Pink verrucous plaque in a man with systemic mastocytosis [PDF]
Porokeratosis ptychotropica is a rare and commonly misdiagnosed subtype of porokeratosis involving the body folds. We present a 53-year-old man with systemic mastocytosis who presented with a pruritic, verrucous plaque in the gluteal fold that showed ...
Fung, Maxwell A +4 more
core
Spectrum of malignant skin adnexal tumors – a single institution study of 17 cases with clinicopathological correlation [PDF]
Background: Skin adnexal tumors are a rare, assorted group of tumors with differentiation towards hair follicle, sebaceous glands or sweat glands. A vast majority of them are benign.
Ilias, Laila M. +3 more
core +2 more sources
A tale of two rare entities: extramammary Paget's disease and hepatocellular carcinoma-a singular case report [PDF]
This case report underscores the intricate challenges in managing extramammary Paget's disease (EMPD) of the vulva, a rare neoplasm with diverse clinical manifestations.
Gupta, Sumedha +3 more
core +2 more sources
Case report: Pyrotinib in the treatment of advanced scrotal EMPD combined with sweat gland carcinoma
Extramammary Paget disease (EMPD) is a rare cutaneous intraepithelial adenocarcinoma, which is mostly distributed in areas with sweat gland cells and mainly occurs in the anogenital skin of women.
Liquan Zhu +11 more
doaj +1 more source
Primary vulvar Paget disease - the importance of clinical suspicion [PDF]
Extramammary Paget disease of the vulva is a rare condition that accounts for only 1-2% of vulvar malignancies and represents a frequent cause of misdiagnosis. It is most commonly seen in postmenopausal women. Clinically it is similar to Paget disease of
Foreid, S. +4 more
core
Trastuzumab monotherapy as maintenance treatment for metastatic HER2+ vulvar Paget disease: systematic review and case report [PDF]
Vulvar Paget's disease (VPD) is a rare intraepithelial malignancy frequently associated with HER2 overexpression. This study offers insights into managing HER2-positive extramammary Paget's disease cases in which trastuzumab monotherapy was administered ...
Berretta, Massimiliano +8 more
core +1 more source
The Effectiveness of Mapping Biopsy in Patients with Extramammary Paget's Disease
Background Extramammary Paget's disease (EMPD) is an intraepithelial carcinoma usually occurring on the skin or mucosa of the perineum. Clinically, it resembles eczema or dermatitis, and misdiagnosis and treatment delays are common.
Byung Jun Kim, Shin Ki Park, Hak Chang
doaj +1 more source
Rare perianal extramammary Paget disease successfully treated using topical Imiquimod therapy
Background Perianal Paget’s disease (PPD) is a rare intraepithelial adenocarcinoma of the anal margin. Primary PPD likely represents intra-epithelial neoplasm from an apocrine source, whereas secondary disease may represent “pagetoid” spread from an ...
Jéssica Silva dos Santos +5 more
doaj +1 more source
asymmetrically pigmented patch on the vulvo perineal area a quiz [PDF]
n/
M Le Donne, M Lentini
core +1 more source

