Cutaneous Rosai-Dorfman Disease - A Rare Non-Langerhans Cell Histiocytosis
JK ScienceCutaneous Rosai-Dorfman disease is classified as non-Langerhans cell histiocytosis. It is a benign lymphoproliferative disorder involving only skin and subcutaneous tissue, which is rare and not well documented.
Afthab Jameela Wahab +2 more
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JDDG: Journal der Deutschen Dermatologischen Gesellschaft, 2021 restriction
Yeongjoo, Oh +2 more
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Langerhans-Cell Histiocytoses - Epidemiology, Classification, Clinical Features, Diagnosis, Complications, Treatment and Prognosis [PDF]
Journal of Biomedical & Clinical Research, 2016 Histiocytoses comprise a group of diverse diseases of unknown etiology with various clinical presentation and evolution. The underlying pathology is characterised by accumulation and infiltration of variable numbers of cells of the monocyte-macrophage ...
Vera Papochieva +3 more
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Adult Langerhans cell histiocytosis with pulmonary and colorectoanal involvement: a case report
Journal of Medical Case Reports, 2017 Background Langerhans cell histiocytosis is a rare systemic disease characterized by the abnormal overproduction of histiocytes that tend to infiltrate single or multiple organ systems leading to significant tissue damage. It mainly affects – by order of
Mohamad Jihad Mansour +4 more
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A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations
Journal of Cutaneous Immunology and Allergy, 2023 Rosai–Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969.
Shintaro Saito +3 more
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A case of Langerhans cell histiocytosis mimicking child abuse
The Turkish Journal of Pediatrics, 2016 Langerhans cell histiocytosis is a rare non-malignant disease with clinical heterogeneity. The disease may present with various clinical findings and may imitate many other conditions.
Şakire Başer +9 more
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BRAFV600E mutation in cutaneous lesions of patients with adult Langerhans cell histiocytosis. [PDF]
, 2015 BACKGROUND: Langerhans cell histiocytosis (LCH) is characterized by the proliferation of pathologic Langerhans cells. The disease can develop in any age and can affect almost any organ. Cutaneous involvement is frequent in LCH.
Badalian-Very +18 more
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A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]
, 2018 Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M. +3 more
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Choroidal Neovascular Membrane Formation and Retinochoroidopathy in a Patient with Systemic Langerhans Cell Histiocytosis: A Case Report and Review of the Literature [PDF]
, 2012 We report a case of bilateral atrophic retinochoroidopathy with choroidal neovascular membrane (CNVM) formation in a patient with systemic Langerhans cell histiocytosis (LCH).
Foster, Charles Stephen +3 more
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Orbital mass and hairy kidney as characteristics of Erdheim‐Chester disease
Clinical Case Reports, 2021 Erdheim‐Chester disease (ECD) is a rare non‐Langerhans cell histiocytosis, involving multiple organs. We report a case of ECD with typical features of an orbital mass and "hairy kidneys," whose recognition can lead to early diagnosis and treatment.
Koichiro Yamamoto +3 more
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