who presented with a progressive facial deformity that began in early childhood.
Tchernev, Georgi +5 more
+7 more sources
Este trabajo tiene como objetivo relatar el abordaje individualizado, inclusivo y humanizado de un niño de 4 años y tres meses, con diagnóstico de neurofibromatosis tipo 1, atendido en la Carrera de Especialización en Odontopediatria de la Escuela ...
Silvina Ferreiro López +4 more
doaj +3 more sources
The Plexiform Neurofibroma Microenvironment [PDF]
Dynamic interactions between tumorigenic cells and surrounding cells, including immunomodulatory hematopoietic cells, can dictate tumor initiation, progression, and transformation. Hematopoietic-stromal interactions underpin the plexiform neurofibroma, a debilitating tumor arising in individuals afflicted with Neurofibromatosis type 1 (NF1), a common ...
Feng-Chun, Yang +2 more
openaire +2 more sources
Plexiform Neurofibroma of Clitoris [PDF]
AbstractThe most frequent genital presentation of neurofibromatosis in females is clitoromegaly. We report a case of a 5-year-old girl with neurofibromatosis type 1 with clitoral plexiform neurofibromatosis. Clitoroplasty was done, and the histopathology confirmed the diagnosis.
Dhanya, Yesodharan +6 more
openaire +2 more sources
Exuberant Plexiform Neurofibroma
N/a.
Catarina Correia +2 more
openaire +3 more sources
Schwannoma plexiforme en eminencia tenar
El schwannoma plexiforme es un tumor raro, que suele aparecer en tronco, cabeza y cuello. Su diagnóstico definitivo es anatomopatológico, siendo de especial relevancia su distinción con el neurofibroma plexiforme.
Miriam Rodríguez Rodríguez +2 more
doaj +1 more source
Plexiform neurofibroma of the upper limb Neurofibroma plexiforme de membro superior
The authors present an unusual case of plexiform neurofibroma affecting the upper limb in a patient diagnosed with type 1 neurofibromatosis. Tumor resection was performed on the median nerve.
Kátia Torres Batista +2 more
doaj +1 more source

