Results 1 to 10 of about 43,184 (256)

S2k guidelines on the management of paraneoplastic pemphigus/paraneoplastic autoimmune multiorgan syndrome initiated by the European Academy of Dermatology and Venereology (EADV). [PDF]

J Eur Acad Dermatol Venereol, 2023
BACKGROUND Paraneoplastic pemphigus (PNP), also called paraneoplastic autoimmune multiorgan syndrome (PAMS), is a rare autoimmune disease with mucocutaneous and multi-organ involvement.
Antiga E, Bech R, Maglie R, Genovese G, Borradori L, Bockle B, Caproni M, Caux F, Chandran NS, Corrà A, D'Amore F, Daneshpazhooh M, De D, Didona D, Dmochowski M, Drenovska K, Ehrchen J, Feliciani C, Goebeler M, Groves R, Günther C, Handa S, Hofmann SC, Horvath B, Ioannidis D, Jedlickova H, Kowalewski C, Kridin K, Joly P, Lim YL, Marinovic B, Maverakis E, Meijer J, Patsatsi A, Pincelli C, Prost C, Setterfield J, Sprecher E, Skiljevic D, Tasanen K, Uzun S, Van Beek N, Vassileva S, Vorobyev A, Vujic I, Wang G, Wang M, Wozniak K, Yayli S, Zambruno G, Hashimoto T, Schmidt E, Mascarò JM, Marzano AV.   +53 more
europepmc   +12 more sources

Case Report: A middle-aged woman with mediastinal follicular dendritic cell sarcoma complicated by paraneoplastic pemphigus [PDF]

Frontiers in Oncology
As a relatively rare malignant entity, follicular dendritic cell sarcoma (FDCS) of the mediastinum currently suffers from insufficient clinical characterization, warranting more comprehensive studies to optimize therapeutic strategies.
Yongchun Wang, Yongchun Wang, Min Zhou, Min Zhou, Feifei Wang, Zhiyan Hu, Yan Ruan   +6 more
doaj   +3 more sources

Paraneoplastic pemphigus regression after thymoma resection [PDF]

World Journal of Surgical Oncology, 2008
Background Among human neoplasms thymomas are associated with highest frequency with paraneoplastic autoimmune diseases. Case presentation A case of a 42-year-old woman with paraneoplastic pemphigus as the first manifestation of thymoma is reported ...
Stergiou Eleni, Asteriou Christos, Boukovinas Ioannis, Paliouras Dimitrios, Samanidis Georgios, Barbetakis Nikolaos, Laschos Kostas, Tsilikas Christodoulos   +7 more
doaj   +7 more sources

Paraneoplastic pemphigus and reported, identified underlying diseases [PDF]

Journal of Education, Health and Sport
Introduction: Pemphigus is a rare group of autoimmune diseases that promote development of various skin eruptions, the most commonly it presents with blisters.
Paweł Iwańczuk
doaj   +4 more sources

Pulmonary small lymphocytic lymphoma combined with paraneoplastic pemphigus and bronchiolitis obliterans: a case report [PDF]

BMC Pulmonary Medicine
Background Paraneoplastic pemphigus is a rare autoimmune mucocutaneous disease often associated with neoplasms. When complicated with bronchiolitis obliterans, it can lead to irreversible pulmonary dysfunction and carries a high risk of mortality.
Shulei Sun, Jie Hu, Yanjun Zheng, Liwen Zheng, Shuo Li, Haiyan Zhao   +5 more
doaj   +4 more sources

Myocardial Damage in a Highly Suspected Case With Paraneoplastic Pemphigus: A Case Report and Literature Review [PDF]

Frontiers in Medicine, 2022
Paraneoplastic pemphigus (PNP) is a rare mucocutaneous autoimmune disease. It has multiple clinical accompanied symptoms by affecting various types of epithelia, including the gastrointestinal and respiratory tract.
Xiao Du, Xiao Du, Xiao Du, Xiao Du, Miao Zhang, Miao Zhang, Miao Zhang, Miao Zhang, Shilan Zhang, Shilan Zhang, Shilan Zhang, Shilan Zhang, Feng Tian, Feng Tian, Feng Tian, Feng Tian, Tie Wen, Tie Wen, Ling Liu, Ling Liu, Ling Liu, Ling Liu   +21 more
doaj   +3 more sources

Paraneoplastic pemphigus with airway involvement [PDF]

Respiratory Medicine Case Reports
We report a case of paraneoplastic pemphigus presenting with acute hypoxemic respiratory failure due to bronchiolitis obliterans which improved with high dose systemic corticosteroids, rituximab, niacinamide and doxycycline.
Oscar A. Estrada Paz, Timothy J. Young
doaj   +6 more sources

Non-classical forms of pemphigus: pemphigus herpetiformis, IgA pemphigus, paraneoplastic pemphigus and IgG/IgA pemphigus [PDF]

Anais Brasileiros de Dermatologia, 2014
The pemphigus group comprises the autoimmune intraepidermal blistering diseases classically divided into two major types: pemphigus vulgaris and pemphigus foliaceous.
Adriana Maria Porro, Livia de Vasconcelos Nasser Caetano, Laura de Sena Nogueira Maehara, Milvia Maria dos Santos Enokihara   +3 more
doaj   +6 more sources

Oral Paraneoplastic Pemphigus and Pharyngeal Squamous Cell Carcinoma: A Rare Case Report and Review of Literature

Acta Medica Iranica, 2020
Paraneoplastic pemphigus (PNP) is an autoimmune vesiculo-bullous disease of skin and mucous membrane associated with benign and malignant neoplasm. Most common malignancies associated with PNP are hematologic and lymphomatoid.
Mohd Saalim, Kaustubh Sansare, Freny R Karjodkar, Bushra Rahman, Sneha R Sharma   +4 more
doaj   +2 more sources

Paraneoplastic pemphigus [PDF]

, 2022
Paraneoplastic pemphigus is a rare but severe potentially fatal autoimmune disease characterized by severe stomatitis and a variety of cutaneous manifestations in association with an underlying neoplasia. Pulmonary involvement may also occur.
Diercks, Gilles F.H., Horváth, Barbara, Jonkman, Marcel F., Pas, Hendri H., Poot, Angelique M.   +4 more
core   +3 more sources