Erdheim Chester disease – 25 year history with early CNS involvement [PDF]
, 2016 We report a case of Erdheim-Chester disease (ECD) with a 25-year history following initial presentation with diabetes insipidus and brainstem involvement.
Cohen, N +5 more
core +1 more source
Histiocytosis: a review focusing on neuroimaging findings
Arquivos de Neuro-Psiquiatria, 2014 Objective: Histiocytosis is a systemic disease that usually affects the central nervous system. The aim of this study is to discuss the neuroimaging characteristics of Langerhans cell histiocytosis (LCH), the most common of these diseases; and the non ...
Larissa Barcessat Gabbay +4 more
doaj +1 more source
Erdheim-Chester Disease Involving Lymph Nodes and Liver Clinically Mimicking Lymphoma: A Case Report [PDF]
Journal of Pathology and Translational Medicine, 2018 Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis and multisystem disease. First described in 1930, there are no more than 750 cases reported.
Yeoun Eun Sung +3 more
doaj +1 more source
Langerhans cell histiocytosis: current concepts in dentistry and case report [PDF]
, 2016 Langerhans cell histiocytosis (LCH), which is a rare granulomatous pediatric disease of unknown etiology, is characterized by the idiopathic proliferation and accumulation of abnormal and clonal Langerhans cells or their ...
Alejo-Gonzalez, Francisco +4 more
core
Case series of volar juvenile xanthogranuloma: Clinical observation of a peripheral rim of hyperkeratosis [PDF]
, 2014 Juvenile xanthogranuloma is a benign histiocytic tumor predominantly occurring in children as yellowish papules on the head and trunk. Presentations on the volar surfaces are rare and may cause diagnostic confusion with pyogenic granuloma, eccrine poroma
Amadi, Ugochukwu +7 more
core +1 more source
Laryngeal involvement with fatal outcome in progressive nodular histiocytosis: A rare case report
Indian Dermatology Online Journal, 2016 Progressive nodular histiocytosis (PNH) represents a very rare type of non-Langerhans cell histiocytosis. It is characterized by progressive appearance of papules and nodules without spontaneous resolution.
Aarti Salunke +3 more
doaj +1 more source
European Journal of Case Reports in Internal Medicine, 2021 Eosinophilic granuloma is a localized, non-invasive form of Langerhans cell histiocytosis. It usually develops in the long bones and is more frequent in children under the age of 10 years. It is very rare in adults.
Tatiana Pires +5 more
doaj +1 more source
The Clinicopathologic Spectrum of Rosai–Dorfman–Destombes Disease in Adults: An Analysis of 16 Cases
European Journal of Haematology, EarlyView.ABSTRACT Rosai–Dorfman–Destombes disease (RDD) is a rare histiocytic proliferation with protean clinical manifestations, resulting from the accumulation of activated histiocytes within nodal and extra‐nodal tissues. The diagnosis can be missed, particularly when biopsies are obtained from extra‐nodal sites, where histological features may be less ...
Mark Trinder +8 more
wiley +1 more source
Solving a Mystery . . . 8 Years Later
Journal of Investigative Medicine High Impact Case Reports, 2018 Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multisystem involvement and insidious symptoms. In this article, we describe an interesting case of Erdheim-Chester disease that was eventually diagnosed 8 years after symptoms ...
Hayan Jouni MD +2 more
doaj +1 more source
A rare case of solitary brain Langerhans cell histiocytosis with intratumoral hemorrhage in a patient affected by Turner syndrome [PDF]
, 2016 Langerhans cell histiocytosis (LCH) is a rare disease involving clonal proliferation of cells with characteristics similar to bone marrow-derived Langerhans cells. The case of a young woman, affected by Turner syndrome and a solitary intraparenchymal LCH
Alafaci, C. +5 more
core +2 more sources