Results 41 to 50 of about 1,172,500 (238)

Hodgkin's lymphoma‐associated vanishing bile duct syndrome successfully treated with radiation as a bridge to chemotherapy

Precision Radiation Oncology, 2021
Vanishing bile duct syndrome is a paraneoplastic manifestation of Hodgkin's lymphoma that often proves fatal. Treatment of the underlying lymphoma with chemotherapy is a priority, and liver dysfunction is frequently prohibitive.
Maryam Ebadi, Jeffrey Olson, Justin Bateman, Damien Mathew, Jianling Yuan, Armin Rashidi   +5 more
doaj   +1 more source

Long‐Term Efficacy of Immunotherapy in Autoimmune Autonomic Ganglionopathy—A 10‐Year Follow Up Study

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Autoimmune autonomic ganglionopathy (AAG) is a rare but potentially treatable cause of severe autonomic failure. Evidence guiding long‐term immunotherapy, treatment sequencing, and residual autonomic impairment is limited. We evaluated long‐term treatment response, residual autonomic dysfunction, and relapse patterns in patients with
Giacomo Chiaro, Shiwen Koay, Gordon T. Ingle, Patricia McNamara, Laura Watson, Fion Bremner, Valeria Iodice   +6 more
wiley   +1 more source

Bi‐ and Mono‐Allelic RFC1 Expansion in a North American Cohort With Idiopathic Axonal Neuropathy

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective RFC1 biallelic repeat expansion is increasingly recognized as a cause of chronic idiopathic axonal polyneuropathy (CIAP), but it remains challenging to know who to test. This study aims to determine the prevalence of biallelic and monoallelic RFC1 expansions and their corresponding neuropathy phenotypes in CIAP patients and identify ...
Amro M. Stino, Lavanya Muthukumar, Evan L. Reynolds, Peter Todd, Sinem Ovunc, Sheng Chih Jin, Zitian Tang, Simone Thomas, PNRR Study Group, Ahmet Höke, Brian C. Callaghan, Sarah Berth, Vinay Chaudhry, David Cornblath, Leana Doherty, Lindsey Hayes, Hristelina Ilieva, Thomas Lloyd, Mohammad Khoshnoodi, Brett McCray, Brett Morrison, Bipasha Mukherjee‐Clavin, Lyle Ostrow, Michael Polydefkis, Ricardo Roda, Charlotte Sumner   +25 more
wiley   +1 more source

Imitated Guillian-Barré syndrome in paraneoplastic syndrome [PDF]

Guillian-Barré syndrome (GBS) is an immune mediated disease which is most commonly caused by infections. Symptoms are rapidly progressive and may include servere weakness of the extremities, bulbar weakness, autonomic dysfunction and respiratory ...
Kristiansen, Linnea Mimi Walsted, Kingstam, Walentin Carl, Holbech, Jakob Vormstrup   +2 more
core   +4 more sources

A Case of Anti-Hu Antibody-positive Paraneoplastic Neurological Syndrome due to Mediastinal Lymph Node Small Cell Carcinoma of Unknown Primary Origin [PDF]

, 2022
A 65-year-old man visited our hospital with the complaint of rapid exacerbation of dysphagia. He had no otolaryngological or digestive system disorders.
Sato, Taiki, Ogawa, Tomohiro, Onoue, Hiroyuki, Numahata, Kyoko, Akaiwa, Yasuhiro, Kobayashi, Satoru, Miyamoto, Tomoyuki   +6 more
core   +1 more source

Sweet′s syndrome with multiple myeloma

Journal of Applied Hematology, 2014
We are reporting a case of 70-yr-old gentleman who presented to dermatology clinic with painful red rash which was confirmed to be a sweet′s syndrome by biopsy . Further work up showed IgA myeloma. The patient showed good response to systemic and topical
Khalid Alsaleh
doaj   +1 more source

Opsoclonus in Pediatric Patients: Differential Diagnosis and a Practical Approach to Evaluation

Annals of the Child Neurology Society, EarlyView.
ABSTRACT Opsoclonus is an ocular dyskinesia characterized by involuntary, arrhythmic, multidirectional saccades. In pediatrics, opsoclonus is most commonly attributed to the rare neuroinflammatory disorder opsoclonus‐myoclonus‐ataxia syndrome (OMAS), typically considered a paraneoplastic syndrome associated with neural crest tumors. However, opsoclonus
Aubrey C. Reed, Supreet S. Randhawa, Jason H. Peragallo, Prabhumallikarjun Patil, Grace Gombolay, Varun Kannan   +5 more
wiley   +1 more source

Autoimmune encephalitis in psychiatric institutions: current perspectives

Neuropsychiatric Disease and Treatment, 2016
Chloe Bost,1–3 Olivier Pascual,2,3 Jérôme Honnorat1–3 1French Reference Center of Paraneoplastic Neurological Syndrome, Hospices Civils de Lyon, Hôpital Neurologique, Bron, France; 2Synatac Team ...
Bost C, Pascual O, Honnorat J
doaj  

New onset refractory status epilepticus (NORSE) versus refractory status epilepticus not meeting NORSE criteria: A comparative clinical and electroencephalography‐based study

Epilepsia, EarlyView.
Abstract Objective New onset refractory status epilepticus (NORSE) is a rare, severe presentation of refractory status epilepticus (RSE), with approximately half of cases cryptogenic NORSE (c‐NORSE). We compared electroencephalographic (EEG) findings alongside clinical features between NORSE and RSE not meeting NORSE criteria to better understand ...
Seren Hawksworth, Nina Moutonnet, Gregory Scott, Sanjeev Rajakulendran, Mahinda Yogarajah, Matthew C. Walker, Umesh Vivekananda   +6 more
wiley   +1 more source

The Neuropathology of Paraneoplastic Syndromes

Brain Pathology, 1999
The term “paraneoplastic neurological syndromes” encompasses a number of uncommon disorders associated with systemic malignancies. In order to be classified a paraneoplastic neurological syndrome, the malignancies must not invade, compress, or metastasize to the nervous system.
F, Scaravilli, S F, An, M, Groves, M, Thom   +3 more
openaire   +3 more sources