Results 21 to 30 of about 18,630 (199)

Beyond Hepatitis: A Rare Case of Multisystem Langerhans Cell Histiocytosis in a Child. [PDF]

Clin Case Rep
ABSTRACT Langerhans cell histiocytosis (LCH) is a rare neoplastic disorder involving abnormal proliferation of dendritic cells, with clinical presentations ranging from isolated lesions to life‐threatening multisystem involvement. This case report describes a 26‐month‐old girl who presented with progressive jaundice, fever, hepatomegaly, pruritic scalp
Neupane D, Banjade RR, Joshi D, Awasthi PR, Mishra S.   +4 more
europepmc   +2 more sources

Adult Langerhans cell histiocytosis with a rare BRAF V600E and V600D mutation, diagnosed through oral manifestations

Advances in Oral and Maxillofacial Surgery, 2022
Langerhans cell histiocytosis, is a rare disorder characterized by an aberrant proliferation of Langerhans-type cells that infiltrates and replaces the involved tissues.
Soukaïna Oujdad, Saadia Zafad, Hicham El Attar, Ihsane Ben Yahya   +3 more
doaj   +1 more source

The Clinicopathologic Spectrum of Rosai-Dorfman-Destombes Disease in Adults: An Analysis of 16 Cases. [PDF]

Eur J Haematol
ABSTRACT Rosai–Dorfman–Destombes disease (RDD) is a rare histiocytic proliferation with protean clinical manifestations, resulting from the accumulation of activated histiocytes within nodal and extra‐nodal tissues. The diagnosis can be missed, particularly when biopsies are obtained from extra‐nodal sites, where histological features may be less ...
Trinder M, Pryma C, Leung E, Slack GW, Farinha P, Young S, Ozkaya N, Carruthers M, Chen LYC.   +8 more
europepmc   +2 more sources

Clinical periodontal diagnosis

Periodontology 2000, EarlyView., 2023
Abstract Periodontal diseases include pathological conditions elicited by the presence of bacterial biofilms leading to a host response. In the diagnostic process, clinical signs such as bleeding on probing, development of periodontal pockets and gingival recessions, furcation involvement and presence of radiographic bone loss should be assessed prior ...
Giovanni E. Salvi, Andrea Roccuzzo, Jean‐Claude Imber, Alexandra Stähli, Björn Klinge, Niklaus P. Lang   +5 more
wiley   +1 more source

Langerhans-Cell Histiocytoses - Epidemiology, Classification, Clinical Features, Diagnosis, Complications, Treatment and Prognosis [PDF]

Journal of Biomedical & Clinical Research, 2016
Histiocytoses comprise a group of diverse diseases of unknown etiology with various clinical presentation and evolution. The underlying pathology is characterised by accumulation and infiltration of variable numbers of cells of the monocyte-macrophage ...
Vera Papochieva, Dimitrinka Miteva, Penka Perenovska, Guergana Petrova   +3 more
doaj   +3 more sources

A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations

Journal of Cutaneous Immunology and Allergy, 2023
Rosai–Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969.
Shintaro Saito, Akihiko Uchiyama, Yayoi Shibusawa, Sei‐ichiro Motegi   +3 more
doaj   +1 more source

Tissue-Resident Myeloid and Histiocytic Cells in Health and Disease: Novel Emerging Concepts. [PDF]

Am J Hematol
ABSTRACT Although all myeloid cells are considered to derive from hematopoietic stem cells, the cells in each myeloid lineage are heterogeneous populations, and their distribution and functions vary, depending on underlying physiologic and pathologic processes, age, sex, and genetic and epigenetic signatures.
Valent P, Wojta J, Kovanen PT, Hermine O, Fend F, Sotlar K, Greinix H, Geissler K, Hartmann K, Schwaab J, Herling M, Boccuni L, Kazianka L, John MV, Sperr WR, Zierfuss C, Tzankov A, Sillaber C, Minkov M, Hoermann G, Collin M, Horny HP, Haferlach T, Sibilia M, Haroche J, La Rosée P, Orfao A, Arock M.   +27 more
europepmc   +2 more sources

Adult Langerhans cell histiocytosis with pulmonary and colorectoanal involvement: a case report

Journal of Medical Case Reports, 2017
Background Langerhans cell histiocytosis is a rare systemic disease characterized by the abnormal overproduction of histiocytes that tend to infiltrate single or multiple organ systems leading to significant tissue damage. It mainly affects – by order of
Mohamad Jihad Mansour, Elias Mokbel, Eddy Fares, Janah Maddah, Fadi Nasr   +4 more
doaj   +1 more source

A case of Langerhans cell histiocytosis mimicking child abuse

The Turkish Journal of Pediatrics, 2016
Langerhans cell histiocytosis is a rare non-malignant disease with clinical heterogeneity. The disease may present with various clinical findings and may imitate many other conditions.
Şakire Başer, Yasemin Taşcı, Esin Boduroğlu, Asuman Gürkan, Umut Kaygusuz, Türkan Aydın-Teke, Zeynep Gökçe Gayretli-Aydın, Işıl Zaimoğlu, Ayşe Kaman, Gönül Tanır   +9 more
doaj   +1 more source

Orbital mass and hairy kidney as characteristics of Erdheim‐Chester disease

Clinical Case Reports, 2021
Erdheim‐Chester disease (ECD) is a rare non‐Langerhans cell histiocytosis, involving multiple organs. We report a case of ECD with typical features of an orbital mass and "hairy kidneys," whose recognition can lead to early diagnosis and treatment.
Koichiro Yamamoto, Kosuke Oka, Kou Hasegawa, Fumio Otsuka   +3 more
doaj   +1 more source