Results 11 to 20 of about 124 (104)

Plexiform neurofibroma

open access: yesCleveland Clinic Journal of Medicine, 2016
Plexiform neurofibromas represent an uncommon variant (30%) of neurofibromatosis type 1 (NF-1) in which neurofibromas arise from multiple nerves as bulging and deforming masses involving also connective tissue and skin folds.We report a rare case of a 30-year-old man who presented with a progressive facial deformity that began in early childhood.
Tchernev, Georgi   +5 more
  +7 more sources

Plexiform Neurofibroma of Clitoris [PDF]

open access: yesJournal of Pediatric Genetics, 2017
AbstractThe most frequent genital presentation of neurofibromatosis in females is clitoromegaly. We report a case of a 5-year-old girl with neurofibromatosis type 1 with clitoral plexiform neurofibromatosis. Clitoroplasty was done, and the histopathology confirmed the diagnosis.
Dhanya, Yesodharan   +6 more
openaire   +2 more sources

The Plexiform Neurofibroma Microenvironment [PDF]

open access: yesCancer Microenvironment, 2012
Dynamic interactions between tumorigenic cells and surrounding cells, including immunomodulatory hematopoietic cells, can dictate tumor initiation, progression, and transformation. Hematopoietic-stromal interactions underpin the plexiform neurofibroma, a debilitating tumor arising in individuals afflicted with Neurofibromatosis type 1 (NF1), a common ...
Feng-Chun, Yang   +2 more
openaire   +2 more sources

Exuberant Plexiform Neurofibroma

open access: yesActa Médica Portuguesa, 2023
N/a.
Catarina Correia   +2 more
openaire   +3 more sources

PLEXIFORM NEUROFIBROMA. [PDF]

open access: yesJAMA: The Journal of the American Medical Association, 1906
n ...
openaire   +2 more sources

Tumores de Sistema Nervioso asociados con la Neurofibromatosis tipo 1 y 2

open access: yesRevista Clínica de la Escuela de Medicina UCR-HSJD, 2018
La Neurofibromatosis, hoy entendida como un concepto abarcando dos tipos de enfermedades diferentes (tipo 1 y tipo 2) es una enfermedad genética perteneciente al  grupo de patologías neurocutáneas, inicialmente descrita en 1849 y que aún en la ...
Carlos Mario Sequeira Quesada   +1 more
doaj   +1 more source

Neurofibroma solitario en el paciente sin neurofibromatosis: Aspectos biológicos y clínicos [PDF]

open access: yesMedUNAB, 2008
El neurofibroma es uno de los tumores de la vaina neuralque se da por una proliferación de células de Schwann,mastocitos, fibroblastos y mayor producción de colágeno,es generalmente benigno y puede ser una manifestación deneurofibromatosis.
Ludwing Flórez Salamanca   +1 more
doaj  

Neurofibromatose Plexiforme Cervicale Compressive de l’Enfant : À Propos d’un Cas à Yaoundé

open access: yesHealth Research in Africa
RÉSUMÉ La neurofibromatose 1 (NF1) ou maladie de Von Recklinghausen est une maladie héréditaire autosomique dominante. C’est l’une des maladies génétiques les plus fréquentes. Le neurofibrome plexiforme est une tumeur rare et bénigne, souvent associée à
Andjock Nkouo Yves Christian   +5 more
doaj   +1 more source

Características del neurofibroma plexiforme en pacientes con neurofibromatosis tipo 1. Pinar del Río Characteristics of plexiform neurofibroma in patients suffering from Type-1 Neurofibromatosis. Pinar del Rio

open access: yesRevista de Ciencias Médicas de Pinar del Río, 2012
El neurofibroma plexiforme es un tumor complejo, que involucra varios tejidos. Llevan a una distorsión masiva del lugar donde se encuentran, originando problemas estéticos y médicos. Con este trabajo se pretende conocer la frecuencia de los neurofibromas
Miladys Orraca Castillo   +1 more
doaj  

Challenging Management of Plexiform Schwannoma and Plexiform Neurofibroma

open access: yesJournal of Craniofacial Surgery, 2021
Abstract Plexiform variants of neurofibromas and schwannomas are rare and typically arise in superficial soft tissues in the head and neck region. The treatment of these tumors is challenging and no generally accepted guidelines exist for their optimal management.
Nicoli, Taija K   +5 more
openaire   +4 more sources

Home - About - Disclaimer - Privacy